One-year clinical experience on the use of Nintedanib in systemic sclerosis.

autoimmunity fibrosis interstitial lung disease rare disease systemic sclerosis

Journal

Respirology case reports
ISSN: 2051-3380
Titre abrégé: Respirol Case Rep
Pays: United States
ID NLM: 101631052

Informations de publication

Date de publication:
Jun 2023
Historique:
received: 13 09 2022
accepted: 24 02 2023
medline: 25 5 2023
pubmed: 25 5 2023
entrez: 25 5 2023
Statut: epublish

Résumé

We reviewed 11 patients with systemic sclerosis-related ILD who were referred to our Scleroderma Unit from January 2020 to January 2021 and started Nintedanib. Non-specific interstitial pneumonia (NSIP) was prevalent (45%), usual interstitial pneumonia (UIP) and UIP/NSIP pattern were both 27%. Only one patient had a history of smoking. Eight patients were on mycophenolate mofetil (MMF), eight were treated with corticosteroids (mean dose 5 mg/day of Prednisone or equivalent), and three were on Rituximab. The mean modified British Council Medical Questionnaire (mmRC) decreased from 3 to 2.5. Two patients had to reduce their daily dose to 200 mg/day for severe diarrhoea. Nintedanib was generally well tolerated.

Identifiants

pubmed: 37229296
doi: 10.1002/rcr2.1120
pii: RCR21120
pmc: PMC10203787
doi:

Types de publication

Case Reports

Langues

eng

Pagination

e01120

Informations de copyright

© 2023 The Authors. Respirology Case Reports published by John Wiley & Sons Australia, Ltd on behalf of The Asian Pacific Society of Respirology.

Déclaration de conflit d'intérêts

None declared.

Références

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Arch Dermatol. 1961 Sep;84:359-71
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Auteurs

Luca Magnani (L)

Rheumatology Unit AUSL-IRCCS of Reggio Emilia Reggio Emilia Italy.

Amelia Spinella (A)

Rheumatology, Scleroderma Unit University of Modena and Reggio Emilia - AOU Modena, VIA DEL POZZO 71 MODENA MODENA 41100 Italy.

Sofia Testoni (S)

Rheumatology Unit AUSL-IRCCS of Reggio Emilia Reggio Emilia Italy.
Rheumatology, Scleroderma Unit University of Modena and Reggio Emilia - AOU Modena, VIA DEL POZZO 71 MODENA MODENA 41100 Italy.

Federica Lumetti (F)

Rheumatology, Scleroderma Unit University of Modena and Reggio Emilia - AOU Modena, VIA DEL POZZO 71 MODENA MODENA 41100 Italy.

Chiara Scelfo (C)

Pneumology Unit AUSL-IRCSS of Reggio Emilia Reggio Emilia Italy.

Lucia Dardani (L)

Rheumatology Unit AUSL-IRCCS of Reggio Emilia Reggio Emilia Italy.

Gianluigi Bajocchi (G)

Rheumatology Unit AUSL-IRCCS of Reggio Emilia Reggio Emilia Italy.

Enrico Clini (E)

Pneumology, Respiratory Disease Unit, Department of Medical & Surgical Sciences for Children & Adult University of Modena e Reggio Emilia Reggio Emilia Italy.

Carlo Salvarani (C)

Rheumatology Unit AUSL-IRCCS of Reggio Emilia Reggio Emilia Italy.
Rheumatology, Scleroderma Unit University of Modena and Reggio Emilia - AOU Modena, VIA DEL POZZO 71 MODENA MODENA 41100 Italy.

Dilia Giuggioli (D)

Rheumatology, Scleroderma Unit University of Modena and Reggio Emilia - AOU Modena, VIA DEL POZZO 71 MODENA MODENA 41100 Italy.

Classifications MeSH