Insight into Elderly ALS Patients in the Emilia Romagna Region: Epidemiological and Clinical Features of Late-Onset ALS in a Prospective, Population-Based Study.

amyotrophic lateral sclerosis elderly ALS epidemiology phenotype prognosis survival

Journal

Life (Basel, Switzerland)
ISSN: 2075-1729
Titre abrégé: Life (Basel)
Pays: Switzerland
ID NLM: 101580444

Informations de publication

Date de publication:
03 Apr 2023
Historique:
received: 17 02 2023
revised: 23 03 2023
accepted: 31 03 2023
medline: 28 4 2023
pubmed: 28 4 2023
entrez: 28 4 2023
Statut: epublish

Résumé

Few studies have focused on elderly (>80 years) amyotrophic lateral sclerosis (ALS) patients, who represent a fragile subgroup generally not included in clinical trials and often neglected because they are more difficult to diagnose and manage. We analyzed the clinical and genetic features of very late-onset ALS patients through a prospective, population-based study in the Emilia Romagna Region of Italy. From 2009 to 2019, 222 (13.76%) out of 1613 patients in incident cases were over 80 years old at diagnosis, with a female predominance (F:M = 1.18). Elderly ALS patients represented 12.02% of patients before 2015 and 15.91% from 2015 onwards (

Identifiants

pubmed: 37109471
pii: life13040942
doi: 10.3390/life13040942
pmc: PMC10144747
pii:
doi:

Types de publication

Journal Article

Langues

eng

Subventions

Organisme : Emilia Romagna Regional Health Authority
ID : GPG/2022/1343

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Auteurs

Giulia Gianferrari (G)

Department of Biomedical, Metabolic and Neural Sciences, University of Modena and Reggio Emilia, 41125 Modena, Italy.

Ilaria Martinelli (I)

Department of Neurosciences, Azienda Ospedaliero Universitaria di Modena, 41124 Modena, Italy.
Clinical and Experimental Medicine Ph.D. Program, University of Modena and Reggio Emilia, 41125 Modena, Italy.

Cecilia Simonini (C)

Department of Neurosciences, Azienda Ospedaliero Universitaria di Modena, 41124 Modena, Italy.

Elisabetta Zucchi (E)

Department of Neurosciences, Azienda Ospedaliero Universitaria di Modena, 41124 Modena, Italy.
Neuroscience Ph.D. Program, University of Modena and Reggio Emilia, 41125 Modena, Italy.

Nicola Fini (N)

Department of Neurosciences, Azienda Ospedaliero Universitaria di Modena, 41124 Modena, Italy.

Maria Caputo (M)

Department of Biomedical, Metabolic and Neural Sciences, University of Modena and Reggio Emilia, 41125 Modena, Italy.

Andrea Ghezzi (A)

Department of Biomedical, Metabolic and Neural Sciences, University of Modena and Reggio Emilia, 41125 Modena, Italy.

Annalisa Gessani (A)

Department of Neurosciences, Azienda Ospedaliero Universitaria di Modena, 41124 Modena, Italy.

Elena Canali (E)

Department of Neurology, IRCCS Arcispedale Santa Maria Nuova, 42123 Reggio Emilia, Italy.

Mario Casmiro (M)

Department of Neurology, Faenza and Ravenna Hospital, 48100 Ravenna, Italy.

Patrizia De Massis (P)

Department of Neurology, Imola Hospital, 40026 Bologna, Italy.

Marco Curro' Dossi (M)

Department of Neurology, Infermi Hospital, 48018 Rimini, Italy.

Silvia De Pasqua (S)

Department of Neurology, Carpi Hospital, 41012 Modena, Italy.

Rocco Liguori (R)

Department of Biomedical and Neuromotor Sciences (DIBINEM), University of Bologna, 40126 Bologna, Italy.
IRCCS Istituto delle Scienze Neurologiche di Bologna, UOC Clinica Neurologica, 40126 Bologna, Italy.

Marco Longoni (M)

Department of Neurology, Infermi Hospital, 48018 Rimini, Italy.
Department of Neurology, Bufalini Hospital, 47521 Cesena, Italy.

Doriana Medici (D)

Department of Neurology, Fidenza Hospital, 43036 Parma, Italy.

Simonetta Morresi (S)

Department of Neurology, Bufalini Hospital, 47521 Cesena, Italy.

Alberto Patuelli (A)

Department of Neurology, Forlì Hospital, 47121 Forlì, Italy.

Maura Pugliatti (M)

Department of Neurosciences, University of Ferrara, 44121 Ferrara, Italy.
Department of Neurology, St. Anna Hospital, 44124 Ferrara, Italy.

Mario Santangelo (M)

Department of Neurology, Carpi Hospital, 41012 Modena, Italy.

Elisabetta Sette (E)

Department of Neurology, St. Anna Hospital, 44124 Ferrara, Italy.

Filippo Stragliati (F)

Department of General and Specialized Medicine, University Hospital of Parma, 43126 Parma, Italy.

Emilio Terlizzi (E)

Department of Neurology, G. Da Saliceto Hospital, 29121 Piacenza, Italy.

Veria Vacchiano (V)

Department of Biomedical and Neuromotor Sciences (DIBINEM), University of Bologna, 40126 Bologna, Italy.
IRCCS Istituto delle Scienze Neurologiche di Bologna, UOC Clinica Neurologica, 40126 Bologna, Italy.

Lucia Zinno (L)

Department of General and Specialized Medicine, University Hospital of Parma, 43126 Parma, Italy.

Salvatore Ferro (S)

Department of Hospital Services, Emilia Romagna Regional Health Authority, 40127 Bologna, Italy.

Amedeo Amedei (A)

Department of Experimental and Clinical Medicine, University of Florence, 50134 Florence, Italy.

Tommaso Filippini (T)

Department of Biomedical, Metabolic and Neural Sciences, University of Modena and Reggio Emilia, 41125 Modena, Italy.
Research Centre in Environmental, Genetic and Nutritional Epidemiology-CREAGEN, University of Modena and Reggio Emilia, 41125 Modena, Italy.
School of Public Health, University of California Berkeley, Berkeley, CA 94704, USA.

Marco Vinceti (M)

Department of Biomedical, Metabolic and Neural Sciences, University of Modena and Reggio Emilia, 41125 Modena, Italy.
Research Centre in Environmental, Genetic and Nutritional Epidemiology-CREAGEN, University of Modena and Reggio Emilia, 41125 Modena, Italy.
Department of Epidemiology, Boston University School of Public Health, Boston University, Boston, MA 02118, USA.

Jessica Mandrioli (J)

Department of Biomedical, Metabolic and Neural Sciences, University of Modena and Reggio Emilia, 41125 Modena, Italy.
Department of Neurosciences, Azienda Ospedaliero Universitaria di Modena, 41124 Modena, Italy.

Classifications MeSH