Echocardiographic Evaluation in Paediatric Sickle Cell Disease Patients: A Pilot Study.
cardiovascular complications
echocardiography
paediatric population
sickle cell disease
Journal
Journal of clinical medicine
ISSN: 2077-0383
Titre abrégé: J Clin Med
Pays: Switzerland
ID NLM: 101606588
Informations de publication
Date de publication:
20 Dec 2022
20 Dec 2022
Historique:
received:
03
11
2022
revised:
11
12
2022
accepted:
12
12
2022
entrez:
8
1
2023
pubmed:
9
1
2023
medline:
9
1
2023
Statut:
epublish
Résumé
Cardiovascular involvement has a great impact on morbidity and mortality in sickle cell disease (SCD). Currently, few studies are available regarding the paediatric setting and, moreover, current guidelines for the echocardiogram screening program in the asymptomatic paediatric population are controversial. We performed a retrospective observational monocentric study on 64 SCD patients (37 male and 27 female, median age 10) at the Bambino Gesù Childrens' Hospital, who had undergone a routine transthoracic echocardiogram. In total, 46 (72%) patients had at least one cardiac abnormality. Left atrial dilatation (LAD) was present in 41 (65%) patients and left ventricular hypertrophy (LVH) was found in 29 (45%) patients. Patients with LAD showed lower median haemoglobin levels (
Identifiants
pubmed: 36614810
pii: jcm12010007
doi: 10.3390/jcm12010007
pmc: PMC9821745
pii:
doi:
Types de publication
Journal Article
Langues
eng
Subventions
Organisme : Italian ministry of health
ID : Current research fund
Références
Blood. 2004 Mar 1;103(5):1934-6
pubmed: 14630822
J Am Soc Echocardiogr. 2016 Apr;29(4):277-314
pubmed: 27037982
Blood. 2011 Mar 3;117(9):2614-7
pubmed: 21217080
J Thromb Haemost. 2013 Dec;11(12):2148-54
pubmed: 24119131
Lancet. 2013 Jan 12;381(9861):142-51
pubmed: 23103089
Exp Biol Med (Maywood). 2016 Apr;241(7):679-88
pubmed: 27013545
Lancet. 2010 Dec 11;376(9757):2018-31
pubmed: 21131035
Am J Hematol. 2002 Aug;70(4):306-12
pubmed: 12210812
Intern Med J. 2004 Apr;34(4):214-6
pubmed: 15086707
Thromb Haemost. 2005 Mar;93(3):512-6
pubmed: 15735803
Blood. 2014 Jan 16;123(3):377-90
pubmed: 24277079
N Engl J Med. 2011 Jul 7;365(1):44-53
pubmed: 21732836
Mediterr J Hematol Infect Dis. 2012;4(1):e2012065
pubmed: 23170194
Nat Rev Dis Primers. 2018 Mar 15;4:18010
pubmed: 29542687
Adv Protein Chem. 1990;40:63-279
pubmed: 2195851
Ann N Y Acad Sci. 2016 Mar;1368(1):56-64
pubmed: 26963698
PLoS One. 2013 Aug 07;8(8):e70794
pubmed: 23951011
Br J Haematol. 2011 Aug;154(4):512-20
pubmed: 21689089
Blood. 1985 Jan;65(1):183-9
pubmed: 3965046
Blood. 2009 Oct 1;114(14):2861-8
pubmed: 19636061
Rev Bras Hematol Hemoter. 2015 Sep-Oct;37(5):324-8
