Bilateral asymptomatic macular hypopigmentation in a young woman: multimodal imaging and pathogenetic hypothesis.

Macular retinal hypopigmentation Near-infrared autofluorescence Optical coherence tomography Retinal pigment epithelium Short-wavelength autofluorescence

Journal

American journal of ophthalmology case reports
ISSN: 2451-9936
Titre abrégé: Am J Ophthalmol Case Rep
Pays: United States
ID NLM: 101679941

Informations de publication

Date de publication:
Dec 2022
Historique:
received: 02 06 2022
revised: 06 10 2022
accepted: 09 10 2022
entrez: 27 10 2022
pubmed: 28 10 2022
medline: 28 10 2022
Statut: epublish

Résumé

Macular retinal pigment epithelium (RPE) hypopigmentation is a recently described very rare condition and its pathogenesis is not completely understood. We report the case of a 23-year-old female who presented with bilateral whitish, oval-shaped foveal lesions and we speculated about the possible etiopathogenetic origin. A 23-year-old female presented to our consideration for a routine ophthalmology visit. Visual acuity was 20/20 in both eyes. The fundus examination revealed a perifoveal choroidal nevus in the right eye and a bilateral yellowish, oval-shaped lesion centered on the fovea. Imaging tests (Spectral Domain-Optical Coherence Tomography, short wavelength and near-infrared autofluorescence) and functional tests (microperimetry and multifocal electroretinogram) were within normal limits, supporting the diagnosis of macular hypopigmentation without functional loss. A complex dysregulation of both choroidal and RPE with melanin loss may be responsible for this condition.

Identifiants

pubmed: 36299983
doi: 10.1016/j.ajoc.2022.101725
pii: S2451-9936(22)00471-6
pmc: PMC9589140
doi:

Types de publication

Case Reports

Langues

eng

Pagination

101725

Informations de copyright

© 2022 The Authors.

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Auteurs

Federico Fantaguzzi (F)

Department of Ophthalmology, University Vita-Salute, IRCCS San Raffaele, Milan, Italy.

Ilaria Zucchiatti (I)

Department of Ophthalmology, University Vita-Salute, IRCCS San Raffaele, Milan, Italy.

Riccardo Sacconi (R)

Department of Ophthalmology, University Vita-Salute, IRCCS San Raffaele, Milan, Italy.

Anna Valeria Bux (AV)

Department of Ophthalmology, University of Foggia, Foggia, Italy.

Francesco Prascina (F)

Department of Ophthalmology, University Vita-Salute, IRCCS San Raffaele, Milan, Italy.

Francesco Bandello (F)

Department of Ophthalmology, University Vita-Salute, IRCCS San Raffaele, Milan, Italy.

Giuseppe Querques (G)

Department of Ophthalmology, University Vita-Salute, IRCCS San Raffaele, Milan, Italy.

Classifications MeSH