Histopathological characteristics of the arrhythmogenic right ventricular cardiomyopathy presenting the electrocardiographic characteristics with Brugada syndrome.
Brugada syndrome
arrhythmogenic right ventricular cardiomyopathy
autopsy
fibrofatty degeneration
ventricular tachycardia
Journal
Journal of cardiovascular electrophysiology
ISSN: 1540-8167
Titre abrégé: J Cardiovasc Electrophysiol
Pays: United States
ID NLM: 9010756
Informations de publication
Date de publication:
09 2023
09 2023
Historique:
revised:
16
07
2023
received:
11
01
2023
accepted:
01
08
2023
medline:
18
9
2023
pubmed:
9
8
2023
entrez:
9
8
2023
Statut:
ppublish
Résumé
The histopathological characteristics of the overlapping disease states of Brugada syndrome (BrS) and arrhythmogenic right ventricular cardiomyopathy (ARVC) have not been fully elucidated. A 71-year-old man showed coved-type ST-segment elevation with the right precordial leads, and the echocardiography demonstrated right ventricular (RV) dilatation. After 11 months, he died of a polymorphic VT storm. The pathological tissue demonstrated fibrofatty degeneration in the free wall of the RV outflow tract based on the heart autopsy. The overlapping disease states of BrS and ARVC showed histopathological characteristics consistent with ARVC.
Types de publication
Case Reports
Langues
eng
Sous-ensembles de citation
IM
Pagination
2006-2009Informations de copyright
© 2023 Wiley Periodicals LLC.
Références
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