Comparison of the structure-function properties of wild-type human apoA-V and a C-terminal truncation associated with elevated plasma triglycerides.

APOA5 TRL metabolism apolipoprotein triglyceride metabolism

Journal

medRxiv : the preprint server for health sciences
Titre abrégé: medRxiv
Pays: United States
ID NLM: 101767986

Informations de publication

Date de publication:
23 Feb 2023
Historique:
pubmed: 4 3 2023
medline: 4 3 2023
entrez: 3 3 2023
Statut: epublish

Résumé

Plasma triglycerides (TGs) are causally associated with coronary artery disease and acute pancreatitis. Apolipoprotein A-V (apoA-V, gene We used hydrogen-deuterium exchange mass spectrometry to determine the secondary structure of human apoA-V in lipid-free and lipid-associated conditions and identified a C-terminal hydrophobic face. Then, we used genomic data in the Penn Medicine Biobank to identify a rare variant, Q252X, predicted to specifically eliminate this region. We interrogated the function of apoA-V Q252X using recombinant protein Human apoA-V Q252X carriers exhibited elevated plasma TG levels consistent with loss of function. Deletion of apoA-V's C-terminus leads to reduced apoA-V bioavailability

Sections du résumé

Background UNASSIGNED
Plasma triglycerides (TGs) are causally associated with coronary artery disease and acute pancreatitis. Apolipoprotein A-V (apoA-V, gene
Methods UNASSIGNED
We used hydrogen-deuterium exchange mass spectrometry to determine the secondary structure of human apoA-V in lipid-free and lipid-associated conditions and identified a C-terminal hydrophobic face. Then, we used genomic data in the Penn Medicine Biobank to identify a rare variant, Q252X, predicted to specifically eliminate this region. We interrogated the function of apoA-V Q252X using recombinant protein
Results UNASSIGNED
Human apoA-V Q252X carriers exhibited elevated plasma TG levels consistent with loss of function.
Conclusions UNASSIGNED
Deletion of apoA-V's C-terminus leads to reduced apoA-V bioavailability

Identifiants

pubmed: 36865344
doi: 10.1101/2023.02.21.23286268
pmc: PMC9980232
pii:
doi:

Types de publication

Preprint

Langues

eng

Auteurs

Sylvia Stankov (S)

Division of Translational Medicine and Human Genetics, Department of Medicine, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, USA.

Cecilia Vitali (C)

Division of Translational Medicine and Human Genetics, Department of Medicine, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, USA.

Joseph Park (J)

Division of Translational Medicine and Human Genetics, Department of Medicine, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, USA.

David Nguyen (D)

Johnson Research Foundation, Department of Biochemistry and Biophysics, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, USA.

Leland Mayne (L)

Johnson Research Foundation, Department of Biochemistry and Biophysics, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, USA.

S Walter Englander (SW)

Johnson Research Foundation, Department of Biochemistry and Biophysics, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, USA.

Michael G Levin (MG)

Division of Cardiovascular Medicine, Department of Medicine, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA.
Corporal Michael J. Crescenz VA Medical Center, Philadelphia, PA.

Marijana Vujkovic (M)

Division of Translational Medicine and Human Genetics, Department of Medicine, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, USA.
Corporal Michael J. Crescenz VA Medical Center, Philadelphia, PA.

Nicholas J Hand (NJ)

Department of Genetics, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, USA.

Michael C Phillips (MC)

Division of Translational Medicine and Human Genetics, Department of Medicine, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, USA.

Daniel J Rader (DJ)

Division of Translational Medicine and Human Genetics, Department of Medicine, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, USA.
Department of Genetics, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, USA.

Classifications MeSH