Crohn's Disease-Like Features in a Patient With IgE and Selective IgG1 and IgG3 Deficiency.

crohn’s disease crohn’s-like disease ige deficiency primary immune deficiency primary immunodeficiency selective igg deficiency

Journal

Cureus
ISSN: 2168-8184
Titre abrégé: Cureus
Pays: United States
ID NLM: 101596737

Informations de publication

Date de publication:
Feb 2023
Historique:
accepted: 05 02 2023
entrez: 10 3 2023
pubmed: 11 3 2023
medline: 11 3 2023
Statut: epublish

Résumé

We report a 19-year-old male with congenital, combined deficiency of immunoglobulin (Ig) E and 2/4 subclasses of IgG (G1, G3) and chronic diarrhea. He presented at six years of age with chronic recurrent diarrhea responsive to immunoglobulin treatment. Initially, it was considered of infectious origin. However, at the age of 14 years, ileocolonoscopy and magnetic resonance enterography (MRE) were performed, and they showed a mild, limited, non-specific, terminal ileitis with increased eosinophil count on histology. A diagnosis of possible eosinophilic gastroenteritis was made, and budesonide was administered with temporary relief. However, at the age of 19 years, repeat ileocolonoscopy showed multiple ulcers in the terminal ileum and aphthous ulcers in the cecum, and repeat MRE demonstrated extensive ileal involvement. Esophagogastroduodenoscopy demonstrated the involvement of the upper GI tract with aphthous ulcers. Subsequently, gastric, ileal, and colonic biopsies revealed Ziehl-Neelsen-negative, non-caseating granulomas. We hereby report the first case of IgE and selective IgG1 and IgG3 deficiency complicated with Crohn's disease-like extensive GI involvement.

Identifiants

pubmed: 36895538
doi: 10.7759/cureus.34655
pmc: PMC9991486
doi:

Types de publication

Case Reports

Langues

eng

Pagination

e34655

Informations de copyright

Copyright © 2023, Drygiannakis et al.

Déclaration de conflit d'intérêts

The authors have declared that no competing interests exist.

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Auteurs

Ioannis Drygiannakis (I)

Department of Gastroenterology, University General Hospital of Heraklion, Heraklion, GRC.

Eirini Theodoraki (E)

Department of Gastroenterology, University General Hospital of Heraklion, Heraklion, GRC.

Maria Tsafaridou (M)

Department of Gastroenterology, University General Hospital of Heraklion, Heraklion, GRC.

Ioannis Koutroubakis (I)

Department of Gastroenterology, University General Hospital of Heraklion, Heraklion, GRC.

Classifications MeSH