Delayed Diagnosis of X-linked Lymphoproliferative Syndrome Type 2 in a 17-year-old Male With Severe Crohn's Disease and Recurrent Skin Infections.

XIAP deficiency hematopoietic stem cell transplantation primary immunodeficiency disease

Journal

JPGN reports
ISSN: 2691-171X
Titre abrégé: JPGN Rep
Pays: United States
ID NLM: 101773885

Informations de publication

Date de publication:
Aug 2021
Historique:
received: 18 12 2020
accepted: 02 06 2021
medline: 12 7 2021
pubmed: 12 7 2021
entrez: 19 5 2023
Statut: epublish

Résumé

X-linked lymphoproliferative syndrome type 2 (XLP2) is a rare genetic primary immunodeficiency disease caused by mutations in the

Identifiants

pubmed: 37205951
doi: 10.1097/PG9.0000000000000102
pmc: PMC10191492
doi:

Types de publication

Case Reports

Langues

eng

Pagination

e102

Informations de copyright

Copyright © 2021 The Author(s). Published by Wolters Kluwer on behalf of European Society for Pediatric Gastroenterology, Hepatology, and Nutrition and North American Society for Pediatric Gastroenterology, Hepatology, and Nutrition.

Déclaration de conflit d'intérêts

The authors report no funding and conflicts of interest.

Références

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pubmed: 31375816
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J Clin Immunol. 2015 May;35(4):331-8
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World J Gastroenterol. 2018 Mar 7;24(9):1035-1045
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pubmed: 29501442

Auteurs

Stephanie A Zacharias (SA)

From the Division of Gastroenterology and Nutrition, Nemours/Alfred I. duPont Hospital for Children, Wilmington, DE.
Sidney Kimmel College of Medicine at Thomas Jefferson University, Philadelphia, PA.

Priyanka Seshadri (P)

From the Division of Gastroenterology and Nutrition, Nemours/Alfred I. duPont Hospital for Children, Wilmington, DE.
Sidney Kimmel College of Medicine at Thomas Jefferson University, Philadelphia, PA.

Sharon Hwang (S)

From the Division of Gastroenterology and Nutrition, Nemours/Alfred I. duPont Hospital for Children, Wilmington, DE.
Sidney Kimmel College of Medicine at Thomas Jefferson University, Philadelphia, PA.

Laura Baker (L)

From the Division of Gastroenterology and Nutrition, Nemours/Alfred I. duPont Hospital for Children, Wilmington, DE.

Jonathan Powell (J)

From the Division of Gastroenterology and Nutrition, Nemours/Alfred I. duPont Hospital for Children, Wilmington, DE.
Sidney Kimmel College of Medicine at Thomas Jefferson University, Philadelphia, PA.

J Fernando Del Rosario (J)

From the Division of Gastroenterology and Nutrition, Nemours/Alfred I. duPont Hospital for Children, Wilmington, DE.
Sidney Kimmel College of Medicine at Thomas Jefferson University, Philadelphia, PA.

Zarela Molle-Rios (Z)

From the Division of Gastroenterology and Nutrition, Nemours/Alfred I. duPont Hospital for Children, Wilmington, DE.
Sidney Kimmel College of Medicine at Thomas Jefferson University, Philadelphia, PA.

Classifications MeSH