Multimodal Detection and Targeting of Biopsy-Proven Myocardial Inflammation in Genetic Cardiomyopathies: A Pilot Report.

cardiomyopathy desmosomal gene variants endomyocardial biopsy genetics immunosuppressive therapy multimodal imaging myocardial inflammation

Journal

JACC. Basic to translational science
ISSN: 2452-302X
Titre abrégé: JACC Basic Transl Sci
Pays: United States
ID NLM: 101677259

Informations de publication

Date de publication:
Jul 2023
Historique:
received: 12 12 2022
revised: 15 02 2023
accepted: 15 02 2023
medline: 7 8 2023
pubmed: 7 8 2023
entrez: 7 8 2023
Statut: epublish

Résumé

The authors present a clinical report focused on the overlap between myocarditis and genetic cardiomyopathies of the dilated and arrhythmogenic spectrum. Our cohort was composed of 25 patients undergoing extensive baseline characterization and prospective reassessment by a dedicated multidisciplinary disease unit during a median follow-up of 69 months. We showed that the use of multimodal imaging allowed both discrimination of specific genotypes and identification of myocardial inflammation proven using endomyocardial biopsy. In addition, we showed that the use of immunomodulatory therapy was beneficial for most patients.

Identifiants

pubmed: 37547072
doi: 10.1016/j.jacbts.2023.02.018
pii: S2452-302X(23)00123-7
pmc: PMC10401291
doi:

Types de publication

Journal Article

Langues

eng

Pagination

755-765

Informations de copyright

© 2023 The Authors.

Déclaration de conflit d'intérêts

The authors have reported that they have no relationships relevant to the contents of this paper to disclose.

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Auteurs

Giovanni Peretto (G)

Department of Cardiac Electrophysiology and Arrhythmology, IRCCS San Raffaele Scientific Institute, Milan, Italy.
Myocarditis Disease Unit, IRCCS San Raffaele Scientific Institute, Milan, Italy.
School of Medicine, Vita-Salute San Raffaele University, Milan, Italy.

Giacomo De Luca (G)

Myocarditis Disease Unit, IRCCS San Raffaele Scientific Institute, Milan, Italy.
School of Medicine, Vita-Salute San Raffaele University, Milan, Italy.
Unit of Immunology, Rheumatology, Allergy and Rare Diseases, IRCCS San Raffaele Scientific Institute, Milan, Italy.

Andrea Villatore (A)

Myocarditis Disease Unit, IRCCS San Raffaele Scientific Institute, Milan, Italy.
School of Medicine, Vita-Salute San Raffaele University, Milan, Italy.

Chiara Di Resta (C)

School of Medicine, Vita-Salute San Raffaele University, Milan, Italy.
Genomic Unit for the Diagnosis of Human Pathologies, IRCCS San Raffaele Scientific Institute, Milan, Italy.

Simone Sala (S)

Department of Cardiac Electrophysiology and Arrhythmology, IRCCS San Raffaele Scientific Institute, Milan, Italy.
Myocarditis Disease Unit, IRCCS San Raffaele Scientific Institute, Milan, Italy.

Anna Palmisano (A)

Myocarditis Disease Unit, IRCCS San Raffaele Scientific Institute, Milan, Italy.
School of Medicine, Vita-Salute San Raffaele University, Milan, Italy.
Experimental Imaging Center, Radiology Unit, IRCCS San Raffaele Scientific Institute, Milan, Italy.

Davide Vignale (D)

Myocarditis Disease Unit, IRCCS San Raffaele Scientific Institute, Milan, Italy.
School of Medicine, Vita-Salute San Raffaele University, Milan, Italy.
Experimental Imaging Center, Radiology Unit, IRCCS San Raffaele Scientific Institute, Milan, Italy.

Corrado Campochiaro (C)

Myocarditis Disease Unit, IRCCS San Raffaele Scientific Institute, Milan, Italy.
School of Medicine, Vita-Salute San Raffaele University, Milan, Italy.
Unit of Immunology, Rheumatology, Allergy and Rare Diseases, IRCCS San Raffaele Scientific Institute, Milan, Italy.

Davide Lazzeroni (D)

IRCCS Fondazione Don Carlo Gnocchi, Parma, Italy.

Monica De Gaspari (M)

Department of Cardiac Thoracic Vascular Sciences and Public Health, Cardiovascular Pathology, Padua University, Padua, Italy.

Stefania Rizzo (S)

Department of Cardiac Thoracic Vascular Sciences and Public Health, Cardiovascular Pathology, Padua University, Padua, Italy.

Elena Busnardo (E)

Myocarditis Disease Unit, IRCCS San Raffaele Scientific Institute, Milan, Italy.
Department of Nuclear Medicine, IRCCS San Raffaele Scientific Institute, Milan, Italy.

Paola Ferro (P)

Myocarditis Disease Unit, IRCCS San Raffaele Scientific Institute, Milan, Italy.
Department of Nuclear Medicine, IRCCS San Raffaele Scientific Institute, Milan, Italy.

Luigi Gianolli (L)

Department of Nuclear Medicine, IRCCS San Raffaele Scientific Institute, Milan, Italy.

Cristina Basso (C)

Department of Cardiac Thoracic Vascular Sciences and Public Health, Cardiovascular Pathology, Padua University, Padua, Italy.

Lorenzo Dagna (L)

Myocarditis Disease Unit, IRCCS San Raffaele Scientific Institute, Milan, Italy.
School of Medicine, Vita-Salute San Raffaele University, Milan, Italy.
Unit of Immunology, Rheumatology, Allergy and Rare Diseases, IRCCS San Raffaele Scientific Institute, Milan, Italy.

Antonio Esposito (A)

Myocarditis Disease Unit, IRCCS San Raffaele Scientific Institute, Milan, Italy.
School of Medicine, Vita-Salute San Raffaele University, Milan, Italy.
Experimental Imaging Center, Radiology Unit, IRCCS San Raffaele Scientific Institute, Milan, Italy.

Sara Benedetti (S)

UOC Screening Neonatale e Malattie Metaboliche, ASST Fatebenefratelli Sacco-Ospedale dei Bambini "Vittore Buzzi," Milan, Italy.

Paolo Della Bella (P)

Department of Cardiac Electrophysiology and Arrhythmology, IRCCS San Raffaele Scientific Institute, Milan, Italy.

Classifications MeSH