Renal X-inactivation in female individuals with X-linked Alport syndrome primarily determined by age.

Alport syndrome COL4A5 X-inactivation end-stage kidney disease microscopic hematuria proteinuria urine-derived cells

Journal

Frontiers in medicine
ISSN: 2296-858X
Titre abrégé: Front Med (Lausanne)
Pays: Switzerland
ID NLM: 101648047

Informations de publication

Date de publication:
2022
Historique:
received: 26 05 2022
accepted: 21 09 2022
entrez: 7 11 2022
pubmed: 8 11 2022
medline: 8 11 2022
Statut: epublish

Résumé

X-linked Alport syndrome (AS) caused by hemizygous disease-causing variants in

Identifiants

pubmed: 36341250
doi: 10.3389/fmed.2022.953643
pmc: PMC9630586
doi:

Types de publication

Journal Article

Langues

eng

Pagination

953643

Informations de copyright

Copyright © 2022 Günthner, Knipping, Jeruschke, Satanoskij, Lorenz-Depiereux, Hemmer, Braunisch, Riedhammer, Ćomić, Tönshoff, Tasic, Abazi-Emini, Nushi-Stavileci, Buiting, Gjorgjievski, Momirovska, Patzer, Kirschstein, Gross, Lungu, Weber, Renders, Heemann, Meitinger, Büscher and Hoefele.

Déclaration de conflit d'intérêts

The authors declare that the research was conducted in the absence of any commercial or financial relationships that could be construed as a potential conflict of interest.

Références

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Auteurs

Roman Günthner (R)

Department of Nephrology, Klinikum rechts der Isar, Technical University of Munich, School of Medicine, Munich, Germany.
Institute of Human Genetics, Klinikum rechts der Isar, Technical University of Munich, School of Medicine, Munich, Germany.

Lea Knipping (L)

Pediatric Nephrology, University Hospital Essen, Essen, Germany.

Stefanie Jeruschke (S)

Pediatric Nephrology, University Hospital Essen, Essen, Germany.

Robin Satanoskij (R)

Department of Nephrology, Klinikum rechts der Isar, Technical University of Munich, School of Medicine, Munich, Germany.

Bettina Lorenz-Depiereux (B)

Molecular Epidemiology, Helmholtz Zentrum München, Munich, Germany.

Clara Hemmer (C)

Institute of Human Genetics, Klinikum rechts der Isar, Technical University of Munich, School of Medicine, Munich, Germany.

Matthias C Braunisch (MC)

Department of Nephrology, Klinikum rechts der Isar, Technical University of Munich, School of Medicine, Munich, Germany.
Institute of Human Genetics, Klinikum rechts der Isar, Technical University of Munich, School of Medicine, Munich, Germany.

Korbinian M Riedhammer (KM)

Department of Nephrology, Klinikum rechts der Isar, Technical University of Munich, School of Medicine, Munich, Germany.
Institute of Human Genetics, Klinikum rechts der Isar, Technical University of Munich, School of Medicine, Munich, Germany.

Jasmina Ćomić (J)

Department of Nephrology, Klinikum rechts der Isar, Technical University of Munich, School of Medicine, Munich, Germany.
Institute of Human Genetics, Klinikum rechts der Isar, Technical University of Munich, School of Medicine, Munich, Germany.

Burkhard Tönshoff (B)

Department of Pediatrics I, University Children's Hospital Heidelberg, Heidelberg, Germany.

Velibor Tasic (V)

University Children's Hospital, Medical Faculty of Skopje, Skopje, North Macedonia.

Nora Abazi-Emini (N)

University Children's Hospital, Medical Faculty of Skopje, Skopje, North Macedonia.

Valbona Nushi-Stavileci (V)

Pediatric Clinic, University Clinical Center of Kosovo, Pristina, Kosovo.

Karin Buiting (K)

Institute for Human Genetics, University Hospital Essen, Essen, Germany.

Nikola Gjorgjievski (N)

University Hospital of Nephrology, Faculty of Medicine, University "Ss Cyril and Methodius," Skopje, North Macedonia.

Ana Momirovska (A)

PHI SYNLAB Skopje Laboratories, Skopje, North Macedonia.

Ludwig Patzer (L)

Department of Pediatrics, Children's Hospital St. Elisabeth and St. Barbara, Halle (Saale), Germany.

Martin Kirschstein (M)

Department of Pediatrics, General Hospital, Celle, Germany.

Oliver Gross (O)

Clinic for Nephrology and Rheumatology, University Medical Center Göttingen, Göttingen, Germany.

Adrian Lungu (A)

Fundeni Clinical Institute, Pediatric Nephrology Department, Bucharest, Romania.

Stefanie Weber (S)

Department of Pediatrics II, University Children's Hospital, Philipps-University Marburg, Marburg, Germany.

Lutz Renders (L)

Department of Nephrology, Klinikum rechts der Isar, Technical University of Munich, School of Medicine, Munich, Germany.

Uwe Heemann (U)

Department of Nephrology, Klinikum rechts der Isar, Technical University of Munich, School of Medicine, Munich, Germany.

Thomas Meitinger (T)

Institute of Human Genetics, Klinikum rechts der Isar, Technical University of Munich, School of Medicine, Munich, Germany.

Anja K Büscher (AK)

Pediatric Nephrology, University Hospital Essen, Essen, Germany.

Julia Hoefele (J)

Institute of Human Genetics, Klinikum rechts der Isar, Technical University of Munich, School of Medicine, Munich, Germany.

Classifications MeSH