Unusual Vascular Ring in the Fetus.

Dysphagia Left aortic arch Right arterial duct Stridor Tracheal compression Vascular ring

Journal

Pediatric cardiology
ISSN: 1432-1971
Titre abrégé: Pediatr Cardiol
Pays: United States
ID NLM: 8003849

Informations de publication

Date de publication:
11 Aug 2023
Historique:
received: 01 05 2023
accepted: 31 07 2023
medline: 11 8 2023
pubmed: 11 8 2023
entrez: 11 8 2023
Statut: aheadofprint

Résumé

We present the clinical course and echocardiographic and genetic findings of two fetuses with an unusual vascular ring, created by a left aortic arch with a right arterial duct and an aberrant right subclavian artery. One fetus was diagnosed with 22q11.2 microdeletion and the other became symptomatic in infancy. It is important to consider the position of the arterial ductal ligament in patients who present with tracheoesophageal compressive symptoms in the presence of a left aortic arch. These cases also highlight that a vascular ring formed from a left arch may have similar associations to a vascular ring formed by a right aortic arch.

Identifiants

pubmed: 37566242
doi: 10.1007/s00246-023-03261-3
pii: 10.1007/s00246-023-03261-3
doi:

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Informations de copyright

© 2023. The Author(s), under exclusive licence to Springer Science+Business Media, LLC, part of Springer Nature.

Références

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Auteurs

A Savis (A)

Department of Congenital Heart Disease, Evelina London Children's Hospital, Westminster Bridge Road, London, SE1 7EH, UK.

C Oakley (C)

Department of Congenital Heart Disease, Evelina London Children's Hospital, Westminster Bridge Road, London, SE1 7EH, UK.

M P M Van Poppel (MPM)

School of Biomedical Engineering and Imaging Sciences, King's College London, London, UK.

D F A Lloyd (DFA)

Department of Congenital Heart Disease, Evelina London Children's Hospital, Westminster Bridge Road, London, SE1 7EH, UK.
School of Biomedical Engineering and Imaging Sciences, King's College London, London, UK.

K Pushparajah (K)

Department of Congenital Heart Disease, Evelina London Children's Hospital, Westminster Bridge Road, London, SE1 7EH, UK.
School of Biomedical Engineering and Imaging Sciences, King's College London, London, UK.

T V Vigneswaran (TV)

Department of Congenital Heart Disease, Evelina London Children's Hospital, Westminster Bridge Road, London, SE1 7EH, UK.
Harris Birthright Centre for Fetal Medicine, King's College Hospital NHS Foundation Trust, London, UK.

V Zidere (V)

Department of Congenital Heart Disease, Evelina London Children's Hospital, Westminster Bridge Road, London, SE1 7EH, UK. Vita.zidere@gstt.nhs.uk.
Harris Birthright Centre for Fetal Medicine, King's College Hospital NHS Foundation Trust, London, UK. Vita.zidere@gstt.nhs.uk.

Classifications MeSH