Fetal Bradycardia Caused by Monogenic Disorders-A Review of the Literature.

arrhythmia bradycardia fetal genetics

Journal

Journal of clinical medicine
ISSN: 2077-0383
Titre abrégé: J Clin Med
Pays: Switzerland
ID NLM: 101606588

Informations de publication

Date de publication:
22 Nov 2022
Historique:
received: 14 10 2022
revised: 03 11 2022
accepted: 18 11 2022
entrez: 11 12 2022
pubmed: 12 12 2022
medline: 12 12 2022
Statut: epublish

Résumé

Introduction: The standard obstetric definition of fetal bradycardia is a sustained fetal heart rate < 110 bpm over at least 10 min. Fetal bradycardia can be the first and only prenatal presentation of a heart disease. We present an overview on different genetic disorders that should be taken into consideration in case of diagnosed fetal bradycardia. Methods: A literature review was conducted using a PubMed- and OMIM-based search for monogenetic disorders causing fetal bradycardia in September 2022. Results: The review on the literature identified nine monogenic diseases that could lead to fetal bradycardia. Four of these disorders can be associated with extracardiac findings. Discussion: Genetic testing should be considered in cases with fetal bradycardia, especially in cases of additional extracardiac findings. Broad sequencing techniques and improved prenatal phenotyping could help to establish a diagnosis in an increasing number of cases.

Identifiants

pubmed: 36498454
pii: jcm11236880
doi: 10.3390/jcm11236880
pmc: PMC9741304
pii:
doi:

Types de publication

Journal Article Review

Langues

eng

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Auteurs

Dominik S Westphal (DS)

Department of Internal Medicine I, Klinikum Rechts der Isar, School of Medicine and Health, Technical University Munich, 81675 Munich, Germany.
Institute of Human Genetics, Klinikum Rechts der Isar, School of Medicine and Health, Technical University Munich, 81675 Munich, Germany.

Michael Hauser (M)

Praxis für Kinderkardiologie, 80638 Munich, Germany.

Britt-Maria Beckmann (BM)

Institute of Legal Medicine, University Hospital Frankfurt, Goethe University, 60596 Frankfurt, Germany.

Cordula M Wolf (CM)

DZHK (German Centre for Cardiovascular Research), Partner Site Munich Heart Alliance, 80802 Munich, Germany.
Department of Congenital Heart Defects and Pediatric Cardiology, German Heart Center Munich, School of Medicine and Health, Technical University Munich, 80636 Munich, Germany.

Gabriele Hessling (G)

Department of Congenital Heart Defects and Pediatric Cardiology, German Heart Center Munich, School of Medicine and Health, Technical University Munich, 80636 Munich, Germany.

Renate Oberhoffer-Fritz (R)

Department of Congenital Heart Defects and Pediatric Cardiology, German Heart Center Munich, School of Medicine and Health, Technical University Munich, 80636 Munich, Germany.
Institute of Preventive Pediatrics, TUM Department of Sport and Health Sciences, Technical University Munich, 80992 Munich, Germany.

Annette Wacker-Gussmann (A)

Department of Congenital Heart Defects and Pediatric Cardiology, German Heart Center Munich, School of Medicine and Health, Technical University Munich, 80636 Munich, Germany.
Institute of Preventive Pediatrics, TUM Department of Sport and Health Sciences, Technical University Munich, 80992 Munich, Germany.

Classifications MeSH