T-cell dysregulation and inflammatory process in


Journal

American journal of physiology. Lung cellular and molecular physiology
ISSN: 1522-1504
Titre abrégé: Am J Physiol Lung Cell Mol Physiol
Pays: United States
ID NLM: 100901229

Informations de publication

Date de publication:
01 05 2023
Historique:
medline: 17 4 2023
pubmed: 1 3 2023
entrez: 28 2 2023
Statut: ppublish

Résumé

Hereditary pulmonary veno-occlusive disease (hPVOD) is a severe form of autosomal recessive pulmonary hypertension and is due to biallelic loss of function of the

Identifiants

pubmed: 36852942
doi: 10.1152/ajplung.00460.2021
doi:

Substances chimiques

Protein Serine-Threonine Kinases EC 2.7.11.1
RNA, Messenger 0
Eif2ak4 protein, rat EC 2.7.-

Banques de données

figshare
['10.6084/m9.figshare.22067858']

Types de publication

Journal Article Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

L609-L624

Auteurs

Juliette Bignard (J)

UMR_S 1166, Sorbonne Université, INSERM, Paris, France.

Fabrice Atassi (F)

UMR_S 1166, Sorbonne Université, INSERM, Paris, France.

Olivier Claude (O)

UMR_S 1166, Sorbonne Université, INSERM, Paris, France.

Maria-Rosa Ghigna (MR)

Department of Pathology, Institut Gustave Roussy, Villejuif, France.
UMR_S999, Université Paris-Saclay, INSERM, Hôpital Marie Lannelongue, Le Plessis Robinson, France.

Nathalie Mougenot (N)

UMS28, Sorbonne Université, Plateforme d'Expérimentation Cœur, Muscles, Vaisseaux (PECMV), Paris, France.

Bahgat Soilih Abdoulkarim (BS)

UMR_S999, Université Paris-Saclay, INSERM, Hôpital Marie Lannelongue, Le Plessis Robinson, France.

Florence Deknuydt (F)

Flow Cytometry Core Cyto-ICAN, Institute of Cardiometabolism and Nutrition, Hôpital Pitié-Salpêtrière, Paris, France.

Aurélie Gestin (A)

Flow Cytometry Core Cyto-ICAN, Institute of Cardiometabolism and Nutrition, Hôpital Pitié-Salpêtrière, Paris, France.

Virginie Monceau (V)

UMR_S 1166, Sorbonne Université, INSERM, Paris, France.

David Montani (D)

UMR_S999, Université Paris-Saclay, INSERM, Hôpital Marie Lannelongue, Le Plessis Robinson, France.
Service de Pneumologie et Soins Intensifs Respiratoires, Hôpital de Bicêtre, Assistance Publique Hôpitaux de paris, Le Kremlin Bicêtre, France.

Sophie Nadaud (S)

UMR_S 1166, Sorbonne Université, INSERM, Paris, France.

Florent Soubrier (F)

UMR_S 1166, Sorbonne Université, INSERM, Paris, France.

Frédéric Perros (F)

UMR_S999, Université Paris-Saclay, INSERM, Hôpital Marie Lannelongue, Le Plessis Robinson, France.
Laboratoire CarMeN, UMR INSERM U1060/INRA U1397, Université Claude Bernard Lyon1, Pierre-Bénite and Bron, France.

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Classifications MeSH