Myeloid/lymphoid neoplasms with eosinophilia and tyrosine kinase gene fusions: reevaluation of the defining characteristics in a registry-based cohort.
Journal
Leukemia
ISSN: 1476-5551
Titre abrégé: Leukemia
Pays: England
ID NLM: 8704895
Informations de publication
Date de publication:
09 2023
09 2023
Historique:
received:
12
10
2022
accepted:
27
06
2023
revised:
18
05
2023
medline:
28
8
2023
pubmed:
16
7
2023
entrez:
15
7
2023
Statut:
ppublish
Résumé
In a registry-based analysis of 135 patients with "myeloid/lymphoid neoplasms with eosinophilia and tyrosine kinase gene fusions" (MLN-TK; FIP1L1::PDGFRA, n = 78; PDGFRB, diverse fusions, n = 26; FGFR1, diverse, n = 9; JAK2, diverse, n = 11; ETV6::ABL1, n = 11), we sought to evaluate the disease-defining characteristics. In 81/135 (60%) evaluable patients, hypereosinophilia (>1.5 × 10
Identifiants
pubmed: 37454239
doi: 10.1038/s41375-023-01958-1
pii: 10.1038/s41375-023-01958-1
pmc: PMC10457188
doi:
Substances chimiques
Receptor, Platelet-Derived Growth Factor beta
EC 2.7.10.1
Receptor, Platelet-Derived Growth Factor alpha
EC 2.7.10.1
Oncogene Proteins, Fusion
0
Types de publication
Journal Article
Research Support, Non-U.S. Gov't
Langues
eng
Sous-ensembles de citation
IM
Pagination
1860-1867Informations de copyright
© 2023. The Author(s).
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