Extremely Preterm Infants with a Near-total Absence of Cerebellum: Usefulness of Quantitative Magnetic Resonance in Predicting the Motor Outcome.

Extremely preterm infants MRI Near-total absence of cerebellum Visual and volumetric scoring systems

Journal

Cerebellum (London, England)
ISSN: 1473-4230
Titre abrégé: Cerebellum
Pays: United States
ID NLM: 101089443

Informations de publication

Date de publication:
21 Aug 2023
Historique:
accepted: 09 08 2023
medline: 21 8 2023
pubmed: 21 8 2023
entrez: 21 8 2023
Statut: aheadofprint

Résumé

This study aims to evaluate in extremely premature infants the severity of brain structural injury causing total absence or near-total absence of cerebellar hemispheres by using MRI visual and volumetric scoring systems. It also aims to assess the role of the score systems in predicting motor outcome. We developed qualitative and quantitative MRI scoring systems to grade the overall brain damage severity in 16 infants with total absence or near-total absence of cerebellar hemispheres. The qualitative scoring system assessed the severity of macrostructural abnormalities of cerebellum, brainstem, supratentorial gray and white matters, ventricles while the quantitative scoring system weighted the loss of brain tissue volumes, and gross motor function classification system (GMFCS) was used to assess motor function at 1- and 5-year follow-ups.Positive correlations between both MRI scores and GMFCS scales were detected at follow-ups (p > 0.05), but only the volumetric score could identify those infants developing higher levels of motor impairment.Brain volumetric MRI offers an unbiassed assessment of prenatal brain damage. The quantitative scoring system, performed at term equivalent age, can be a helpful tool for predicting the long-term motor outcome in extremely preterm infants with a near-total absence of cerebellum.

Identifiants

pubmed: 37603264
doi: 10.1007/s12311-023-01593-7
pii: 10.1007/s12311-023-01593-7
doi:

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Informations de copyright

© 2023. The Author(s), under exclusive licence to Springer Science+Business Media, LLC, part of Springer Nature.

