Genetic forms of primary progressive aphasia within the GENetic Frontotemporal dementia Initiative (GENFI) cohort: comparison with sporadic primary progressive aphasia.

GRN MAPT c9orf72 primary progressive aphasia

Journal

Brain communications
ISSN: 2632-1297
Titre abrégé: Brain Commun
Pays: England
ID NLM: 101755125

Informations de publication

Date de publication:
2023
Historique:
received: 04 03 2022
revised: 26 08 2022
accepted: 15 02 2023
entrez: 20 3 2023
pubmed: 21 3 2023
medline: 21 3 2023
Statut: epublish

Résumé

Primary progressive aphasia is most commonly a sporadic disorder, but in some cases, it can be genetic. This study aimed to understand the clinical, cognitive and imaging phenotype of the genetic forms of primary progressive aphasia in comparison to the canonical nonfluent, semantic and logopenic subtypes seen in sporadic disease. Participants with genetic primary progressive aphasia were recruited from the international multicentre GENetic Frontotemporal dementia Initiative study and compared with healthy controls as well as a cohort of people with sporadic primary progressive aphasia. Symptoms were assessed using the GENetic Frontotemporal dementia Initiative language, behavioural, neuropsychiatric and motor scales. Participants also underwent a cognitive assessment and 3 T volumetric T1-weighted MRI. One

Identifiants

pubmed: 36938528
doi: 10.1093/braincomms/fcad036
pii: fcad036
pmc: PMC10019761
doi:

Types de publication

Journal Article

Langues

eng

Pagination

fcad036

Investigateurs

Sónia Afonso (S)
Maria Rosario Almeida (MR)
Sarah Anderl-Straub (S)
Christin Andersson (C)
Anna Antonell (A)
Silvana Archetti (S)
Andrea Arighi (A)
Mircea Balasa (M)
Myriam Barandiaran (M)
Nuria Bargalló (N)
Robart Bartha (R)
Benjamin Bender (B)
Alberto Benussi (A)
Maxime Bertoux (M)
Anne Bertrand (A)
Valentina Bessi (V)
Sandra Black (S)
Sergi Borrego-Ecija (S)
Jose Bras (J)
Alexis Brice (A)
Rose Bruffaerts (R)
Agnès Camuzat (A)
Marta Cañada (M)
Valentina Cantoni (V)
Paola Caroppo (P)
Miguel Castelo-Branco (M)
Olivier Colliot (O)
Thomas Cope (T)
Vincent Deramecourt (V)
María de Arriba (M)
Giuseppe Di Fede (GD)
Alina Díez (A)
Diana Duro (D)
Chiara Fenoglio (C)
Camilla Ferrari (C)
Catarina B Ferreira (CB)
Nick Fox (N)
Morris Freedman (M)
Giorgio Fumagalli (G)
Aurélie Funkiewiez (A)
Institut du Cerveau (I)
Alazne Gabilondo (A)
Roberto Gasparotti (R)
Serge Gauthier (S)
Stefano Gazzina (S)
Giorgio Giaccone (G)
Ana Gorostidi (A)
Rita Guerreiro (R)
Carolin Heller (C)
Tobias Hoegen (T)
Begoña Indakoetxea (B)
Vesna Jelic (V)
Hans-Otto Karnath (HO)
Ron Keren (R)
Gregory Kuchcinski (G)
Tobias Langheinrich (T)
Thibaud Lebouvier (T)
Maria João Leitão (M)
Albert Lladó (A)
Gemma Lombardi (G)
Sandra Loosli (S)
Carolina Maruta (C)
Simon Mead (S)
Lieke Meeter (L)
Gabriel Miltenberger (G)
Rick van Minkelen (R)
Sara Mitchell (S)
Katrina Moore (K)
Benedetta Nacmias (B)
Annabel Nelson (A)
Linn Öijerstedt (L)
Jaume Olives (J)
Sebastien Ourselin (S)
Alessandro Padovani (A)
Jessica Panman (J)
Janne M Papma (JM)
Yolande Pijnenburg (Y)
Cristina Polito (C)
Enrico Premi (E)
Sara Prioni (S)
Catharina Prix (C)
Rosa Rademakers (R)
Veronica Redaelli (V)
Daisy Rinaldi (D)
Institut du Cerveau (I)
Tim Rittman (T)
Ekaterina Rogaeva (E)
Adeline Rollin (A)
Pedro Rosa-Neto (P)
Giacomina Rossi (G)
Martin Rossor (M)
Beatriz Santiago (B)
Dario Saracino (D)
Sabrina Sayah (S)
Elio Scarpini (E)
Sonja Schönecker (S)
Elisa Semler (E)
Rachelle Shafei (R)
Christen Shoesmith (C)
Imogen Swift (I)
Miguel Tábuas-Pereira (M)
Mikel Tainta (M)
Ricardo Taipa (R)
David Tang-Wai (D)
David L Thomas (DL)
Paul Thompson (P)
Hakan Thonberg (H)
Carolyn Timberlake (C)
Pietro Tiraboschi (P)
Emily Todd (E)
Philip Van Damme (PV)
Mathieu Vandenbulcke (M)
Michele Veldsman (M)
Ana Verdelho (A)
Jorge Villanua (J)
Carlo Wilke (C)
Ione Woollacott (I)
Elisabeth Wlasich (E)
Henrik Zetterberg (H)
Miren Zulaica (M)

