A case of vanishing gastroschisis with short bowel syndrome treated by total parenteral nutrition and intestinal lengthening procedures.

Gastroschisis neonate short bowel syndrome

Journal

SAGE open medical case reports
ISSN: 2050-313X
Titre abrégé: SAGE Open Med Case Rep
Pays: England
ID NLM: 101638686

Informations de publication

Date de publication:
2023
Historique:
received: 19 11 2022
accepted: 29 01 2023
entrez: 10 3 2023
pubmed: 11 3 2023
medline: 11 3 2023
Statut: epublish

Résumé

The diagnosis of vanishing gastroschisis is made when in the presence of a full-thickness intrauterine abdominal wall defect the eviscerated loops are incarcerated in the fascial interruption. Four types of vanishing gastroschisis are described (A-D). We report on the case of a newborn with a vanishing gastroschisis-D. Gastroschisis was diagnosed at the 19th week of gestation, confirmed at the 30th, when the herniated loops previously visible to the right of the funiculus were no longer visualized. At the 32nd week, delivery was induced. The neonate weighed 1600 g, and the abdomen was distended, free from skin defects. On surgical exploration, the jejunum was 13 cm in length, with a blind ending. The post-atretic intestine measured 22 cm. A jejunostomy and a colostomy were built. The child received total parenteral nutrition for 13 months due to short bowel syndrome and was then subjected to intestinal lengthening procedure when she was 18 months old. Vanishing gastroschisis is a rare entity with a worse prognosis of the "classic" gastroschisis.

Identifiants

pubmed: 36896328
doi: 10.1177/2050313X231157490
pii: 10.1177_2050313X231157490
pmc: PMC9989415
doi:

Types de publication

Case Reports

Langues

eng

Pagination

2050313X231157490

Informations de copyright

© The Author(s) 2023.

Déclaration de conflit d'intérêts

The author(s) declared no potential conflicts of interest with respect to the research, authorship, and/or publication of this article.

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Auteurs

Riccardo Guanà (R)

Pediatric Surgery Unit, University Hospital of Health and Science, Regina Margherita Children's Hospital, Turin, Italy.
Division of Pediatric General, Thoracic, Neonatal & Minimally Invasive Surgery, Regina Margherita Children's Hospital, Turin, Italy.

Lucia Marocco (L)

Post-graduate School of Pediatrics, Regina Margherita Children's Hospital, University of Turin, Turin, Italy.

Salvatore Garofalo (S)

Pediatric Surgery Unit, University Hospital of Health and Science, Regina Margherita Children's Hospital, Turin, Italy.

Elisa Zambaiti (E)

Pediatric Surgery Unit, University Hospital of Health and Science, Regina Margherita Children's Hospital, Turin, Italy.

Alessandro Pane (A)

Pediatric Surgery Unit, University Hospital of Health and Science, Regina Margherita Children's Hospital, Turin, Italy.

Federico Scottoni (F)

Pediatric Surgery Unit, University Hospital of Health and Science, Regina Margherita Children's Hospital, Turin, Italy.

Fabio Fusaro (F)

Bambino Gesù Children's Hospital, Rome, Italy.

Giulia Perucca (G)

Pediatric Radiology Unit, Great Ormond Street Hospital, London, UK.

Fabrizio Gennari (F)

Pediatric Surgery Unit, University Hospital of Health and Science, Regina Margherita Children's Hospital, Turin, Italy.

Classifications MeSH