Uncovering a Novel Site of Ewing's Sarcoma: the Hypopharynx.
Airway emergency
Ewing's sarcoma
Hypopharynx
Pediatric
Rare tumor
Surgery
Journal
Indian journal of otolaryngology and head and neck surgery : official publication of the Association of Otolaryngologists of India
ISSN: 2231-3796
Titre abrégé: Indian J Otolaryngol Head Neck Surg
Pays: India
ID NLM: 9422551
Informations de publication
Date de publication:
Sep 2023
Sep 2023
Historique:
received:
11
04
2023
accepted:
18
04
2023
pmc-release:
01
09
2024
medline:
28
8
2023
pubmed:
28
8
2023
entrez:
28
8
2023
Statut:
ppublish
Résumé
Ewing's sarcoma is usually seen in bones but 20-30% are found in extra skeletal soft tissues like in head and neck region. We present the case of Ewing sarcoma of hypopharynx in a 1 year old child who presented to us with acute respiratory distress. Child was intubated using videolaryngoscope and mass was removed using microdebrider. Final histopathological examination revealed Ewing sarcoma. EWSR1 gene rearrangement studies were advised, which the patient refused. Post-operative patient was started on adjuvant chemotherapy. PET CT after 2 months showed no FDG avid lesions within or elsewhere in the region of the body surveyed. There is no case of Ewing's sarcoma in hypopharynx reported to date. The clinical presentation, management and outcome has been discussed with a review of the literature.
Identifiants
pubmed: 37636598
doi: 10.1007/s12070-023-03821-2
pii: 3821
pmc: PMC10447781
doi:
Types de publication
Journal Article
Langues
eng
Pagination
2630-2633Informations de copyright
© Association of Otolaryngologists of India 2023. Springer Nature or its licensor (e.g. a society or other partner) holds exclusive rights to this article under a publishing agreement with the author(s) or other rightsholder(s); author self-archiving of the accepted manuscript version of this article is solely governed by the terms of such publishing agreement and applicable law.
Déclaration de conflit d'intérêts
Conflict of interestAll authors certify that they have no affiliations with or involvement in any organization or entity with any financial interest or non-financial interest in the subject matter or materials discussed in this manuscript.
Références
Eur J Cancer. 1998 Jun;34(7):1050-62
pubmed: 9849454
Ann Otol Rhinol Laryngol. 2017 Mar;126(3):179-184
pubmed: 28056517
Curr Oncol. 2019 Aug;26(4):e574-e577
pubmed: 31548827
Strahlenther Onkol. 2013 Jul;189(7):586-9
pubmed: 23732462
Eur J Nucl Med Mol Imaging. 2009 Jan;36(1):23-36
pubmed: 18719909
Int J Pediatr Otorhinolaryngol. 1999 May 25;48(3):209-16
pubmed: 10402117
Cancer. 2011 Jul 1;117(13):3027-32
pubmed: 21692057
Lancet. 2022 Oct 29;400(10362):1513-1521
pubmed: 36522207
J Clin Oncol. 2012 Nov 20;30(33):4148-54
pubmed: 23091096
J Clin Oncol. 2011 Apr 1;29(10):1304-11
pubmed: 21357792