A multicenter study of genetic testing for Parkinson's disease in the clinical setting.


Journal

NPJ Parkinson's disease
ISSN: 2373-8057
Titre abrégé: NPJ Parkinsons Dis
Pays: United States
ID NLM: 101675390

Informations de publication

Date de publication:
04 Nov 2022
Historique:
received: 15 03 2022
accepted: 05 10 2022
entrez: 5 11 2022
pubmed: 6 11 2022
medline: 6 11 2022
Statut: epublish

Résumé

Parkinson's disease (PD) guidelines lack clear criteria for genetic evaluation. We assessed the yield and rationale of genetic testing for PD in a routine clinical setting on a multicenter cohort of 149 early-onset and familial patients by exome sequencing and semi-quantitative multiplex ligation-dependent probe amplification of evidence-based PD-associated gene panel. We show that genetic testing for PD should be considered for both early-onset and familial patients alike, and a clinical yield of about 10% in the Caucasian population can be expected.

Identifiants

pubmed: 36333361
doi: 10.1038/s41531-022-00408-6
pii: 10.1038/s41531-022-00408-6
pmc: PMC9636217
doi:

Types de publication

Journal Article

Langues

eng

Pagination

149

Subventions

Organisme : Javna Agencija za Raziskovalno Dejavnost RS (Slovenian Research Agency)
ID : V3-1911
Organisme : Javna Agencija za Raziskovalno Dejavnost RS (Slovenian Research Agency)
ID : V3-1911
Organisme : Javna Agencija za Raziskovalno Dejavnost RS (Slovenian Research Agency)
ID : V3-1911
Organisme : Javna Agencija za Raziskovalno Dejavnost RS (Slovenian Research Agency)
ID : V3-1911
Organisme : Javna Agencija za Raziskovalno Dejavnost RS (Slovenian Research Agency)
ID : J3-9280
Organisme : Javna Agencija za Raziskovalno Dejavnost RS (Slovenian Research Agency)
ID : V3-1911
Organisme : Hrvatska Zaklada za Znanost (Croatian Science Foundation)
ID : IP-2019-04-7276
Organisme : Hrvatska Zaklada za Znanost (Croatian Science Foundation)
ID : IP-2019-04-7276
Organisme : Hrvatska Zaklada za Znanost (Croatian Science Foundation)
ID : IP-2019-04-7276
Organisme : Ministarstvo Prosvete, Nauke i Tehnološkog Razvoja (Ministry of Education, Science and Technological Development of the Republic of Serbia)
ID : 175090

Informations de copyright

© 2022. The Author(s).

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Auteurs

Anja Kovanda (A)

Clinical Institute of Genomic Medicine, University Medical Centre Ljubljana, Ljubljana, Slovenia.

Valentino Rački (V)

Department of Neurology, University of Rijeka, Faculty of Medicine, Rijeka, Croatia.

Gaber Bergant (G)

Clinical Institute of Genomic Medicine, University Medical Centre Ljubljana, Ljubljana, Slovenia.

Dejan Georgiev (D)

Department of Neurology, University Medical Centre Ljubljana, Ljubljana, Slovenia.
Artificial Intelligence Lab, Faculty of Computer and Information Sciences, University of Ljubljana, Ljubljana, Slovenia.

Dušan Flisar (D)

Department of Neurology, University Medical Centre Ljubljana, Ljubljana, Slovenia.

Eliša Papić (E)

Department of Neurology, University of Rijeka, Faculty of Medicine, Rijeka, Croatia.

Marija Brankovic (M)

Neurology Clinic, Faculty of Medicine, University of Belgrade, Belgrade, Serbia.

Milena Jankovic (M)

Neurology Clinic, UCCS, Belgrade, Serbia.

Marina Svetel (M)

Neurology Clinic, Faculty of Medicine, University of Belgrade, Belgrade, Serbia.

Nataša Teran (N)

Clinical Institute of Genomic Medicine, University Medical Centre Ljubljana, Ljubljana, Slovenia.

Aleš Maver (A)

Clinical Institute of Genomic Medicine, University Medical Centre Ljubljana, Ljubljana, Slovenia.

Vladimir S Kostic (VS)

Neurology Clinic, Faculty of Medicine, University of Belgrade, Belgrade, Serbia.

Ivana Novakovic (I)

Institute of Human Genetics and Neurology Clinic, Faculty of Medicine, University of Belgrade, Belgrade, Serbia.

Zvezdan Pirtošek (Z)

Department of Neurology, University Medical Centre Ljubljana, Ljubljana, Slovenia.
Department of Neurology, Faculty of Medicine, University of Ljubljana, Ljubljana, Slovenia.

Martin Rakuša (M)

Department of Neurology, University Medical Centre Maribor, Maribor, Slovenia.

Vladimira Vuletić (V)

Department of Neurology, University of Rijeka, Faculty of Medicine, Rijeka, Croatia.

Borut Peterlin (B)

Clinical Institute of Genomic Medicine, University Medical Centre Ljubljana, Ljubljana, Slovenia. borut.peterlin@kclj.si.

Classifications MeSH