Motor Phenomena Associated With Leucine-Rich Glioma-Inactivated (LGI1) Emi-Encephalitis.

caudatum chorea epilptetic spasms fbds lgi1 antibody autoimmune encephalitis temporal lobe

Journal

Cureus
ISSN: 2168-8184
Titre abrégé: Cureus
Pays: United States
ID NLM: 101596737

Informations de publication

Date de publication:
Mar 2023
Historique:
accepted: 26 02 2023
medline: 11 4 2023
entrez: 10 4 2023
pubmed: 11 4 2023
Statut: epublish

Résumé

LGI1 encephalitis is a rare immune-mediated brain disorder. Its typical features include faciobrachial dystonic seizures (FBDS), startle reactions, chorea, myoclonus, atypical parkinsonism, cogni-tive impairment, and personality changes. We report the case of a 57-year-old woman presenting with distinct patterns of involuntary movements, including faciobrachial dystonic spasms, dyskinetic movements, and chorea. Magnetic resonance imaging (MRI) and tests on blood and cerebrospinal fluid (CSF) demonstrated encephalitis involving the right temporal lobe and caudate nucleus and associated with LGI1-antibody. LGI1 encephalitis may present with simultaneous distinct patterns of movement disorders depending on the cortical and subcortical structures involved in the disease.

Identifiants

pubmed: 37033571
doi: 10.7759/cureus.35882
pmc: PMC10080185
doi:

Types de publication

Case Reports

Langues

eng

Pagination

e35882

Informations de copyright

Copyright © 2023, Giorelli et al.

Déclaration de conflit d'intérêts

The authors have declared that no competing interests exist.

Références

J Neuroinflammation. 2018 Sep 25;15(1):279
pubmed: 30253786
Ann Neurol. 2011 May;69(5):892-900
pubmed: 21416487
Tremor Other Hyperkinet Mov (N Y). 2014 Jan 08;4:
pubmed: 24459615
BMC Neurol. 2021 Oct 29;21(1):420
pubmed: 34715809
Epileptic Disord. 2018 Dec 1;20(6):525-529
pubmed: 30530418
J Neurol. 2022 Jul;269(7):3511-3521
pubmed: 35024921
Tremor Other Hyperkinet Mov (N Y). 2019 Oct 09;9:
pubmed: 31656690
Neurol Neuroimmunol Neuroinflamm. 2015 Oct 01;2(6):e161
pubmed: 26468474

Auteurs

Maurizio Giorelli (M)

Operative Unit of Neurology, "Dimiccoli" General Hospital, Barletta, ITA.

Maria S Aniello (MS)

Operative Unit of Neurology, "Dimiccoli" General Hospital, Barletta, ITA.

Sergio Altomare (S)

Operative Unit of Neurology, "Dimiccoli" General Hospital, Barletta, ITA.

Ruggiero Leone (R)

Operative Unit of Neurology, "Dimiccoli" General Hospital, Barletta, ITA.

Daniele Liuzzi (D)

Operative Unit of Neurology, "Dimiccoli" General Hospital, Barletta, ITA.

Classifications MeSH