Late Transformation of a Dermatofibrosarcoma Protuberans Neck Sarcoma to a Neoplasm With Fibrosarcomatous Elements: Lessons Learned.
dermatofibrosarcoma protuberans
fibrosarcoma
head and neck
neoplasm
oncology
Journal
Cureus
ISSN: 2168-8184
Titre abrégé: Cureus
Pays: United States
ID NLM: 101596737
Informations de publication
Date de publication:
Oct 2022
Oct 2022
Historique:
accepted:
26
10
2022
entrez:
2
12
2022
pubmed:
3
12
2022
medline:
3
12
2022
Statut:
epublish
Résumé
Dermatofibrosarcoma protuberans is a low-grade soft tissue sarcoma not often related to the head and neck area. Distant metastases are not often recorded. Wide surgical excision is considered the most appropriate treatment modality. In cases of insufficient or positive surgical margins, the role of adjuvant radiation therapy or targeted therapy might be beneficial. Dermatofibrosarcoma protuberans transformation to a neoplasm with fibrosarcomatous elements is extremely rare. The presence of fibrosarcomatous elements is associated with more aggressive behavior of the tumor and increases significantly its metastatic potential. We present a rare case of head and neck dermatofibrosarcoma protuberans with multiple local recurrences 13 years after the initial diagnosis.
Identifiants
pubmed: 36457621
doi: 10.7759/cureus.30690
pmc: PMC9704858
doi:
Types de publication
Case Reports
Langues
eng
Pagination
e30690Informations de copyright
Copyright © 2022, Poutoglidis et al.
Déclaration de conflit d'intérêts
The authors have declared that no competing interests exist.
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