Prader-Willi Syndrome and Weight Gain Control: From Prevention to Surgery-A Narrative Review.
Prader–Willi syndrome
bariatric surgery
diet
exercise
hormonal therapy
weight gain
Journal
Children (Basel, Switzerland)
ISSN: 2227-9067
Titre abrégé: Children (Basel)
Pays: Switzerland
ID NLM: 101648936
Informations de publication
Date de publication:
16 Mar 2023
16 Mar 2023
Historique:
received:
26
01
2023
revised:
01
03
2023
accepted:
12
03
2023
medline:
30
3
2023
entrez:
29
3
2023
pubmed:
30
3
2023
Statut:
epublish
Résumé
Severe obesity remains one of the most important symptoms of Prader-Willi Syndrome (PWS), and controlling weight represents a crucial point in the therapeutical approach to the syndrome. We present an overview of different progressive patterns of growth that involve controlling weight in PWS. Mechanisms involved in the development of obesity and in preventive and therapeutic strategies to control weight gain are discussed. Early diagnosis, a controlled diet regimen, regular physical activity, follow-up by multidisciplinary teams, and hormonal treatment improved the management of excessive weight gain. In selected cases, a surgical approach can be also considered. Controlling weight in PWS remains a challenge for pediatricians. The importance of consulting different healthcare specialists, starting from the neonatal and pediatric age, is also considered as a crucial approach to controlling weight, as well as to limiting and preventing the onset of obesity and its complications.
Identifiants
pubmed: 36980122
pii: children10030564
doi: 10.3390/children10030564
pmc: PMC10047227
pii:
doi:
Types de publication
Journal Article
Review
Langues
eng
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