A private hospital's approach to treating acute familial Mediterranean fever in Dar es Salaam.

Familial Mediterranean fever rheumatology

Journal

SAGE open medical case reports
ISSN: 2050-313X
Titre abrégé: SAGE Open Med Case Rep
Pays: England
ID NLM: 101638686

Informations de publication

Date de publication:
2023
Historique:
received: 02 05 2023
accepted: 03 08 2023
medline: 1 9 2023
pubmed: 1 9 2023
entrez: 1 9 2023
Statut: epublish

Résumé

Familial Mediterranean fever is a rare autosomal recessive autoinflammatory disorder prevalent in Middle Eastern populations, characterized by episodic abdominal pain. This case report presents a 34-year-old Egyptian man with severe lower abdominal pain, chest discomfort, and joint pain, along with a positive family history of familial Mediterranean fever but had no previous personal history of this condition. Blood work revealed leukocytosis with neutrophilia and elevated C-reactive protein and erythrocyte sedimentation rate. The patient received intravenous fluids, antiemetics, and analgesics before further evaluation. Diagnosis of familial Mediterranean fever relies on clinical symptoms, ethnic origin, and family history, supported by specific criteria. Typical familial Mediterranean fever attacks involve serositis-induced pain, recurrent episodes, short-duration fever (12 h to 3 days), and arthritis. Familial Mediterranean fever may mimic other acute abdominal conditions, warranting consideration, particularly in individuals from Mediterranean regions. Genetic testing is valuable in confirming familial Mediterranean fever diagnosis.

Identifiants

pubmed: 37654544
doi: 10.1177/2050313X231195964
pii: 10.1177_2050313X231195964
pmc: PMC10467234
doi:

Types de publication

Case Reports

Langues

eng

Pagination

2050313X231195964

Informations de copyright

© The Author(s) 2023.

Déclaration de conflit d'intérêts

The author(s) declared no potential conflicts of interest with respect to the research, authorship, and/or publication of this article.

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Auteurs

Willbroad Kyejo (W)

Department of Family Medicine, Aga Khan University, Dar es Salaam, Tanzania.

Musa Machibya (M)

Department of Accident and Emergency, Aga Khan Hospital, Dar es Salaam, Tanzania.

Faisal Hooda (F)

Department of Internal Medicine, Aga Khan Hospital, Dar es Salaam, Tanzania.

Waziri Gahhu (W)

Department of Accident and Emergency, Aga Khan Hospital, Dar es Salaam, Tanzania.

Shivangi Mandania (S)

Department of Accident and Emergency, Aga Khan Hospital, Dar es Salaam, Tanzania.

Neelam Ismail (N)

Department of Family Medicine, Aga Khan University, Dar es Salaam, Tanzania.

Nancy Matillya (N)

Department of Family Medicine, Aga Khan University, Dar es Salaam, Tanzania.

Kilalo Mjema (K)

Department of Accident and Emergency, Aga Khan Hospital, Dar es Salaam, Tanzania.

Kamran Hameed (K)

Department of Internal Medicine, Aga Khan Hospital, Dar es Salaam, Tanzania.

Classifications MeSH