Références

Miall LS, Cornette LG, Tanner SF, Arthur RJ, Levene MI. Posterior fossa abnormalities seen on magnetic resonance brain imaging in a cohort of newborn infants. J Perinatol Off J Calif Perinat Assoc. 2003;23:396–403.
Poretti A, Prayer D, Boltshauser E. Morphological spectrum of prenatal cerebellar disruptions. Eur J Paediatr Neurol EJPN Off J Eur Paediatr Neurol Soc. 2009;13:397–407.
doi: 10.1016/j.ejpn.2008.09.001
Benbir G, Kara S, Yalcinkaya BC, Karhkaya G, Tuysuz B, Kocer N, et al. Unilateral cerebellar hypoplasia with different clinical features. Cerebellum Lond Engl. 2011;10:49–60.
doi: 10.1007/s12311-010-0225-2
Grunnet ML, Shields WD. Cerebellar hemorrhage in the premature infant. J Pediatr. 1976;88:605–8.
pubmed: 1255321 doi: 10.1016/S0022-3476(76)80019-4
Mercuri E, He J, Curati WL, Dubowitz LM, Cowan FM, Bydder GM. Cerebellar infarction and atrophy in infants and children with a history of premature birth. Pediatr Radiol. 1997;27:139–43.
pubmed: 9028846 doi: 10.1007/s002470050085
Rollins NK, Wen TS, Dominguez R. Crossed cerebellar atrophy in children: a neurologic sequela of extreme prematurity. Pediatr Radiol. 1995;25(Suppl 1):S20–5.
pubmed: 8577528 doi: 10.1007/BF03545574
Tam EWY, Ferriero DM, Xu D, Berman JI, Vigneron DB, Barkovich AJ, et al. Cerebellar development in the preterm neonate: effect of supratentorial brain injury. Pediatr Res. 2009;66:102–6.
pubmed: 19287350 pmcid: 2700193 doi: 10.1203/PDR.0b013e3181a1fb3d
Gano D, Barkovich AJ. Cerebellar hypoplasia of prematurity: causes and consequences. Handb Clin Neurol. 2019;162:201–16.
pubmed: 31324311 doi: 10.1016/B978-0-444-64029-1.00009-6
Lee C, Kim DW, Jeon GS, Roh EJ, Seo JH, Wang KC, et al. Cerebellar alterations induced by chronic hypoxia: an immunohistochemical study using a chick embryonic model. Brain Res. 2001;901:271–6.
pubmed: 11368977 doi: 10.1016/S0006-8993(01)02362-9
Robins JB, Mason GC, Watters J, Martinez D. Case report: cerebellar hemi-hypoplasia. Prenat Diagn. 1998;18:173–7.
pubmed: 9516019 doi: 10.1002/(SICI)1097-0223(199802)18:2<173::AID-PD227>3.0.CO;2-A
Hiller L, McGahan JP, Bijan B, Melendres G, Towner D. Sonographic detection of in utero isolated cerebellar hemorrhage. J Ultrasound Med Off J Am Inst Ultrasound Med. 2003;22:649–52.
Boltshauser E. Cerebellum-small brain but large confusion: a review of selected cerebellar malformations and disruptions. Am J Med Genet A. 2004;126A:376–85.
pubmed: 15098235 doi: 10.1002/ajmg.a.20662
Poretti A, Limperopoulos C, Roulet-Perez E, Wolf NI, Rauscher C, Prayer D, et al. Outcome of severe unilateral cerebellar hypoplasia. Dev Med Child Neurol. 2010;52:718–24.
pubmed: 19863638 doi: 10.1111/j.1469-8749.2009.03522.x
Poretti A, Boltshauser E, Doherty D. Cerebellar hypoplasia: differential diagnosis and diagnostic approach. Am J Med Genet C: Semin Med Genet. 2014;166C:211–26.
pubmed: 24839100 doi: 10.1002/ajmg.c.31398
Poretti A, Boltshauser E. Terminology in morphological anomalies of the cerebellum does matter. Cerebellum Ataxias. 2015;2:8.
pubmed: 26331051 pmcid: 4552363 doi: 10.1186/s40673-015-0027-x
Yu F, Jiang Q, Sun X, Zhang R. A new case of complete primary cerebellar agenesis: clinical and imaging findings in a living patient. Brain J Neurol. 2015;138:e353.
doi: 10.1093/brain/awu239
Kidokoro H, Neil JJ, Inder TE. New MR imaging assessment tool to define brain abnormalities in very preterm infants at term. AJNR Am J Neuroradiol. 2013;34:2208–14.
pubmed: 23620070 pmcid: 4163698 doi: 10.3174/ajnr.A3521
Kidokoro H, Anderson PJ, Doyle LW, Woodward LJ, Neil JJ, Inder TE. Brain injury and altered brain growth in preterm infants: predictors and prognosis. Pediatrics. 2014;134:e444–53.
pubmed: 25070300 doi: 10.1542/peds.2013-2336
Miller SP, Ferriero DM, Leonard C, Piecuch R, Glidden DV, Partridge JC, et al. Early brain injury in premature newborns detected with magnetic resonance imaging is associated with adverse early neurodevelopmental outcome. J Pediatr. 2005;147:609–16.
pubmed: 16291350 doi: 10.1016/j.jpeds.2005.06.033
Inder TE, Wells SJ, Mogridge NB, Spencer C, Volpe JJ. Defining the nature of the cerebral abnormalities in the premature infant: a qualitative magnetic resonance imaging study. J Pediatr. 2003;143:171–9.
pubmed: 12970628 doi: 10.1067/S0022-3476(03)00357-3
