Uncovering a Novel Site of Ewing's Sarcoma: the Hypopharynx.

Airway emergency Ewing's sarcoma Hypopharynx Pediatric Rare tumor Surgery

Journal

Indian journal of otolaryngology and head and neck surgery : official publication of the Association of Otolaryngologists of India
ISSN: 2231-3796
Titre abrégé: Indian J Otolaryngol Head Neck Surg
Pays: India
ID NLM: 9422551

Informations de publication

Date de publication:
Sep 2023
Historique:
received: 11 04 2023
accepted: 18 04 2023
pmc-release: 01 09 2024
medline: 28 8 2023
pubmed: 28 8 2023
entrez: 28 8 2023
Statut: ppublish

Résumé

Ewing's sarcoma is usually seen in bones but 20-30% are found in extra skeletal soft tissues like in head and neck region. We present the case of Ewing sarcoma of hypopharynx in a 1 year old child who presented to us with acute respiratory distress. Child was intubated using videolaryngoscope and mass was removed using microdebrider. Final histopathological examination revealed Ewing sarcoma. EWSR1 gene rearrangement studies were advised, which the patient refused. Post-operative patient was started on adjuvant chemotherapy. PET CT after 2 months showed no FDG avid lesions within or elsewhere in the region of the body surveyed. There is no case of Ewing's sarcoma in hypopharynx reported to date. The clinical presentation, management and outcome has been discussed with a review of the literature.

Identifiants

pubmed: 37636598
doi: 10.1007/s12070-023-03821-2
pii: 3821
pmc: PMC10447781
doi:

Types de publication

Journal Article

Langues

eng

Pagination

2630-2633

Informations de copyright

© Association of Otolaryngologists of India 2023. Springer Nature or its licensor (e.g. a society or other partner) holds exclusive rights to this article under a publishing agreement with the author(s) or other rightsholder(s); author self-archiving of the accepted manuscript version of this article is solely governed by the terms of such publishing agreement and applicable law.

Déclaration de conflit d'intérêts

Conflict of interestAll authors certify that they have no affiliations with or involvement in any organization or entity with any financial interest or non-financial interest in the subject matter or materials discussed in this manuscript.

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Auteurs

T B Shashidhar (TB)

Artemis Health Institue, Gurugram, Haryana India.

Trisha Srivastava (T)

Artemis Health Institue, Gurugram, Haryana India.

Ankita Yadav (A)

Artemis Health Institue, Gurugram, Haryana India.

Varsha S Nambiar (VS)

Artemis Health Institue, Gurugram, Haryana India.

Classifications MeSH