Maintenance Chemotherapy for Patients with Rhabdomyosarcoma.

low-dose chemotherapy maintenance chemotherapy metronomic chemotherapy rhabdomyosarcoma

Journal

Cancers
ISSN: 2072-6694
Titre abrégé: Cancers (Basel)
Pays: Switzerland
ID NLM: 101526829

Informations de publication

Date de publication:
07 Aug 2023
Historique:
received: 22 06 2023
revised: 28 07 2023
accepted: 28 07 2023
medline: 12 8 2023
pubmed: 12 8 2023
entrez: 12 8 2023
Statut: epublish

Résumé

Maintenance chemotherapy (MC) defines the administration of prolonged relatively low-intensity chemotherapy with the aim of "maintaining" tumor complete remission. This paper aims to report an update of the RMS2005 trial, which demonstrated better survival for patients with high-risk localized rhabdomyosarcoma (RMS) when MC with vinorelbine and low-dose cyclophosphamide was added to standard chemotherapy, and to discuss the published experience on MC in RMS. In the RMS2005 study, the outcome for patients receiving MC vs. those who stopped the treatment remains superior, with a 5-year disease-free survival of 78.1% vs. 70.1% (

Identifiants

pubmed: 37568826
pii: cancers15154012
doi: 10.3390/cancers15154012
pmc: PMC10417571
pii:
doi:

Types de publication

Journal Article Review

Langues

eng

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Auteurs

Gianni Bisogno (G)

Department of Women's and Children's Health, University of Padua, 35128 Padua, Italy.
Pediatric Hematology Oncology Division, University Hospital of Padua, 35128 Padua, Italy.

Veronique Minard-Colin (V)

Department of Pediatric and Adolescent Oncology, Institut Gustave-Roussy, Université Paris-Saclay, 94800 Villejuif, France.

Meriel Jenney (M)

Department of Paediatric Oncology, Children's Hospital for Wales, Heath Park, Cardiff CF14 4XW, UK.

Andrea Ferrari (A)

Pediatric Oncology Unit, Fondazione IRCCS Istituto Nazionale Tumori, 20133 Milan, Italy.

Julia Chisholm (J)

Children and Young People's Unit, Royal Marsden Hospital and Institute of Cancer Research, Sutton SM2 5PT, UK.

Daniela Di Carlo (D)

Department of Women's and Children's Health, University of Padua, 35128 Padua, Italy.

Lisa Lyngsie Hjalgrim (LL)

Department of Paediatric and Adolescent Medicine, University Hospital Copenhagen, 2100 Copenhagen, Denmark.

Daniel Orbach (D)

SIREDO Oncology Centre (Care, Innovation and Research for Children, Adolescents and Young Adults with Cancer), Institut Curie, Paris Sciences et Lettres L University, 75005 Paris, France.

Johannes Hendrikus Maria Merks (JHM)

Princess Máxima Centre for Pediatric Oncology, 3584 CS Utrecht, The Netherlands.
Division of Imaging and Oncology, University Medical Center Utrecht, 3584 CX Utrecht, The Netherlands.

Michela Casanova (M)

Pediatric Oncology Unit, Fondazione IRCCS Istituto Nazionale Tumori, 20133 Milan, Italy.

Classifications MeSH