Sie LTL, Hart AAM, van Hof J, de Groot L, Lems W, Lafeber HN, et al. Predictive value of neonatal MRI with respect to late MRI findings and clinical outcome. A study in infants with periventricular densities on neonatal ultrasound. Neuropediatrics. 2005;36:78–89.
pubmed: 15822020 doi: 10.1055/s-2005-837574
George JM, Fiori S, Fripp J, Pannek K, Bursle J, Moldrich RX, et al. Validation of an MRI brain injury and growth scoring system in very preterm infants scanned at 29- to 35-week postmenstrual age. AJNR Am J Neuroradiol. 2017;38:1435–42.
pubmed: 28522659 pmcid: 7959923 doi: 10.3174/ajnr.A5191
Limperopoulos C, Chilingaryan G, Sullivan N, Guizard N, Robertson RL, du Plessis AJ. Injury to the premature cerebellum: outcome is related to remote cortical development. Cereb Cortex N Y N. 1991;2014(24):728–36.
Tam EWY, Rosenbluth G, Rogers EE, Ferriero DM, Glidden D, Goldstein RB, et al. Cerebellar hemorrhage on magnetic resonance imaging in preterm newborns associated with abnormal neurologic outcome. J Pediatr. 2011;158:245–50.
pubmed: 20833401 doi: 10.1016/j.jpeds.2010.07.049
Nguyen The Tich S, Anderson PJ, Shimony JS, Hunt RW, Doyle LW, Inder TE. A novel quantitative simple brain metric using MR imaging for preterm infants. AJNR Am J Neuroradiol. 2009;30:125–31.
pubmed: 18832662 doi: 10.3174/ajnr.A1309
Sener RN, Jinkins JR. Subtotal agenesis of the cerebellum in an adult: MRI demonstration. Neuroradiology. 1993;35:286–7.
pubmed: 8492897 doi: 10.1007/BF00602617
Poretti A, Boltshauser E, Huisman TAGM. Prenatal cerebellar disruptions: neuroimaging spectrum of findings in correlation with likely mechanisms and etiologies of injury. Neuroimaging Clin N Am. 2016;26:359–72.
pubmed: 27423799 doi: 10.1016/j.nic.2016.03.006
Calandrelli R, D’Apolito G, Marco P, Zampino G, Tartaglione T, Colosimo C. Costello syndrome: analysis of the posterior cranial fossa in children with posterior fossa crowding. Neuroradiol J. 2015;28:254–8.
pubmed: 26246091 pmcid: 4757298 doi: 10.1177/1971400915592549
Yushkevich PA, Piven J, Hazlett HC, Smith RG, Ho S, Gee JC, et al. User-guided 3D active contour segmentation of anatomical structures: significantly improved efficiency and reliability. Neuroimage. 2006;31:1116–28.
pubmed: 16545965 doi: 10.1016/j.neuroimage.2006.01.015
Calandrelli R, Panfili M, D’Apolito G, Zampino G, Pedicelli A, Pilato F, et al. Quantitative approach to the posterior cranial fossa and craniocervical junction in asymptomatic children with achondroplasia. Neuroradiology. 2017;59:1031–41.
pubmed: 28819680 doi: 10.1007/s00234-017-1887-y
Calandrelli R, D’Apolito G, Panfili M, Massimi L, Caldarelli M, Colosimo C. Role of “major” and “minor” lambdoid arch sutures in posterior cranial fossa changes: mechanism of cerebellar tonsillar herniation in infants with multisutural craniosynostosis. Childs Nerv Syst ChNS Off J Int Soc Pediatr Neurosurg. 2016;32:451–9.
doi: 10.1007/s00381-015-2956-3
Calandrelli R, Pilato F, Massimi L, Panfili M, Di Rocco C, Colosimo C. Quantitative analysis of cranial-orbital changes in infants with anterior synostotic plagiocephaly. Childs Nerv Syst ChNS Off J Int Soc Pediatr Neurosurg. 2018;34:1725–33.
doi: 10.1007/s00381-018-3824-8
Calandrelli R, Pilato F, Massimi L, Panfili M, Colosimo C. A systematic quantitative morpho-volumetric analysis in infants with sagittal craniosynostosis and relationship with the severity of scaphocephalic deformity. Radiol Med (Torino). 2020;125:585–94.
pubmed: 32067161 doi: 10.1007/s11547-020-01150-w
Balikci A, May-Benson TA, Aracikul Balikci AF, Tarakci E, Ikbal Dogan Z, Ilbay G. Evaluation of Ayres Sensory Integration® intervention on sensory processing and motor function in a child with rubinstein-taybi syndrome: a case report. Clin Med Insights Case Rep. 2023;16:11795476221148866.
pubmed: 36760339 pmcid: 9903040 doi: 10.1177/11795476221148866
Salavati M, Krijnen WP, Rameckers EAA, Looijestijn PL, CGB M, van der Schans CP, et al. Reliability of the modified gross motor function measure-88 (GMFM-88) for children with both spastic cerebral palsy and cerebral visual impairment: a preliminary study. Res Dev Disabil. 2015;45–46:32–48.
pubmed: 26210850 doi: 10.1016/j.ridd.2015.07.013
Papile LA, Burstein J, Burstein R, Koffler H. Incidence and evolution of subependymal and intraventricular hemorrhage: a study of infants with birth weights less than 1,500 gm. J Pediatr. 1978;92:529–34.
