A Boy Who Knows No Pain: Anaesthetic Management of Congenital Insensitivity to Pain With Anhidrosis.

anaesthetic complications analgesia autonomic dysregulation cipa perioperative management

Journal

Cureus
ISSN: 2168-8184
Titre abrégé: Cureus
Pays: United States
ID NLM: 101596737

Informations de publication

Date de publication:
Oct 2022
Historique:
accepted: 28 10 2022
entrez: 30 11 2022
pubmed: 1 12 2022
medline: 1 12 2022
Statut: epublish

Résumé

Congenital insensitivity to pain with anhidrosis (CIPA) is a rare disorder with an absence of pain perception, anhidrosis, heat intolerance, and varying degrees of mental retardation. Though cases of CIPA have innate analgesia, they have been known to have tactile hyperesthesia, thus making anesthesia necessary in case of any surgery. Perioperative complications due to abnormal autonomic functions like bradycardia, hypotension, and hyperthermia are major challenges in the anesthetic management of these cases. Here, we report a case on the anesthetic management of CIPA.

Identifiants

pubmed: 36447712
doi: 10.7759/cureus.30790
pmc: PMC9701320
doi:

Types de publication

Case Reports

Langues

eng

Pagination

e30790

Informations de copyright

Copyright © 2022, Paul et al.

Déclaration de conflit d'intérêts

The authors have declared that no competing interests exist.

Références

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Auteurs

Maria Paul (M)

Anesthesia and Critical Care, Vardhman Mahavir Medical College and Safdarjung Hospital, New Delhi, IND.

Charu Bamba (C)

Anesthesia and Critical Care, Vardhman Mahavir Medical College and Safdarjung Hospital, New Delhi, IND.

Vanya Chugh (V)

Anesthesia and Critical Care, Vardhman Mahavir Medical College and Safdarjung Hospital, New Delhi, IND.

Nisha Ravikumar (N)

Anesthesia and Critical Care, Vardhman Mahavir Medical College and Safdarjung Hospital, New Delhi, IND.

Jayaram S (J)

Anesthesia and Critical Care, Vardhman Mahavir Medical College and Safdarjung Hospital, New Delhi, IND.

Classifications MeSH