pubmed: 26408367
Pediatr Hematol Oncol. 2007 Apr-May;24(3):159-70
pubmed: 17454785
Am J Respir Crit Care Med. 2014 Mar 15;189(6):727-40
pubmed: 24628312
JACC Cardiovasc Imaging. 2016 Mar;9(3):243-52
pubmed: 26897687
Br J Haematol. 2012 Jun;157(6):664-73
pubmed: 22530942
Blood. 2007 Sep 15;110(6):2166-72
pubmed: 17536019
Br J Haematol. 2019 Jan;184(2):253-262
pubmed: 30467843
Blood Adv. 2019 Dec 10;3(23):3867-3897
pubmed: 31794601
J Am Coll Cardiol. 2007 Jan 30;49(4):472-9
pubmed: 17258093
Pediatr Cardiol. 2019 Dec;40(8):1670-1678
pubmed: 31542803
Blood Adv. 2020 Apr 28;4(8):1554-1588
pubmed: 32298430
Blood. 2014 Jun 12;123(24):3689-90
pubmed: 24926069
Blood. 2017 Nov 16;130(20):2215-2223
pubmed: 28931524
Eur J Echocardiogr. 2011 Mar;12(3):167-205
pubmed: 21385887
J Am Soc Echocardiogr. 2016 Mar;29(3):209-225.e6
pubmed: 26747685
Echocardiography. 2018 Sep;35(9):1271-1276
pubmed: 29756358
Br J Haematol. 2018 Dec;183(5):796-806
pubmed: 30450553
Eur Heart J. 2022 Sep 14;43(35):3290-3301
pubmed: 35896123
Front Mol Biosci. 2019 Dec 05;6:140
pubmed: 31867340
N Engl J Med. 1997 Sep 11;337(11):762-9
pubmed: 9287233
Proc Natl Acad Sci U S A. 2002 Mar 5;99(5):3047-51
pubmed: 11880644
Lancet. 2016 Jun 18;387(10037):2565-74
pubmed: 27353687
Am J Hematol. 2014 Sep;89(9):904-6
pubmed: 24891147
Ann Neurol. 1997 Nov;42(5):699-704
pubmed: 9392568
Thromb Res. 2008;122(5):599-603
pubmed: 18334267
J Card Fail. 2013 May;19(5):333-41
pubmed: 23663816
Br J Haematol. 2014 Jul;166(2):165-76
pubmed: 24862308
Cardiol Young. 2017 Jul;27(5):918-924
pubmed: 27839523
J Am Soc Echocardiogr. 2008 Oct;21(10):1163-7
pubmed: 18926392
Circulation. 2011 Sep 27;124(13):1452-60
pubmed: 21900080
Am J Hematol. 2022 Nov;97(11):E385-E388
pubmed: 36056794
Circ Cardiovasc Imaging. 2012 Nov;5(6):791-6
pubmed: 23074344
J Am Soc Echocardiogr. 2014 Dec;27(12):1279-92.e2
pubmed: 25240494
Pediatr Blood Cancer. 2011 Jan;56(1):116-21
pubmed: 20949593
Blood. 2016 Sep 8;128(10):1436-8
pubmed: 27439910
Pediatr Res. 2022 Jun;91(7):1709-1714
pubmed: 34903834
Hematology Am Soc Hematol Educ Program. 2017 Dec 8;2017(1):423-430
pubmed: 29222288
Hypertension. 2005 Jan;45(1):64-8
pubmed: 15557389
Am J Hematol. 2010 Oct;85(10):831-3
pubmed: 20872960
Echocardiography. 2011 Feb;28(2):175-80
pubmed: 20738369
Curr Opin Hematol. 2002 Mar;9(2):101-6
pubmed: 11844991
Am J Cardiol. 1986 Feb 15;57(6):450-8
pubmed: 2936235
N Engl J Med. 1998 Jul 2;339(1):5-11
pubmed: 9647873
J Am Soc Echocardiogr. 2010 May;23(5):465-95; quiz 576-7
pubmed: 20451803
Am J Hematol. 2007 Jun;82(6):433-8
pubmed: 17266053
J Pediatr. 2016 Mar;170:193-8
pubmed: 26670053
Cardiovasc J Afr. 2007 Mar-Apr;18(2):84-9
pubmed: 17497044