Pulmonary Arterial Hypertension in Connective Tissue Diseases Beyond Systemic Sclerosis.
Associated pulmonary arterial hypertension
Connective tissue disease
Epidemiology
Mixed connective tissue disease
Pulmonary hypertension
Scleroderma
Screening
Systemic lupus erythematosus
Journal
Heart failure clinics
ISSN: 1551-7136
Titre abrégé: Heart Fail Clin
Pays: United States
ID NLM: 101231934
Informations de publication
Date de publication:
Jan 2023
Jan 2023
Historique:
entrez:
26
11
2022
pubmed:
27
11
2022
medline:
30
11
2022
Statut:
ppublish
Résumé
Pulmonary arterial hypertension (PAH) associated with connective tissue disease (CTD) (CTD-PAH) is a devastating condition that may progress rapidly to cause right ventricular dysfunction, resulting in significant morbidity and mortality. The pathobiology, epidemiology, natural history, early diagnosis, and treatment response of PAH associated with scleroderma (SSc-PAH) have been the subjects of intense research efforts over the previous decade. The success of these efforts has resulted in increased awareness and earlier detection of SSc-PAH. Practitioners are less aware of the risk of PAH associated with other CTDs; the aim of this article is to discuss the broader scope of CTD-PAH.
Identifiants
pubmed: 36435572
pii: S1551-7136(22)00068-X
doi: 10.1016/j.hfc.2022.08.016
pii:
doi:
Types de publication
Journal Article
Review
Langues
eng
Sous-ensembles de citation
IM
Pagination
45-54Informations de copyright
Copyright © 2022 Elsevier Inc. All rights reserved.
Déclaration de conflit d'intérêts
Disclosure The authors have nothing to disclose.