Klippel Trenaunay syndrome in a 3-year-old: A case report.
Case report
Klippel Trenaunay syndrome
Port-wine stain
Sclerotherapy
Varicose veins
Vascular malformations
Journal
International journal of surgery case reports
ISSN: 2210-2612
Titre abrégé: Int J Surg Case Rep
Pays: Netherlands
ID NLM: 101529872
Informations de publication
Date de publication:
Oct 2022
Oct 2022
Historique:
received:
13
08
2022
revised:
13
09
2022
accepted:
14
09
2022
pubmed:
29
9
2022
medline:
29
9
2022
entrez:
28
9
2022
Statut:
ppublish
Résumé
Klippel-Trenaunay syndrome (KTS) is characterized by a triad of port-wine stain, varicose veins and soft tissue or bony hypertrophy of lower limb. Varicose veins in Klippel Trenaunay syndrome are mostly distributed in the lateral aspect of the lower limb. The exact etiology of KTS is not known, and the treatment usually starts with conservative management- limb elevation, compression stockings and physiotherapy. However, some cases are severe enough to warrant surgical management. Here we present a case of a 3-year-old male child with clinical features suggestive of Klippel Trenaunay Syndrome managed successfully with sclerotherapy of persistent lateral marginal vein of servelle. At one month follow-up the vein was sclerosed and there was a significant reduction in varicosities of leg. Starting treatment of varicose veins in Klippel Trenaunay Syndrome in children is effective in preventing long-term complications in adults. Thus, treating venous malformation with sclerotherapy is warranted in early childhood to prevent venous hypertension and chronic venous insufficiency. Varicose veins in KT syndrome can be managed successfully by sclerotherapy of lateral marginal vein of servelle resulting in significant reduction in varicosities of leg.
Identifiants
pubmed: 36170793
pii: S2210-2612(22)00919-1
doi: 10.1016/j.ijscr.2022.107673
pmc: PMC9568750
pii:
doi:
Types de publication
Case Reports
Langues
eng
Pagination
107673Informations de copyright
Copyright © 2022 The Authors. Published by Elsevier Ltd.. All rights reserved.
Déclaration de conflit d'intérêts
Declaration of competing interest None.
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