Development and Validation of a Novel Score to Predict Mortality in Stevens-Johnson Syndrome and Toxic Epidermal Necrolysis: CRISTEN.

Disease mortality Scoring system Stevens-Johnson syndrome Toxic epidermal necrolysis

Journal

The journal of allergy and clinical immunology. In practice
ISSN: 2213-2201
Titre abrégé: J Allergy Clin Immunol Pract
Pays: United States
ID NLM: 101597220

Informations de publication

Date de publication:
Oct 2023
Historique:
received: 26 10 2022
revised: 13 06 2023
accepted: 02 07 2023
pubmed: 11 7 2023
medline: 11 7 2023
entrez: 10 7 2023
Statut: ppublish

Résumé

Stevens-Johnson syndrome (SJS) and toxic epidermal necrolysis (TEN) are life-threatening, severe mucocutaneous adverse reactions. Severity prediction at early onset is urgently required for treatment. However, previous prediction scores have been based on data of blood tests. This study aimed to present a novel score that predicts mortality in patients with SJS/TEN in the early stages based on only clinical information. We retrospectively evaluated 382 patients with SJS/TEN in a development study. A clinical risk score for TEN (CRISTEN) was created according to the association of potential risk factors with death. We calculated the sum of these risk factors using CRISTEN, and this was validated in a multinational survey of 416 patients and was compared with previous scoring systems. The significant risk factors for death in SJS/TEN comprised 10 items, including patients' age of ≥65 years, ≥10% body surface area involvement, the use of antibiotics as culprit drugs, the use of systemic corticosteroid therapy before the onset, and mucosal damage affecting the ocular, buccal, and genital mucosa. Renal impairment, diabetes, cardiovascular disease, malignant neoplasm, and bacterial infection were included as underlying diseases. The CRISTEN model showed good discrimination (area under the curve [AUC] = 0.884) and calibration. In the validation study, the AUC was 0.827, which was statistically comparable to those of previous systems. A scoring system based on only clinical information was developed to predict mortality in SJS/TEN and was validated in an independent multinational study. CRISTEN may predict individual survival probabilities and direct the management and therapy of patients with SJS/TEN.

Sections du résumé

BACKGROUND BACKGROUND
Stevens-Johnson syndrome (SJS) and toxic epidermal necrolysis (TEN) are life-threatening, severe mucocutaneous adverse reactions. Severity prediction at early onset is urgently required for treatment. However, previous prediction scores have been based on data of blood tests.
OBJECTIVE OBJECTIVE
This study aimed to present a novel score that predicts mortality in patients with SJS/TEN in the early stages based on only clinical information.
METHODS METHODS
We retrospectively evaluated 382 patients with SJS/TEN in a development study. A clinical risk score for TEN (CRISTEN) was created according to the association of potential risk factors with death. We calculated the sum of these risk factors using CRISTEN, and this was validated in a multinational survey of 416 patients and was compared with previous scoring systems.
RESULTS RESULTS
The significant risk factors for death in SJS/TEN comprised 10 items, including patients' age of ≥65 years, ≥10% body surface area involvement, the use of antibiotics as culprit drugs, the use of systemic corticosteroid therapy before the onset, and mucosal damage affecting the ocular, buccal, and genital mucosa. Renal impairment, diabetes, cardiovascular disease, malignant neoplasm, and bacterial infection were included as underlying diseases. The CRISTEN model showed good discrimination (area under the curve [AUC] = 0.884) and calibration. In the validation study, the AUC was 0.827, which was statistically comparable to those of previous systems.
CONCLUSION CONCLUSIONS
A scoring system based on only clinical information was developed to predict mortality in SJS/TEN and was validated in an independent multinational study. CRISTEN may predict individual survival probabilities and direct the management and therapy of patients with SJS/TEN.

Identifiants

pubmed: 37429419
pii: S2213-2198(23)00729-8
doi: 10.1016/j.jaip.2023.07.001
pii:
doi:

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Pagination

3161-3168.e2

Informations de copyright

Copyright © 2023 American Academy of Allergy, Asthma & Immunology. Published by Elsevier Inc. All rights reserved.

Auteurs

Natsumi Hama (N)

Division of Dermatology, Niigata University Graduate School of Medical and Dental Sciences, Niigata, Japan.

Yuma Sunaga (Y)

Department of Dermatology, Showa University School of Medicine, Tokyo, Japan; Department of Hygiene, Public Health and Preventive Medicine, Showa University School of Medicine, Tokyo, Japan.

Hirotaka Ochiai (H)

Department of Hygiene, Public Health and Preventive Medicine, Showa University School of Medicine, Tokyo, Japan.

Akatsuki Kokaze (A)

Department of Hygiene, Public Health and Preventive Medicine, Showa University School of Medicine, Tokyo, Japan.

Hideaki Watanabe (H)

Department of Dermatology, Showa University School of Medicine, Tokyo, Japan.

Michiko Kurosawa (M)

Department of Epidemiology and Environmental Health, Juntendo University Faculty of Medicine, Tokyo, Japan.

