Paramacular Choriocapillaris Atrophy.
choriocapillaris atrophy
choroidal dystrophy
foveal sparing
macular atrophy
retinal dystrophy
Journal
Biomedicines
ISSN: 2227-9059
Titre abrégé: Biomedicines
Pays: Switzerland
ID NLM: 101691304
Informations de publication
Date de publication:
24 Jul 2023
24 Jul 2023
Historique:
received:
26
06
2023
revised:
21
07
2023
accepted:
22
07
2023
medline:
29
7
2023
pubmed:
29
7
2023
entrez:
29
7
2023
Statut:
epublish
Résumé
In this paper, a review of a rare case of paramacular choriocapillaris atrophy with a foveal-sparing phenotype is carried out. The 73-year-old patient stated that they had impaired vision and photophobia in both eyes during a regular ophthalmological examination, denying visual field defects and night blindness. A complete ophthalmological examination (best-corrected visual acuity, applanation tonometry, and biomicroscopy of anterior and posterior segments) and diagnostic tests, including fundus autofluorescence, fluorescein angiography, optical coherence tomography with angiography, computerized perimetry, and electroretinography, were carried out. The underlying genetic pattern is unclear, which points to paramacular choriocapillaris atrophy. According to recent research on histology, pathologies categorized as regional choroidal dystrophies are caused by alterations at the level of the retinal pigment epithelium. Despite the unresolved etiopathogenetic mechanism of foveal sparing in central choroidal and retinal dystrophies, a highly variable disease phenotype with spared fovea and central visual acuity present in a variety of heterogeneous dystrophies supports a disease-independent mechanism that allows the survival of foveal cones. The related preservation of BCVA has implications for individual prognosis and influences how treatment trials for choroidal and retinal dystrophies are designed.
Identifiants
pubmed: 37509713
pii: biomedicines11072074
doi: 10.3390/biomedicines11072074
pmc: PMC10377535
pii:
doi:
Types de publication
Case Reports
Langues
eng
Références
Prog Retin Eye Res. 2017 Jul;59:53-96
pubmed: 28363849
Br J Ophthalmol. 1977 Jan;61(1):43-53
pubmed: 836777
Ophthalmology. 2015 Jul;122(7):1356-65
pubmed: 25972258
Invest Ophthalmol Vis Sci. 2014 Oct 16;55(11):7467-78
pubmed: 25324290
Invest Ophthalmol Vis Sci. 2014 Jul 17;55(8):4832-41
pubmed: 25034602
Invest Ophthalmol Vis Sci. 2002 Sep;43(9):2815-8
pubmed: 12202496
Invest Ophthalmol Vis Sci. 2007 Mar;48(3):1319-29
pubmed: 17325179
Indian J Ophthalmol. 2018 Dec;66(12):1874-1876
pubmed: 30451210
Am J Ophthalmol. 1971 Sep;72(3):562-85
pubmed: 5315093
Hum Mol Genet. 2013 Dec 20;22(25):5136-45
pubmed: 23918662
Invest Ophthalmol Vis Sci. 2011 Jan 05;52(1):7-15
pubmed: 21169527
Nat Genet. 2004 Jul;36(7):755-9
pubmed: 15220920
Invest Ophthalmol Vis Sci. 1993 Nov;34(12):3278-96
pubmed: 8225863
J Clin Invest. 2008 May;118(5):1955-64
pubmed: 18414684
Invest Ophthalmol Vis Sci. 1989 Aug;30(8):1732-7
pubmed: 2759788
Nat Genet. 2000 Jul;25(3):306-10
pubmed: 10888879
Invest Ophthalmol Vis Sci. 2015 Feb 09;56(2):918-31
pubmed: 25667399
Invest Ophthalmol Vis Sci. 2019 Aug 1;60(10):3456-3467
pubmed: 31398255
Ophthalmology. 2012 Jun;119(6):1199-210
pubmed: 22449572
Eye (Lond). 2018 May;32(5):858-862
pubmed: 29148528
Invest Ophthalmol Vis Sci. 2015 May;56(5):3242-52
pubmed: 25758814
Br J Ophthalmol. 2007 Nov;91(11):1504-11
pubmed: 17504850