Genetically unresolved case of Rauch-Steindl syndrome diagnosed by its wolf-hirschhorn associated DNA methylation episignature.

DNA methylation epigenetics episignature molecular diagnostics neurodevelopmental disorders

Journal

Frontiers in cell and developmental biology
ISSN: 2296-634X
Titre abrégé: Front Cell Dev Biol
Pays: Switzerland
ID NLM: 101630250

Informations de publication

Date de publication:
2022
Historique:
received: 18 08 2022
accepted: 14 11 2022
entrez: 2 1 2023
pubmed: 3 1 2023
medline: 3 1 2023
Statut: epublish

Résumé

Wolf-Hirschhorn syndrome (WHS) is caused by deletion of a critical region of the short arm of chromosome 4. Clinical features of WHS include distinct dysmorphic facial features, growth restriction, developmental delay, intellectual disability, epilepsy, and other malformations. The

Identifiants

pubmed: 36589751
doi: 10.3389/fcell.2022.1022683
pii: 1022683
pmc: PMC9800036
doi:

Types de publication

Journal Article

Langues

eng

Pagination

1022683

Informations de copyright

Copyright © 2022 McConkey, White-Brown, Kerkhof, Dyment and Sadikovic.

Déclaration de conflit d'intérêts

The authors declare that the research was conducted in the absence of any commercial or financial relationships that could be construed as a potential conflict of interest.

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Auteurs

Haley McConkey (H)

Verspeeten Clinical Genome Centre, London Health Sciences Centre, London, ON, Canada.
Department of Pathology and Laboratory Medicine, Western University, London, ON, Canada.

Alexandre White-Brown (A)

Children's Hospital of Eastern Ontario Research Institute, University of Ottawa, Ottawa, ON, Canada.

Jennifer Kerkhof (J)

Verspeeten Clinical Genome Centre, London Health Sciences Centre, London, ON, Canada.

David Dyment (D)

Children's Hospital of Eastern Ontario Research Institute, University of Ottawa, Ottawa, ON, Canada.
Department of Genetics, Children's Hospital of Eastern Ontario, Ottawa, ON, Canada.

Bekim Sadikovic (B)

Verspeeten Clinical Genome Centre, London Health Sciences Centre, London, ON, Canada.
Department of Pathology and Laboratory Medicine, Western University, London, ON, Canada.

Classifications MeSH