Molecular Mechanism in the Development of Pulmonary Fibrosis in Patients with Sarcoidosis.
advanced pulmonary fibrosis
molecular pathway
sarcoidosis
signaling
Journal
International journal of molecular sciences
ISSN: 1422-0067
Titre abrégé: Int J Mol Sci
Pays: Switzerland
ID NLM: 101092791
Informations de publication
Date de publication:
28 Jun 2023
28 Jun 2023
Historique:
received:
23
05
2023
revised:
21
06
2023
accepted:
26
06
2023
medline:
17
7
2023
pubmed:
14
7
2023
entrez:
14
7
2023
Statut:
epublish
Résumé
Sarcoidosis is a multisystemic disease of unknown etiology characterized by the formation of granulomas in various organs, especially lung and mediastinal hilar lymph nodes. The clinical course and manifestations are unpredictable: spontaneous remission can occur in approximately two thirds of patients; up to 20% of patients have chronic course of the lung disease (called advanced pulmonary sarcoidosis, APS) resulting in progressive loss of lung function, sometimes life-threatening that can lead to respiratory failure and death. The immunopathology mechanism leading from granuloma formation to the fibrosis in APS still remains elusive. Recent studies have provided new insights into the genetic factors and immune components involved in the clinical manifestation of the disease. In this review we aim to summarize the clinical-prognostic characteristics and molecular pathways which are believed to be associated with the development of APS.
Identifiants
pubmed: 37445947
pii: ijms241310767
doi: 10.3390/ijms241310767
pmc: PMC10341418
pii:
doi:
Types de publication
Journal Article
Review
Langues
eng
Sous-ensembles de citation
IM
Références
Thorax. 2001 Jul;56(7):549-56
pubmed: 11413354
Thorax. 2021 Jan;76(1):4-20
pubmed: 33268456
Am J Pathol. 2003 May;162(5):1495-502
pubmed: 12707032
Semin Diagn Pathol. 2007 Aug;24(3):150-61
pubmed: 17882899
Respir Med. 2021 Jan 5;177:106294
pubmed: 33485108
FEBS Lett. 2017 Oct;591(19):3089-3103
pubmed: 28600802
Respir Med. 2018 Nov;144S:S20-S27
pubmed: 30166087
PLoS One. 2008 May 14;3(5):e2142
pubmed: 18478089
Cell. 2012 Apr 13;149(2):274-93
pubmed: 22500797
Br Med J. 1961 Nov 4;2(5261):1165-72
pubmed: 14497750
Eur Respir J. 2019 Aug 1;54(2):
pubmed: 31023854
Clin Rev Allergy Immunol. 2015 Aug;49(1):36-44
pubmed: 25762348
Clin Immunol. 2010 Oct;137(1):89-101
pubmed: 20674506
AJR Am J Roentgenol. 2000 Jun;174(6):1751-7
pubmed: 10845518
J Immunol. 2005 Oct 15;175(8):5390-5
pubmed: 16210645
Sarcoidosis Vasc Diffuse Lung Dis. 2020;37(2):99-103
pubmed: 33093775
Curr Opin Pulm Med. 2021 Sep 1;27(5):423-429
pubmed: 34175860
Eur Respir J. 2011 Dec;38(6):1368-73
pubmed: 22075486
Respir Med. 2013 Mar;107(3):439-47
pubmed: 23261309
Tissue Antigens. 2011 Feb;77(2):112-7
pubmed: 21214523
Sarcoidosis Vasc Diffuse Lung Dis. 2019;36(2):92-107
pubmed: 32476942
Postgrad Med. 2022 Aug;134(6):603-608
pubmed: 35619233
Am J Respir Cell Mol Biol. 2019 Jan;60(1):84-95
pubmed: 30134122
Sci Rep. 2017 Jun 26;7(1):4237
pubmed: 28652588
Curr Opin Pulm Med. 2020 Sep;26(5):574-581
pubmed: 32740378
Eur Respir J. 2010 Feb;35(2):324-30
pubmed: 19679608
Hum Genet. 2018 Sep;137(9):705-716
pubmed: 30054724
Cytokine. 2013 Mar;61(3):906-11
pubmed: 23384655
Curr Opin Pulm Med. 2020 Sep;26(5):598-607
pubmed: 32657837
Eur Respir J. 2018 Dec 20;52(6):
pubmed: 30361243
Biomed Pharmacother. 2021 Feb;134:111046
pubmed: 33341049
J Clin Med. 2020 Aug 13;9(8):
pubmed: 32823753
Eur Respir J. 2021 Jul 22;58(1):
pubmed: 33446605
Am J Respir Crit Care Med. 2016 Jun 1;193(11):1281-91
pubmed: 26649486
Respir Med. 1991 Jan;85(1):59-64
pubmed: 2014359
Eur Respir J. 2017 Jun 15;49(6):
pubmed: 28619957
Am J Respir Crit Care Med. 2001 Dec 1;164(11):2085-91
pubmed: 11739139