pubmed: 305471 doi: 10.1016/S0022-3476(78)80282-0
Limperopoulos C, Robertson RL, Sullivan NR, Bassan H, du Plessis AJ. Cerebellar injury in term infants: clinical characteristics, magnetic resonance imaging findings, and outcome. Pediatr Neurol. 2009;41:1–8.
pubmed: 19520266 doi: 10.1016/j.pediatrneurol.2009.02.007
Bodensteiner JB, Johnsen SD. Cerebellar injury in the extremely premature infant: newly recognized but relatively common outcome. J Child Neurol. 2005;20:139–42.
pubmed: 15794181 doi: 10.1177/08830738050200021101
Messerschmidt A, Brugger PC, Boltshauser E, Zoder G, Sterniste W, Birnbacher R, et al. Disruption of cerebellar development: potential complication of extreme prematurity. AJNR Am J Neuroradiol. 2005;26:1659–67.
pubmed: 16091510 pmcid: 7975176
Kline JE, Sita Priyanka Illapani V, He L, Parikh NA. Automated brain morphometric biomarkers from MRI at term predict motor development in very preterm infants. NeuroImage Clin. 2020;28:102475.
pubmed: 33395969 pmcid: 7649646 doi: 10.1016/j.nicl.2020.102475
Parikh NA, Lasky RE, Kennedy KA, McDavid G, Tyson JE. Perinatal factors and regional brain volume abnormalities at term in a cohort of extremely low birth weight infants. PLoS One. 2013;8:e62804.
pubmed: 23671636 pmcid: 3650008 doi: 10.1371/journal.pone.0062804
Woodward LJ, Anderson PJ, Austin NC, Howard K, Inder TE. Neonatal MRI to predict neurodevelopmental outcomes in preterm infants. N Engl J Med. 2006;355:685–94.
pubmed: 16914704 doi: 10.1056/NEJMoa053792
Balakrishnan U, Amboiram P, Ninan B, Chandrasekar A, Rangasami R. Correlation among magnetic resonance imaging parameters of brain in preterm neonates at term equivalent age. Indian J Pediatr. 2017;84:13–9.
pubmed: 27619814 doi: 10.1007/s12098-016-2215-y
Volpe JJ. Brain injury in premature infants: a complex amalgam of destructive and developmental disturbances. Lancet Neurol. 2009;8:110–24.
pubmed: 19081519 pmcid: 2707149 doi: 10.1016/S1474-4422(08)70294-1
Calandrelli R, Marco P, Tran HE, Colosimo C, Pilato F. A novel radiological score system to assess the clinical severity in patients with acute cerebellitis. Cerebellum Lond Engl. 2023;22:173–82.
doi: 10.1007/s12311-022-01377-5
Jiang X, Faber J, Giordano I, Machts J, Kindler C, Dudesek A, et al. Characterization of cerebellar atrophy and resting state functional connectivity patterns in sporadic adult-onset ataxia of unknown etiology (SAOA). Cerebellum Lond Engl. 2019;18:873–81.
doi: 10.1007/s12311-019-01072-y
Zhang H, Ji S, Ren S, Liu M, Ran W, Zhang X, et al. Cerebellar atrophy in multiple system atrophy (cerebellar type) and its implication for network connectivity. Cerebellum Lond Engl. 2020;19:636–44.
doi: 10.1007/s12311-020-01144-4
Peterson BS, Vohr B, Staib LH, Cannistraci CJ, Dolberg A, Schneider KC, et al. Regional brain volume abnormalities and long-term cognitive outcome in preterm infants. JAMA. 2000;284:1939–47.
pubmed: 11035890 doi: 10.1001/jama.284.15.1939
Narberhaus A, Segarra D, Caldú X, Giménez M, Pueyo R, Botet F, et al. Corpus callosum and prefrontal functions in adolescents with history of very preterm birth. Neuropsychologia. 2008;46:111–6.
pubmed: 17897687 doi: 10.1016/j.neuropsychologia.2007.08.004
ten Donkelaar HJ, Lammens M, Wesseling P, Thijssen HOM, Renier WO. Development and developmental disorders of the human cerebellum. J Neurol. 2003;250:1025–36.
pubmed: 14504962 doi: 10.1007/s00415-003-0199-9
Molinari M, Filippini V, Leggio MG. Neuronal plasticity of interrelated cerebellar and cortical networks. Neuroscience. 2002;111:863–70.
pubmed: 12031409 doi: 10.1016/S0306-4522(02)00024-6
Mehrkanoon S, Boonstra TW, Breakspear M, Hinder M, Summers JJ. Upregulation of cortico-cerebellar functional connectivity after motor learning. NeuroImage. 2016;128:252–63.
pubmed: 26767943 doi: 10.1016/j.neuroimage.2015.12.052
Yamamoto T, Hayashi T, Murata Y, Ose T, Higo N. Premotor cortical-cerebellar reorganization in a macaque model of primary motor cortical lesion and recovery. J Neurosci. 2019;39:8484–96.
pubmed: 31582526 pmcid: 6807278 doi: 10.1523/JNEUROSCI.0077-19.2019
Pagnozzi AM, van Eijk L, Pannek K, Boyd RN, Saha S, George J, et al. Early brain morphometrics from neonatal MRI predict motor and cognitive outcomes at 2-years corrected age in very preterm infants. NeuroImage. 2023;267:119815.
pubmed: 36529204 doi: 10.1016/j.neuroimage.2022.119815

