Small heat shock proteins operate as molecular chaperones in the mitochondrial intermembrane space.


Journal

Nature cell biology
ISSN: 1476-4679
Titre abrégé: Nat Cell Biol
Pays: England
ID NLM: 100890575

Informations de publication

Date de publication:
03 2023
Historique:
received: 20 10 2021
accepted: 12 12 2022
pubmed: 24 1 2023
medline: 17 3 2023
entrez: 23 1 2023
Statut: ppublish

Résumé

Mitochondria are complex organelles with different compartments, each harbouring their own protein quality control factors. While chaperones of the mitochondrial matrix are well characterized, it is poorly understood which chaperones protect the mitochondrial intermembrane space. Here we show that cytosolic small heat shock proteins are imported under basal conditions into the mitochondrial intermembrane space, where they operate as molecular chaperones. Protein misfolding in the mitochondrial intermembrane space leads to increased recruitment of small heat shock proteins. Depletion of small heat shock proteins leads to mitochondrial swelling and reduced respiration, while aggregation of aggregation-prone substrates is countered in their presence. Charcot-Marie-Tooth disease-causing mutations disturb the mitochondrial function of HSPB1, potentially linking previously observed mitochondrial dysfunction in Charcot-Marie-Tooth type 2F to its role in the mitochondrial intermembrane space. Our results reveal that small heat shock proteins form a chaperone system that operates in the mitochondrial intermembrane space.

Identifiants

pubmed: 36690850
doi: 10.1038/s41556-022-01074-9
pii: 10.1038/s41556-022-01074-9
pmc: PMC10014586
doi:

Substances chimiques

Heat-Shock Proteins, Small 0
Molecular Chaperones 0
Mitochondrial Proteins 0

Types de publication

Journal Article Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

467-480

Informations de copyright

© 2023. The Author(s).

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Auteurs

Elias Adriaenssens (E)

Peripheral Neuropathy Research Group, Department of Biomedical Sciences, University of Antwerp, Antwerp, Belgium.
Laboratory of Neuromuscular Pathology, Institute Born Bunge, Antwerp, Belgium.

Bob Asselbergh (B)

Neuromics Support Facility, VIB Center for Molecular Neurology, University of Antwerp, Antwerp, Belgium.
Neuromics Support Facility, Department of Biomedical Sciences, University of Antwerp, Antwerp, Belgium.

Pablo Rivera-Mejías (P)

Max Planck Institute for Biology of Ageing, Cologne, Germany.

Sven Bervoets (S)

VIB Center for Molecular Neurology, University of Antwerp, Antwerp, Belgium.

Leen Vendredy (L)

Peripheral Neuropathy Research Group, Department of Biomedical Sciences, University of Antwerp, Antwerp, Belgium.
Laboratory of Neuromuscular Pathology, Institute Born Bunge, Antwerp, Belgium.

Vicky De Winter (V)

Peripheral Neuropathy Research Group, Department of Biomedical Sciences, University of Antwerp, Antwerp, Belgium.
Laboratory of Neuromuscular Pathology, Institute Born Bunge, Antwerp, Belgium.

Katrien Spaas (K)

Neuromics Support Facility, VIB Center for Molecular Neurology, University of Antwerp, Antwerp, Belgium.
Neuromics Support Facility, Department of Biomedical Sciences, University of Antwerp, Antwerp, Belgium.

Riet de Rycke (R)

VIB Bioimaging Core, Ghent University, Ghent, Belgium.
Department of Biomedical Molecular Biology, Ghent University, Ghent, Belgium.
VIB Center for Inflammation Research, Ghent, Belgium.

Gert van Isterdael (G)

Department of Biomedical Molecular Biology, Ghent University, Ghent, Belgium.
VIB Center for Inflammation Research, Ghent, Belgium.
VIB Flow Core, Ghent, Belgium.

Francis Impens (F)

VIB-UGent Center for Medical Biotechnology, VIB, Ghent, Belgium.
VIB Proteomics Core, VIB, Ghent, Belgium.
Department of Biomolecular Medicine, Ghent University, Ghent, Belgium.

Thomas Langer (T)

Max Planck Institute for Biology of Ageing, Cologne, Germany.
Cologne Excellence Cluster on Cellular Stress Responses in Aging-Associated Diseases (CECAD), University of Cologne, Cologne, Germany.

Vincent Timmerman (V)

Peripheral Neuropathy Research Group, Department of Biomedical Sciences, University of Antwerp, Antwerp, Belgium. vincent.timmerman@uantwerpen.be.
Laboratory of Neuromuscular Pathology, Institute Born Bunge, Antwerp, Belgium. vincent.timmerman@uantwerpen.be.

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