Sarcoidosis Vasc Diffuse Lung Dis. 1996 Sep;13(2):120-8
pubmed: 8893380
Respir Med. 2020 Aug;169:105997
pubmed: 32442108
J Histochem Cytochem. 2016 Mar;64(3):157-67
pubmed: 26747705
Respir Med. 2011 Feb;105(2):282-91
pubmed: 21146388
Respir Res. 2022 Jun 25;23(1):169
pubmed: 35752806
Adv Exp Med Biol. 2019;1165:347-364
pubmed: 31399973
Eur Respir J. 2021 Dec 16;58(6):
pubmed: 34140301
J Heart Lung Transplant. 2021 Nov;40(11):1349-1379
pubmed: 34419372
Lancet Respir Med. 2020 Feb;8(2):147-157
pubmed: 31578169
Sci Rep. 2019 Mar 11;9(1):4061
pubmed: 30858405
Chest. 2018 Jan;153(1):105-113
pubmed: 28728933
Am J Respir Crit Care Med. 2001 Jan;163(1):115-21
pubmed: 11208635
Dev Comp Immunol. 2004 May 3;28(5):461-85
pubmed: 15062644
J Clin Med. 2020 Jan 05;9(1):
pubmed: 31948067
Eur Respir J. 2013 Mar;41(3):621-6
pubmed: 22743676
Eur Radiol. 2014 Apr;24(4):807-16
pubmed: 24399491
Thorax. 2003 Jun;58(6):519-24
pubmed: 12775866
Am J Respir Crit Care Med. 2006 Apr 1;173(7):781-92
pubmed: 16415274
J Clin Med. 2022 Apr 06;11(7):
pubmed: 35407673
Mt Sinai J Med. 2009 Feb;76(1):30-6
pubmed: 19170216
Lancet Respir Med. 2018 May;6(5):389-402
pubmed: 29625772
Am J Pathol. 2011 Mar;178(3):1279-86
pubmed: 21356378
Chest. 2021 Aug;160(2):562-571
pubmed: 33440183
Biochem Soc Trans. 2009 Aug;37(Pt 4):849-54
pubmed: 19614606
Nat Rev Immunol. 2003 Nov;3(11):900-11
pubmed: 14668806
Hum Immunol. 2018 Jan;79(1):63-69
pubmed: 29107084
Sci Rep. 2019 Dec 9;9(1):18633
pubmed: 31819081
Thorax. 2000 Sep;55(9):751-4
pubmed: 10950893
Am J Respir Crit Care Med. 2022 Mar 1;205(5):495-506
pubmed: 34813386
Chest. 2016 Feb;149(2):499-507
pubmed: 26158549
Eur Respir J. 2012 Jun;39(6):1520-33
pubmed: 22241743
JAMA. 2002 Mar 13;287(10):1301-7
pubmed: 11886322
Chest. 2006 Jun;129(6):1584-91
pubmed: 16778279
Eur Respir J. 2010 Mar;35(3):695-7
pubmed: 20190336
Lab Invest. 2020 Jun;100(6):801-811
pubmed: 32051533
Biochem Biophys Res Commun. 2011 Aug 19;412(1):109-14
pubmed: 21802406
Respir Med. 2019 Oct;157:69-76
pubmed: 31522032
Am J Respir Crit Care Med. 2015 Jul 15;192(2):e3-19
pubmed: 26177183
Eur Respir J. 2018 Aug 16;52(2):
pubmed: 29946010
Eur Respir J. 2005 May;25(5):783-8
pubmed: 15863633
Clin Immunol. 2011 Jul;140(1):71-83
pubmed: 21482483
Respir Res. 2019 Mar 14;20(1):57
pubmed: 30871560
Thorax. 2013 May;68(5):436-41
pubmed: 23321605
Sarcoidosis Vasc Diffuse Lung Dis. 1999 Mar;16(1):24-31
pubmed: 10207939
Eur Respir J. 2018 Jan 25;51(1):
pubmed: 29371395
Sci Rep. 2016 Dec 08;6:38689
pubmed: 27929051
Eur Respir J. 2021 Aug 5;58(2):
pubmed: 33479107
Am J Respir Cell Mol Biol. 2016 Jul;55(1):128-34
pubmed: 26807608
J Immunol. 1998 Jun 1;160(11):5347-54
pubmed: 9605134
Ann Am Thorac Soc. 2017 Dec;14(Supplement_6):S429-S436
pubmed: 29073364
Expert Rev Clin Immunol. 2016 Sep;12(9):973-88
pubmed: 27101234
Lancet. 2014 Mar 29;383(9923):1155-67
pubmed: 24090799
Am J Respir Crit Care Med. 2013 Sep 15;188(6):733-48
pubmed: 24032382
Immunity. 2016 Mar 15;44(3):450-462
pubmed: 26982353
Nat Rev Immunol. 2004 Aug;4(8):583-94
pubmed: 15286725
Adv Exp Med Biol. 2015;852:59-69
pubmed: 25753554
N Engl J Med. 2019 Oct 31;381(18):1718-1727
pubmed: 31566307
Fibrogenesis Tissue Repair. 2011 Apr 04;4:10
pubmed: 21463523
Eur Respir J. 2018 Mar 1;51(3):
pubmed: 29449421
Am J Respir Cell Mol Biol. 2017 Jan;56(1):74-82
pubmed: 27564547
DNA Cell Biol. 2021 Jan;40(1):18-25
pubmed: 33306933
Am J Respir Crit Care Med. 2006 Oct 15;174(8):915-22
pubmed: 16840740
Eur Respir Rev. 2019 Oct 1;28(153):
pubmed: 31578213
J Clin Med. 2020 Jul 24;9(8):
pubmed: 32722050
Am J Surg Pathol. 2013 Apr;37(4):593-600
pubmed: 23426125
Cell. 2017 Jun 1;169(6):985-999
pubmed: 28575679
Int J Mol Sci. 2018 Aug 20;19(8):
pubmed: 30127261
Immunol Cell Biol. 2011 Jan;89(1):130-42
pubmed: 20514074