Genetic Abnormalities of the Sinoatrial Node and Atrioventricular Conduction.

Arrhythmia Atrioventricular node Electrophysiology Inherited arrhythmias Sinoatrial node dysfunction

Journal

Cardiology clinics
ISSN: 1558-2264
Titre abrégé: Cardiol Clin
Pays: Netherlands
ID NLM: 8300331

Informations de publication

Date de publication:
Aug 2023
Historique:
medline: 19 6 2023
pubmed: 16 6 2023
entrez: 15 6 2023
Statut: ppublish

Résumé

The peculiar electrophysiological properties of the sinoatrial node and the cardiac conduction system are key components of the normal physiology of cardiac impulse generation and propagation. Multiple genes and transcription factors and metabolic proteins are involved in their development and regulation. In this review, we have summarized the genetic underlying causes, key clinical findings, and the latest available clinical evidence. We will discuss clinical diagnosis and management of the genetic conditions associated with conduction disorders that are more prevalent in clinical practice, for this reason, very rare genetic diseases presenting sinus node or cardiac conduction system abnormalities are not discussed.

Identifiants

pubmed: 37321685
pii: S0733-8651(23)00040-1
doi: 10.1016/j.ccl.2023.03.014
pii:
doi:

Types de publication

Journal Article Review

Langues

eng

Sous-ensembles de citation

IM

Pagination

333-347

Informations de copyright

Copyright © 2023 Elsevier Inc. All rights reserved.

Auteurs

Andreu Porta-Sánchez (A)

Cardiología Molecular, Fundación Centro Nacional de Investigaciones Cardiovasculares Carlos III (CNIC) Madrid, Spain; Departamento de Cardiología, Unidad de Arritmias, Hospital Universitario Quironsalud Madrid, Spain; Departamento de Medicina, Universidad Europea de Madrid, Spain.

Silvia Giuliana Priori (SG)

Cardiología Molecular, Fundación Centro Nacional de Investigaciones Cardiovasculares Carlos III (CNIC) Madrid, Spain; Molecular Medicine Department, University of Pavia, Italy; Istituti Clinici Scientifici Maugeri, IRCCS, Pavia, Italy. Electronic address: silvia.priori@icsmaugeri.it.

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Classifications MeSH