Short-term outcome of patients with adult IgA vasculitis: a single-center experience.

adult IgA vasculitis follow-up mortality persistent urinary abnormalities relapse

Journal

Frontiers in medicine
ISSN: 2296-858X
Titre abrégé: Front Med (Lausanne)
Pays: Switzerland
ID NLM: 101648047

Informations de publication

Date de publication:
2023
Historique:
received: 22 04 2023
accepted: 26 06 2023
medline: 2 8 2023
pubmed: 2 8 2023
entrez: 2 8 2023
Statut: epublish

Résumé

Follow-up data on IgA vasculitis (IgAV) in adults are scarce. We aimed to investigate the outcome of adult IgAV in a well-defined cohort. Data from histologically proven patients diagnosed between January 2010 and July 2022 with at least a 3-month follow-up were analyzed. The frequency and type of relapses and information on kidney function were extracted. Risk factors for IgAV relapse and decline in renal function were studied using the Cox hazards regression analysis. Mortality in IgAV was assessed using the Kaplan-Meier analysis and the standardized mortality ratio (SMR). In total, 265 patients were followed for a median of 24 months. At baseline, 38.9, 29.8, and 44.5% had articular, gastrointestinal, and renal involvement, respectively. Initially, 189 (71.3%) patients received systemic glucocorticoids, and 32 (12.1%) patients received an additional immunomodulator. During follow-up, 42 (15.8%) patients relapsed. Relapses were more common in younger patients (HR 1.03 [95%CI 1.01-1.05]) and those without baseline glucocorticoid treatment (HR 3.70 [95%CI 2.0-6.67]). Furthermore, 74 (27.9%) patients had persistent abnormal urinalysis and a substantial (≥20%) decline in glomerular filtration rate (eGFR) was recorded in 41 (15.5%) patients. The factors associated with persistent abnormal urinalysis were an absence of IgAV joint involvement and baseline immunomodulatory treatment. Pre-existent chronic kidney disease and heart failure were associated with eGFR decline. The overall SMR was 1.4 (95%CI 1.14-1.71) compared to the Slovenian general population. IgAV relapses occurred in 15% of patients, with younger patients with symptomatically managed IgAV experiencing it more frequently. Heart failure emerged as a predictor of persistent abnormal urinalysis and a decline in eGFR. Adults with IgAV had increased mortality compared to the general population.

Sections du résumé

Background UNASSIGNED
Follow-up data on IgA vasculitis (IgAV) in adults are scarce. We aimed to investigate the outcome of adult IgAV in a well-defined cohort.
Methods UNASSIGNED
Data from histologically proven patients diagnosed between January 2010 and July 2022 with at least a 3-month follow-up were analyzed. The frequency and type of relapses and information on kidney function were extracted. Risk factors for IgAV relapse and decline in renal function were studied using the Cox hazards regression analysis. Mortality in IgAV was assessed using the Kaplan-Meier analysis and the standardized mortality ratio (SMR).
Results UNASSIGNED
In total, 265 patients were followed for a median of 24 months. At baseline, 38.9, 29.8, and 44.5% had articular, gastrointestinal, and renal involvement, respectively. Initially, 189 (71.3%) patients received systemic glucocorticoids, and 32 (12.1%) patients received an additional immunomodulator. During follow-up, 42 (15.8%) patients relapsed. Relapses were more common in younger patients (HR 1.03 [95%CI 1.01-1.05]) and those without baseline glucocorticoid treatment (HR 3.70 [95%CI 2.0-6.67]). Furthermore, 74 (27.9%) patients had persistent abnormal urinalysis and a substantial (≥20%) decline in glomerular filtration rate (eGFR) was recorded in 41 (15.5%) patients. The factors associated with persistent abnormal urinalysis were an absence of IgAV joint involvement and baseline immunomodulatory treatment. Pre-existent chronic kidney disease and heart failure were associated with eGFR decline. The overall SMR was 1.4 (95%CI 1.14-1.71) compared to the Slovenian general population.
Conclusion UNASSIGNED
IgAV relapses occurred in 15% of patients, with younger patients with symptomatically managed IgAV experiencing it more frequently. Heart failure emerged as a predictor of persistent abnormal urinalysis and a decline in eGFR. Adults with IgAV had increased mortality compared to the general population.

Identifiants

pubmed: 37529245
doi: 10.3389/fmed.2023.1210307
pmc: PMC10387581
doi:

Types de publication

Journal Article

Langues

eng

Pagination

1210307

Informations de copyright

Copyright © 2023 Hočevar, Ostrovršnik, Jurčić, Tomšič and Rotar.

Déclaration de conflit d'intérêts

The authors declare that the research was conducted in the absence of any commercial or financial relationships that could be construed as a potential conflict of interest.

Références

Sci Rep. 2018 Apr 3;8(1):5585
pubmed: 29615640
Clin Kidney J. 2021 Jan 11;14(8):1953-1960
pubmed: 34345419
J Rheumatol. 2001 May;28(5):1019-24
pubmed: 11361182
J Natl Cancer Inst. 2003 Oct 1;95(19):1434-9
pubmed: 14519749
Scand J Rheumatol. 2018 Nov;47(6):481-486
pubmed: 29912602
Mayo Clin Proc. 2019 Sep;94(9):1769-1780
pubmed: 31486380
Arthritis Res Ther. 2019 Dec 26;21(1):302
pubmed: 31878954
J Am Acad Dermatol. 2020 Jun;82(6):1393-1399
pubmed: 31881295
Rheumatology (Oxford). 2021 Sep 1;60(9):4245-4251
pubmed: 33410479
Arthritis Rheum. 2013 Jan;65(1):1-11
pubmed: 23045170
J Am Soc Nephrol. 2002 May;13(5):1271-8
pubmed: 11961015
Medicine (Baltimore). 2014 Mar;93(2):106-113
pubmed: 24646467
Am J Kidney Dis. 2006 Jun;47(6):993-1003
pubmed: 16731294
Semin Arthritis Rheum. 2002 Dec;32(3):149-56
pubmed: 12528079
Br J Dermatol. 2014 Sep;171(3):524-7
pubmed: 24601900
Rheumatology (Oxford). 2021 Dec 24;61(1):291-298
pubmed: 33779729
Ann Rheum Dis. 2010 May;69(5):798-806
pubmed: 20413568
Clin Exp Rheumatol. 2020 Mar-Apr;38 Suppl 124(2):155-160
pubmed: 32083544
J Korean Med Sci. 2014 Feb;29(2):198-203
pubmed: 24550645

Auteurs

Alojzija Hočevar (A)

Department of Rheumatology, University Medical Centre Ljubljana, Ljubljana, Slovenia.
Faculty of Medicine, University of Ljubljana, Ljubljana, Slovenia.

Jaka Ostrovršnik (J)

Department of Rheumatology, University Medical Centre Ljubljana, Ljubljana, Slovenia.

Vesna Jurčić (V)

Institute of Pathology, Faculty of Medicine, University of Ljubljana, Ljubljana, Slovenia.

Matija Tomšič (M)

Department of Rheumatology, University Medical Centre Ljubljana, Ljubljana, Slovenia.
Faculty of Medicine, University of Ljubljana, Ljubljana, Slovenia.

Žiga Rotar (Ž)

Department of Rheumatology, University Medical Centre Ljubljana, Ljubljana, Slovenia.
Faculty of Medicine, University of Ljubljana, Ljubljana, Slovenia.

Classifications MeSH