Informations de copyright

© The Author(s) 2023. Published by Oxford University Press on behalf of the Guarantors of Brain.

Déclaration de conflit d'intérêts

The authors report no competing interests.

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Auteurs

Kiran Samra (K)

Dementia Research Centre, Department of Neurodegenerative Disease, UCL Queen Square Institute of Neurology, London, UK.

Amy M MacDougall (AM)

Department of Medical Statistics, London School of Hygiene and Tropical Medicine, London, UK.

Arabella Bouzigues (A)

Dementia Research Centre, Department of Neurodegenerative Disease, UCL Queen Square Institute of Neurology, London, UK.

Martina Bocchetta (M)

Dementia Research Centre, Department of Neurodegenerative Disease, UCL Queen Square Institute of Neurology, London, UK.

David M Cash (DM)

Dementia Research Centre, Department of Neurodegenerative Disease, UCL Queen Square Institute of Neurology, London, UK.

Caroline V Greaves (CV)

Dementia Research Centre, Department of Neurodegenerative Disease, UCL Queen Square Institute of Neurology, London, UK.

Rhian S Convery (RS)

Dementia Research Centre, Department of Neurodegenerative Disease, UCL Queen Square Institute of Neurology, London, UK.

Chris Hardy (C)

Dementia Research Centre, Department of Neurodegenerative Disease, UCL Queen Square Institute of Neurology, London, UK.

John C van Swieten (JC)

Department of Neurology, Erasmus Medical Centre, Rotterdam, Netherlands.

Harro Seelaar (H)

Department of Neurology, Erasmus Medical Centre, Rotterdam, Netherlands.

Lize C Jiskoot (LC)

Department of Neurology, Erasmus Medical Centre, Rotterdam, Netherlands.

Fermin Moreno (F)

Cognitive Disorders Unit, Department of Neurology, Donostia Universitary Hospital, San Sebastian, Spain.
Neuroscience Area, Biodonostia Health Research Institute, San Sebastian, Gipuzkoa, Spain.

Raquel Sanchez-Valle (R)

Alzheimer's disease and Other Cognitive Disorders Unit, Neurology Service, Hospital Clínic, Institut d'Investigacións Biomèdiques August Pi I Sunyer, University of Barcelona, Barcelona, Spain.

Robert Laforce (R)

Clinique Interdisciplinaire de Mémoire, Département des Sciences Neurologiques, CHU de Québec, and Faculté de Médecine, Université Laval, Québec City, Canada.

Caroline Graff (C)

Center for Alzheimer Research, Division of Neurogeriatrics, Department of Neurobiology, Care Sciences and Society, Bioclinicum, Karolinska Institutet, Solna, Sweden.
Unit for Hereditary Dementias, Theme Aging, Karolinska University Hospital, Solna, Sweden.

Mario Masellis (M)

Sunnybrook Health Sciences Centre, Sunnybrook Research Institute, University of Toronto, Toronto, Canada.

