Immune dysregulation in Glycogen Storage Disease 1b - a CyTOF approach.

CyTOF GSD1b immunity immunodeficiency immunometabolism neutropenia

Journal

Research square
Titre abrégé: Res Sq
Pays: United States
ID NLM: 101768035

Informations de publication

Date de publication:
23 Feb 2023
Historique:
pubmed: 4 3 2023
medline: 4 3 2023
entrez: 3 3 2023
Statut: epublish

Résumé

Glycogen Storage Disease type 1b (GSD1b) is a rare disease manifesting as hypoglycemia, recurrent infections and neutropenia, resulting from deleterious mutations in the

Identifiants

pubmed: 36865166
doi: 10.21203/rs.3.rs-2598829/v1
pmc: PMC9980199
pii:
doi:

Types de publication

Preprint

Langues

eng

Déclaration de conflit d'intérêts

Competing interests The authors have no relevant financial or non-financial interests to disclose.

Auteurs

Arne Gehlhaar (A)

Yale University School of Medicine.

Dror Shouval (D)

Yale University School of Medicine.

Eduardo Gonzalez Santiago (EG)

Yale University School of Medicine.

Galina Ling (G)

Yale University School of Medicine.

Blake McCourt (B)

Yale University School of Medicine.

Lael Werner (L)

Yale University School of Medicine.

Baruch Yerushalmi (B)

Yale University School of Medicine.

Liza Konnikova (L)

Yale University School of Medicine.

Classifications MeSH