Auteurs

Rosalinda Calandrelli (R)

Radiology and Neuroradiology Unit, Department of Imaging, Radiation Therapy and Hematology, Fondazione Policlinico Universitario Agostino Gemelli IRCCS, Largo A. Gemelli 1, 00168, Rome, Italy. rosalinda.calandrelli@policlinicogemelli.it.

Laura Tuzza (L)

Radiology and Neuroradiology Unit, Department of Imaging, Radiation Therapy and Hematology, Fondazione Policlinico Universitario Agostino Gemelli IRCCS, Largo A. Gemelli 1, 00168, Rome, Italy.

Domenico Marco Romeo (DM)

Pediatric Neurology Unit, Fondazione Policlinico Universitario A. Gemelli IRCCS, 00168, Rome, Italy.
Pediatric Neurology Unit, Università Cattolica del Sacro Cuore, 00168, Rome, Italy.

Chiara Arpaia (C)

Pediatric Neurology Unit, Fondazione Policlinico Universitario A. Gemelli IRCCS, 00168, Rome, Italy.
Pediatric Neurology Unit, Università Cattolica del Sacro Cuore, 00168, Rome, Italy.

Cesare Colosimo (C)

Radiology and Neuroradiology Unit, Department of Imaging, Radiation Therapy and Hematology, Fondazione Policlinico Universitario Agostino Gemelli IRCCS, Largo A. Gemelli 1, 00168, Rome, Italy.
Istituto di Radiologia, Università Cattolica del Sacro Cuore, Rome, Italy.

Fabio Pilato (F)

Research Unit of Neurology, Department of Medicine and Surgery, Università Campus Bio-Medico di Roma, Via Alvaro del Portillo, 21, -00128, Rome, Italy.
Fondazione Policlinico Universitario Campus Bio-Medico, Via Alvaro del Portillo, 200, -00128, Rome, Italy.

Classifications MeSH