Inhibitory synapse dysfunction and epileptic susceptibility associated with KIF2A deletion in cortical interneurons.

epilepsy inhibitory synapses interneuron microtubules tangential migration

Journal

Frontiers in molecular neuroscience
ISSN: 1662-5099
Titre abrégé: Front Mol Neurosci
Pays: Switzerland
ID NLM: 101477914

Informations de publication

Date de publication:
2022
Historique:
received: 29 11 2022
accepted: 30 12 2022
entrez: 3 2 2023
pubmed: 4 2 2023
medline: 4 2 2023
Statut: epublish

Résumé

Malformation of cortical development (MCD) is a family of neurodevelopmental disorders, which usually manifest with intellectual disability and early-life epileptic seizures. Mutations in genes encoding microtubules (MT) and MT-associated proteins are one of the most frequent causes of MCD in humans. KIF2A is an atypical kinesin that depolymerizes MT in ATP-dependent manner and regulates MT dynamics. In humans, single

Identifiants

pubmed: 36733270
doi: 10.3389/fnmol.2022.1110986
pmc: PMC9887042
doi:

Types de publication

Journal Article

Langues

eng

Pagination

1110986

Informations de copyright

Copyright © 2023 Ruiz-Reig, García-Sánchez, Schakman, Gailly and Tissir.

Déclaration de conflit d'intérêts

The authors declare that the research was conducted in the absence of any commercial or financial relationships that could be construed as a potential conflict of interest.

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Auteurs

Nuria Ruiz-Reig (N)

Institute of Neuroscience, Université catholique de Louvain, Brussels, Belgium.

Dario García-Sánchez (D)

Institute of Neuroscience, Université catholique de Louvain, Brussels, Belgium.

Olivier Schakman (O)

Institute of Neuroscience, Université catholique de Louvain, Brussels, Belgium.

Philippe Gailly (P)

Institute of Neuroscience, Université catholique de Louvain, Brussels, Belgium.

Fadel Tissir (F)

Institute of Neuroscience, Université catholique de Louvain, Brussels, Belgium.
College of Health and Life Sciences, Hamad Bin Khalifa University, Doha, Qatar.

Classifications MeSH