Gathering the Stakeholder's Perspective: Experiences and Opportunities in Rare Genetic Disease Research.

22q11.2 deletion syndrome copy number variations (CNVs) neurodevelopmental psychiatric disorders (NPDs)

Journal

Genes
ISSN: 2073-4425
Titre abrégé: Genes (Basel)
Pays: Switzerland
ID NLM: 101551097

Informations de publication

Date de publication:
07 01 2023
Historique:
received: 03 11 2022
revised: 22 12 2022
accepted: 03 01 2023
entrez: 21 1 2023
pubmed: 22 1 2023
medline: 25 1 2023
Statut: epublish

Résumé

Research participant feedback is rarely collected; therefore, investigators have limited understanding regarding stakeholders' (affected individuals/caregivers) motivation to participate. Members of the Genes to Mental Health Network (G2MH) surveyed stakeholders affected by copy number variants (CNVs) regarding perceived incentives for study participation, opinions concerning research priorities, and the necessity for future funding. Respondents were also asked about feelings of preparedness, research burden, and satisfaction with research study participation. Modified validated surveys were used to assess stakeholders´ views across three domains: (1) Research Study Enrollment, Retainment, Withdrawal, and Future Participation; (2) Overall Research Experience, Burden, and Preparedness; (3) Research Priorities and Obstacles. Top box score analyses were performed. A total of 704 stakeholders´ responded from 29 countries representing 55 CNVs. The top reasons for initial participation in the research included reasons related to education and altruism. The top reasons for leaving a research study included treatment risks and side effects. The importance of sharing research findings and laboratory results with stakeholders was underscored by participants. Most stakeholders reported positive research experiences. This study provides important insight into how individuals and families affected with a rare CNV feel toward research participation and their overall experience in rare disease research. There are clear targets for areas of improvement for study teams, although many stakeholders reported positive research experiences. Key findings from this international survey may help advance collaborative research and improve the experience of participants, investigators, and other stakeholders moving forward.

Sections du résumé

BACKGROUND
Research participant feedback is rarely collected; therefore, investigators have limited understanding regarding stakeholders' (affected individuals/caregivers) motivation to participate. Members of the Genes to Mental Health Network (G2MH) surveyed stakeholders affected by copy number variants (CNVs) regarding perceived incentives for study participation, opinions concerning research priorities, and the necessity for future funding. Respondents were also asked about feelings of preparedness, research burden, and satisfaction with research study participation.
METHODS
Modified validated surveys were used to assess stakeholders´ views across three domains: (1) Research Study Enrollment, Retainment, Withdrawal, and Future Participation; (2) Overall Research Experience, Burden, and Preparedness; (3) Research Priorities and Obstacles. Top box score analyses were performed.
RESULTS
A total of 704 stakeholders´ responded from 29 countries representing 55 CNVs. The top reasons for initial participation in the research included reasons related to education and altruism. The top reasons for leaving a research study included treatment risks and side effects. The importance of sharing research findings and laboratory results with stakeholders was underscored by participants. Most stakeholders reported positive research experiences.
CONCLUSIONS
This study provides important insight into how individuals and families affected with a rare CNV feel toward research participation and their overall experience in rare disease research. There are clear targets for areas of improvement for study teams, although many stakeholders reported positive research experiences. Key findings from this international survey may help advance collaborative research and improve the experience of participants, investigators, and other stakeholders moving forward.

Identifiants

pubmed: 36672911
pii: genes14010169
doi: 10.3390/genes14010169
pmc: PMC9859499
pii:
doi:

Types de publication

Journal Article Research Support, N.I.H., Extramural

Langues

eng

Sous-ensembles de citation

IM

Subventions

Organisme : NICHD NIH HHS
ID : R13 HD103471
Pays : United States
Organisme : NIMH NIH HHS
ID : U01 MH119705
Pays : United States
Organisme : NIH HHS
ID : MH 1U01MH119738
Pays : United States

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Auteurs

Lauren K White (LK)

Children's Hospital of Philadelphia, Philadelphia, PA 19104, USA.
Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA 19104, USA.

T Blaine Crowley (TB)

Children's Hospital of Philadelphia, Philadelphia, PA 19104, USA.

Brenda Finucane (B)

Geisinger Medical Center, Danville, PA 17821, USA.

Emily J McClellan (EJ)

Children's Hospital of Philadelphia, Philadelphia, PA 19104, USA.
Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA 19104, USA.

Sarah Donoghue (S)

Children's Hospital of Philadelphia, Philadelphia, PA 19104, USA.

Sixto Garcia-Minaur (S)

Institute of Medical and Molecular Genetics (INGEMM), La Paz University Hospital, 28046 Madrid, Spain.

Gabriela M Repetto (GM)

Clinic Aldemana, University for Development, Santiago 7690000, Chile.

Matthias Fischer (M)

Clinic and Policlinic for Psychiatry and Psychotherapy, University of Rostock, 18147 Rostock, Germany.
Sigma-Zentrum, 79713 Bad Säckingen, Germany.

Sebastien Jacquemont (S)

Sainte Justine Research Center, University of Montreal, Montreal, QC H3T 1J4, Canada.

Raquel E Gur (RE)

Children's Hospital of Philadelphia, Philadelphia, PA 19104, USA.
Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA 19104, USA.

Anne M Maillard (AM)

Lausanne University Hospital, 1011 Lausanne, Switzerland.

Kirsten A Donald (KA)

Department of Paediatrics and Child Health, Red Cross War Memorial Children's Hospital, Rondebosch, Cape Town 7700, South Africa.
Neuroscience Institute, University of Cape Town, Cape Town 7935, South Africa.

Anne S Bassett (AS)

The Dalglish Family 22q Clinic, University Health Network, Toronto, ON M5G 2C4, Canada.
Clinical Genetics Research Program and Campbell Family Mental Health Research Institute, Centre for Addiction and Mental Health, and Department of Psychiatry, University of Toronto, Toronto, ON M5S 2S1, Canada.
Division of Cardiology, Department of Medicine, and Centre for Mental Health, and Toronto General Hospital Research Institute, University Health Network, Toronto, ON M5G 2N2, Canada.

Ann Swillen (A)

Center for Human Genetics, University Hospital UZ Leuven, and Department of Human Genetics, KU Leuven, 3000 Leuven, Belgium.

Donna M McDonald-McGinn (DM)

Children's Hospital of Philadelphia, Philadelphia, PA 19104, USA.
Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA 19104, USA.
Department of Human Biology and Medical Genetics, Sapienza University, 00185 Roma, Italy.

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