Keeping you on your toes: Smith-Lemli-Opitz Syndrome is an easily missed cause of developmental delays.

7‐Dehydrocholesterol biochemical genetics diagnosis metabolism smith–lemli–opitz syndrome

Journal

Clinical case reports
ISSN: 2050-0904
Titre abrégé: Clin Case Rep
Pays: England
ID NLM: 101620385

Informations de publication

Date de publication:
Feb 2023
Historique:
received: 24 06 2022
revised: 10 10 2022
accepted: 28 12 2022
entrez: 23 2 2023
pubmed: 24 2 2023
medline: 24 2 2023
Statut: epublish

Résumé

Smith-Lemli-Opitz syndrome (SLOS) is a relatively common genetic cause of developmental delay and may only present in conjunction with 2,3 toe syndactyly. This case series illustrates a milder phenotype of SLOS, where the predominant findings are neurocognitive in the presence of 2,3 toe syndactyly.

Identifiants

pubmed: 36814711
doi: 10.1002/ccr3.6920
pii: CCR36920
pmc: PMC9939576
doi:

Types de publication

Case Reports

Langues

eng

Pagination

e6920

Informations de copyright

© 2023 The Authors. Clinical Case Reports published by John Wiley & Sons Ltd.

Déclaration de conflit d'intérêts

No authors have any conflicts of interest to disclose.

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Auteurs

Simone Coupe (S)

NSW Biochemical Genetics Service The Children's Hospital at Westmead Westmead New South Wales Australia.

Ashley Hertzog (A)

NSW Biochemical Genetics Service The Children's Hospital at Westmead Westmead New South Wales Australia.
Faculty of Medicine and Health University of Sydney Westmead New South Wales Australia.

Carolyn Foran (C)

NSW Biochemical Genetics Service The Children's Hospital at Westmead Westmead New South Wales Australia.

Adviye Ayper Tolun (AA)

NSW Biochemical Genetics Service The Children's Hospital at Westmead Westmead New South Wales Australia.
Faculty of Medicine and Health University of Sydney Westmead New South Wales Australia.

Megan Suthern (M)

Paediatric Department Wagga Wagga Base Hospital Wagga Wagga New South Wales Australia.
Rural Clinical School, Faculty of Medicine and Health University of New South Wales Wagga Wagga New South Wales Australia.

Clara W T Chung (CWT)

Department of Clinical Genetics Liverpool Hospital Liverpool New South Wales Australia.
School of Women's and Children's Health University of New South Wales Sydney New South Wales Australia.

Carolyn Ellaway (C)

Faculty of Medicine and Health University of Sydney Westmead New South Wales Australia.
Genetic Metabolic Disorders Service The Children's Hospital at Westmead Westmead New South Wales Australia.

Classifications MeSH