Morphological and molecular comparison of HIV-associated and sporadic inclusion body myositis.


Journal

Journal of neurology
ISSN: 1432-1459
Titre abrégé: J Neurol
Pays: Germany
ID NLM: 0423161

Informations de publication

Date de publication:
Sep 2023
Historique:
received: 20 03 2023
accepted: 11 05 2023
revised: 10 05 2023
medline: 14 8 2023
pubmed: 7 6 2023
entrez: 6 6 2023
Statut: ppublish

Résumé

The molecular characteristics of sporadic inclusion body myositis (sIBM) have been intensively studied, and specific patterns on the cellular, protein and RNA level have emerged. However, these characteristics have not been studied in the context of HIV-associated IBM (HIV-IBM). In this study, we compared clinical, histopathological, and transcriptomic patterns of sIBM and HIV-IBM. In this cross-sectional study, we compared patients with HIV-IBM and sIBM based on clinical and morphological features as well as gene expression levels of specific T-cell markers in skeletal muscle biopsy samples. Non-disease individuals served as controls (NDC). Cell counts for immunohistochemistry and gene expression profiles for quantitative PCR were used as primary outcomes. 14 muscle biopsy samples (7 HIV-IBM, 7 sIBM) of patients and 6 biopsy samples from NDC were included. Clinically, HIV-IBM patients showed a significantly lower age of onset and a shorter period between symptom onset and muscle biopsy. Histomorphologically, HIV-IBM patients showed no KLRG1 Despite HIV-IBM and sIBM sharing important clinical, histopathological, and transcriptomic signatures, the presence of KLRG1

Identifiants

pubmed: 37280376
doi: 10.1007/s00415-023-11779-y
pii: 10.1007/s00415-023-11779-y
pmc: PMC10243696
doi:

Substances chimiques

Proteins 0

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Pagination

4434-4443

Informations de copyright

© 2023. The Author(s).

Références

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Auteurs

Sinja Vogt (S)

Department of Neurology, Charité, Universitätsmedizin Berlin, Corporate Member of Freie Universität Berlin and Humboldt-Universität zu Berlin, 10117, Berlin, Germany.

Felix Kleefeld (F)

Department of Neurology, Charité, Universitätsmedizin Berlin, Corporate Member of Freie Universität Berlin and Humboldt-Universität zu Berlin, 10117, Berlin, Germany.
BIH Charité Clinician Scientist Program, BIH Biomedical Innovation Academy, Berlin Institute of Health at Charité, Universitätsmedizin Berlin, 10117, Berlin, Germany.

Corinna Preusse (C)

Department of Neuropathology, Charité, Universitätsmedizin Berlin, Corporate Member of Freie Universität Berlin and Humboldt-Universität zu Berlin, 10117, Berlin, Germany.

Gabriele Arendt (G)

Neuro-Centrum Düsseldorf, 40211, Düsseldorf, Germany.

Stefan Bieneck (S)

Department of Internal Medicine, Rheumatology, Schlosspark-Klinik, 14059, Berlin, Germany.

Anna Brunn (A)

Faculty of Medicine, Institute of Neuropathology, University Hospital Cologne, 50937, Cologne, Germany.

Martina Deckert (M)

Faculty of Medicine, Institute of Neuropathology, University Hospital Cologne, 50937, Cologne, Germany.

Benjamin Englert (B)

Center for Neuropathology and Prion Research, Ludwig-Maximilians University Munich, 81337, Munich, Germany.

Hans-Hilmar Goebel (HH)

Department of Neuropathology, Charité, Universitätsmedizin Berlin, Corporate Member of Freie Universität Berlin and Humboldt-Universität zu Berlin, 10117, Berlin, Germany.

Anja Masuhr (A)

Department of Internal Medicine, Infectiology, Auguste-Viktoria-Klinikum, 12157, Berlin, Germany.

Eva Neuen-Jacob (E)

Department of Neuropathology, University Hospital Düsseldorf, 40225, Düsseldorf, Germany.

Cornelia Kornblum (C)

Department of Neurology, University Hospital Bonn, 53127, Bonn, Germany.

Jens Reimann (J)

Department of Neurology, University Hospital Bonn, 53127, Bonn, Germany.

Federica Montagnese (F)

Department of Neurology, Friedrich-Baur-Institute, University Hospital Munich, 80336, Munich, Germany.

Benedikt Schoser (B)

Department of Neurology, Friedrich-Baur-Institute, University Hospital Munich, 80336, Munich, Germany.

Werner Stenzel (W)

Department of Neuropathology, Charité, Universitätsmedizin Berlin, Corporate Member of Freie Universität Berlin and Humboldt-Universität zu Berlin, 10117, Berlin, Germany. Werner.Stenzel@charite.de.

Katrin Hahn (K)

Department of Neurology, Charité, Universitätsmedizin Berlin, Corporate Member of Freie Universität Berlin and Humboldt-Universität zu Berlin, 10117, Berlin, Germany. Katrin.Hahn@charite.de.

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