Hiroaki Azukizawa (H)

Department of Dermatology, Nara Medical University, Nara, Japan.

Hideo Asada (H)

Department of Dermatology, Nara Medical University, Nara, Japan.

Yuko Watanabe (Y)

Department of Environmental Immuno-Dermatology, Yokohama City University Graduate School of Medicine, Kanagawa, Japan.

Yukie Yamaguchi (Y)

Department of Environmental Immuno-Dermatology, Yokohama City University Graduate School of Medicine, Kanagawa, Japan.

Michiko Aihara (M)

Department of Environmental Immuno-Dermatology, Yokohama City University Graduate School of Medicine, Kanagawa, Japan.

Yoshiko Mizukawa (Y)

Department of Dermatology, Kyorin University Faculty of Medicine, Tokyo, Japan.

Manabu Ohyama (M)

Department of Dermatology, Kyorin University Faculty of Medicine, Tokyo, Japan.

Hideo Hashizume (H)

Department of Dermatology, Iwata City Hospital, Shizuoka, Japan.

Saeko Nakajima (S)

Department of Dermatology, Kyoto University Graduate School of Medicine, Kyoto, Japan.

Takashi Nomura (T)

Department of Dermatology, Kyoto University Graduate School of Medicine, Kyoto, Japan.

Kenji Kabashima (K)

Department of Dermatology, Kyoto University Graduate School of Medicine, Kyoto, Japan.

Mikiko Tohyama (M)

Department of Dermatology, National Hospital Organization Shikoku Cancer Center, Ehime, Japan.

Akito Hasegawa (A)

Division of Dermatology, Niigata University Graduate School of Medical and Dental Sciences, Niigata, Japan.

Hayato Takahashi (H)

Department of Dermatology, Keio University School of Medicine, Tokyo, Japan.

Hiroki Mieno (H)

Department of Ophthalmology, Kyoto Prefectural University of Medicine, Kyoto, Japan.

Mayumi Ueta (M)

Department of Ophthalmology, Kyoto Prefectural University of Medicine, Kyoto, Japan.

Chie Sotozono (C)

Department of Ophthalmology, Kyoto Prefectural University of Medicine, Kyoto, Japan.

Hiroyuki Niihara (H)

Department of Dermatology, Shimane University Faculty of Medicine, Shimane, Japan.

Eishin Morita (E)

Department of Dermatology, Shimane University Faculty of Medicine, Shimane, Japan.

Marie-Charlotte Brüggen (MC)

Department of Dermatology, University Hospital of Zürich, Zürich, Switzerland; Faculty of Medicine, University of Zurich, Zurich, Switzerland; Christine Kühne Foundation for Allergy Research and Education (CK Care), Davos, Switzerland.

Iris Motro Feingold (IM)

Technion-Israel Institute of Technology, Haifa, Israel.

Marc G Jeschke (MG)

Sunnybrook Health Sciences Centre, Toronto, Ontario, Canada.

Roni P Dodiuk-Gad (RP)

Technion-Israel Institute of Technology, Haifa, Israel; Department of Dermatology, Emek Medical Center, Afula, Israel; Bruce Rappaport Faculty of Medicine, Technion, Haifa, Israel; Department of Medicine, University of Toronto, Ontario, Canada.

Eva Maria Oppel (EM)

Department of Dermatology and Allergy, University Hospital, LMU, Munich, Germany.

Lars E French (LE)

Department of Dermatology and Allergy, University Hospital, LMU, Munich, Germany; Dr. Philip Frost Department of Dermatology and Cutaneous Surgery, University of Miami Miller School of Medicine, Miami, Fla.

Wei-Ti Chen (WT)

Department of Dermatology, Drug Hypersensitivity Clinical and Research Center, Chang Gung Memorial Hospital, Keelung, Linkou, Taipei, Taiwan.

Wen-Hung Chung (WH)

Department of Dermatology, Drug Hypersensitivity Clinical and Research Center, Chang Gung Memorial Hospital, Keelung, Linkou, Taipei, Taiwan.

Chia-Yu Chu (CY)

Department of Dermatology, National Taiwan University Hospital and National Taiwan College of Medicine, Taipei, Taiwan.

Hye-Ryun Kang (HR)

Department of Internal Medicine, Seoul National University College of Medicine, Seoul, Korea.

Saskia Ingen-Housz-Oro (S)

Department of Dermatology, AP-HP, Henri Mondor Hospital, Créteil, France; Univ Paris Est Créteil EpidermE, Créteil, France; Reference Center for Toxic Bullous Diseases TOXIBUL, Créteil, France.

Kazutoshi Nakamura (K)

Division of Preventive Medicine, Niigata University Graduate School of Medical and Dental Sciences, Niigata, Japan.

Hirohiko Sueki (H)

Department of Dermatology, Showa University School of Medicine, Tokyo, Japan.

Riichiro Abe (R)

Division of Dermatology, Niigata University Graduate School of Medical and Dental Sciences, Niigata, Japan. Electronic address: aberi@med.niigata-u.ac.jp.

Classifications MeSH