T-cell Large Granular Lymphocytic Leukemia and Felty Syndrome in Rheumatoid Arthritis: A Case Report.

felty’s syndrome large granular lymphocytic leukemia lgl leukemia neutropenia rheumatoid arthritis t-cell leukemia

Journal

Cureus
ISSN: 2168-8184
Titre abrégé: Cureus
Pays: United States
ID NLM: 101596737

Informations de publication

Date de publication:
Jul 2023
Historique:
accepted: 12 07 2023
medline: 14 8 2023
pubmed: 14 8 2023
entrez: 14 8 2023
Statut: epublish

Résumé

T-cell large granular lymphocytic (LGL) leukemia is characterized by a clonal proliferation of CD3+ T-cells and has been associated with rheumatoid arthritis (RA). Splenomegaly is a common finding and a majority of cases present with cytopenia. Felty syndrome (FS) is characterized by neutropenia and splenomegaly and is also classically described in the literature for its association with RA. Similarities in clinical features, pathogenesis, management, genetics, and immunologic basis of FS and T-cell LGL leukemia have led to the suggestion that they exist on the same spectrum of disease. We present a case of T-cell LGL leukemia in an RA patient with clinical features not distinguishable from features of FS.

Identifiants

pubmed: 37575786
doi: 10.7759/cureus.41780
pmc: PMC10419330
doi:

Types de publication

Case Reports

Langues

eng

Pagination

e41780

Informations de copyright

Copyright © 2023, Prasad et al.

Déclaration de conflit d'intérêts

The authors have declared that no competing interests exist.

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Auteurs

Supritha Prasad (S)

Internal Medicine, University of Illinois at Chicago, Chicago, USA.

Iman Mushfiq Farooqui (I)

Medicine, Aga Khan University, Karachi, PAK.
Rheumatology, University of Illinois at Chicago, Chicago, USA.

Lujain AlZoubi (L)

Medicine, The University of Jordan, Amman, JOR.
Rheumatology, University of Illinois at Chicago, Chicago, USA.

Shiva Arami (S)

Rheumatology, University of Illinois at Chicago, Chicago, USA.

Classifications MeSH