Maria Carmela Tartaglia (MC)

Tanz Centre for Research in Neurodegenerative Diseases, University of Toronto, Toronto, ON, Canada.

James B Rowe (JB)

Department of Clinical Neurosciences, University of Cambridge, Cambridge, UK.

Barbara Borroni (B)

Neurology Unit, Department of Clinical and Experimental Sciences, University of Brescia, Brescia, Italy.

Elizabeth Finger (E)

Department of Clinical Neurological Sciences, University of Western Ontario, London, ON, Canada.

Matthis Synofzik (M)

Department of Neurodegenerative Diseases, Hertie-Institute for Clinical Brain Research and Center of Neurology, University of Tübingen, Tübingen, Germany.
Centre for Neurodegenerative Diseases (DZNE), Tübingen, Germany.

Daniela Galimberti (D)

Fondazione Ca' Granda, IRCCS Ospedale Policlinico, Milan, Italy.
University of Milan, Centro Dino Ferrari, Milan, Italy.

Rik Vandenberghe (R)

Laboratory for Cognitive Neurology, Department of Neurosciences, KU Leuven, Leuven, Belgium.
Neurology Service, University Hospitals Leuven, Leuven, Belgium.
Leuven Brain Institute, KU Leuven, Leuven, Belgium.

Alexandre de Mendonça (A)

Laboratory of Neurosciences, Institute of Molecular Medicine, Faculty of Medicine, University of Lisbon, Lisbon, Portugal.

Chris R Butler (CR)

Nuffield Department of Clinical Neurosciences, Medical Sciences Division, University of Oxford, Oxford, UK.
Department of Brain Sciences, Imperial College London, London, UK.

Alexander Gerhard (A)

Division of Neuroscience and Experimental Psychology, Wolfson Molecular Imaging Centre, University of Manchester, Manchester, UK.
Departments of Geriatric Medicine and Nuclear Medicine, University of Duisburg-Essen, Germany.

Simon Ducharme (S)

Department of Psychiatry, McGill University Health Centre, McGill University, Montreal, Québec, Canada.
McConnell Brain Imaging Centre, Montreal Neurological Institute, McGill University, Montreal, Québec, Canada.

Isabelle Le Ber (I)

Sorbonne Université, Paris Brain Institute - Institut du Cerveau - ICM, Inserm U1127, CNRS UMR 7225, AP-HP - Hôpital Pitié-Salpêtrière, Paris, France.
Centre de référence des démences rares ou précoces, IM2A, Département de Neurologie, AP-HP - Hôpital Pitié-Salpêtrière, Paris, France.
Département de Neurologie, AP-HP - Hôpital Pitié-Salpêtrière, Paris, France.

Isabel Santana (I)

University Hospital of Coimbra (HUC), Neurology Service, Faculty of Medicine, University of Coimbra, Coimbra, Portugal.
Center for Neuroscience and Cell Biology, Faculty of Medicine, University of Coimbra, Coimbra, Portugal.

Florence Pasquier (F)

Univ Lille, Inserm 1172, Lille, France.
Inserm 1172, Lille, France.
CHU, CNR-MAJ, Labex Distalz, LiCEND Lille, France.

Johannes Levin (J)

Department of Neurology, Ludwig-Maximilians Universität München, Munich, Germany.
German Centre for Neurodegenerative Diseases (DZNE), Munich, Germany.
Munich Cluster of Systems Neurology (SyNergy), Munich, Germany.

Markus Otto (M)

Department of Neurology, University of Ulm, Ulm, Germany.

Sandro Sorbi (S)

Department of Neurofarba, University of Florence, Florence, Italy.
IRCCS Fondazione Don Carlo Gnocchi, Florence, Italy.

Jason D Warren (JD)

Dementia Research Centre, Department of Neurodegenerative Disease, UCL Queen Square Institute of Neurology, London, UK.

Jonathan D Rohrer (JD)

Dementia Research Centre, Department of Neurodegenerative Disease, UCL Queen Square Institute of Neurology, London, UK.

Lucy L Russell (LL)

Dementia Research Centre, Department of Neurodegenerative Disease, UCL Queen Square Institute of Neurology, London, UK.

Classifications MeSH