A Hemoglobin Variant Causing an Unexplained Low Oxygen Saturation by Pulse Oximetry: Two Case Reports.

hematology hemoglobinopathies neonatology oxygen saturation pulse oximetry

Journal

Cureus
ISSN: 2168-8184
Titre abrégé: Cureus
Pays: United States
ID NLM: 101596737

Informations de publication

Date de publication:
Jul 2023
Historique:
accepted: 20 07 2023
medline: 21 8 2023
pubmed: 21 8 2023
entrez: 21 8 2023
Statut: epublish

Résumé

Pulse oximetry is now routinely used in neonatal resuscitation and for neonatal screening for congenital heart diseases. Beyond respiratory and cardiac diseases, hemoglobin (Hb) variants must be included in the differential diagnosis of low oxygen saturation detected by pulse oximetry. We aim to describe two cases of fetal Hb variant (heterozygous γ-globin gene (HBG1) mutation in exon 2 c.202G>A (p.Val68Met)), which was identified in two unrelated newborns.

Identifiants

pubmed: 37602010
doi: 10.7759/cureus.42182
pmc: PMC10439765
doi:

Types de publication

Case Reports

Langues

eng

Pagination

e42182

Informations de copyright

Copyright © 2023, Rua et al.

Déclaration de conflit d'intérêts

The authors have declared that no competing interests exist.

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Auteurs

Inês B Rua (IB)

Neonatology Department, Maternidade Daniel de Matos, Centro Hospitalar e Universitário de Coimbra, Coimbra, PRT.

Beatriz Vala (B)

Pediatrics Department, Centro Hospitalar de Leiria, Leiria, PRT.

Inês Gameiro (I)

Neonatology Department, Maternidade Daniel de Matos, Centro Hospitalar e Universitário de Coimbra, Coimbra, PRT.

João R Martins (JR)

Neonatology Department, Maternidade Daniel de Matos, Centro Hospitalar e Universitário de Coimbra, Coimbra, PRT.

Rui Castelo (R)

Neonatology Department, Maternidade Daniel de Matos, Centro Hospitalar e Universitário de Coimbra, Coimbra, PRT.

Classifications MeSH