Tissue Characterization in Cardiac Amyloidosis.
AL amyloidosis
abdominal fat tissue biopsy
cardiac amyloidosis
endomyocardial biopsy
histology
immunohistochemistry
mass spectrometry
transthyretin amyloidosis
Journal
Biomedicines
ISSN: 2227-9059
Titre abrégé: Biomedicines
Pays: Switzerland
ID NLM: 101691304
Informations de publication
Date de publication:
28 Nov 2022
28 Nov 2022
Historique:
received:
25
08
2022
revised:
14
11
2022
accepted:
18
11
2022
entrez:
23
12
2022
pubmed:
24
12
2022
medline:
24
12
2022
Statut:
epublish
Résumé
Cardiac amyloidosis (CA) has long been considered a rare disease, but recent advancements in diagnostic tools have led to a reconsideration of the epidemiology of CA. Amyloid light-chain (AL) and transthyretin (ATTR) amyloidoses are the most common forms of cardiac amyloidosis. Due to the distinct treatments and the different prognoses, amyloid typing is crucial. Although a non-biopsy diagnosis can be obtained in ATTR amyloidosis when certain diagnostic criteria are fulfilled, tissue characterization still represents the gold standard for the diagnosis and typing of CA, particularly in AL amyloidosis. The present review focuses on the status of tissue characterization in cardiac amyloidosis, from histochemistry to immunohistochemistry and mass spectrometry, as well as on its future directions.
Identifiants
pubmed: 36551810
pii: biomedicines10123054
doi: 10.3390/biomedicines10123054
pmc: PMC9775200
pii:
doi:
Types de publication
Journal Article
Review
Langues
eng
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