Insights into the Value of Lyso-Gb1 as a Predictive Biomarker in Treatment-Naïve Patients with Gaucher Disease Type 1 in the LYSO-PROOF Study.

GD-DS3 Gaucher disease biomarkers glucosylsphingosine lyso-Gb1

Journal

Diagnostics (Basel, Switzerland)
ISSN: 2075-4418
Titre abrégé: Diagnostics (Basel)
Pays: Switzerland
ID NLM: 101658402

Informations de publication

Date de publication:
30 Aug 2023
Historique:
received: 13 07 2023
revised: 04 08 2023
accepted: 10 08 2023
medline: 9 9 2023
pubmed: 9 9 2023
entrez: 9 9 2023
Statut: epublish

Résumé

Gaucher disease (GD) is a rare autosomal recessive disorder arising from bi-allelic variants in the

Identifiants

pubmed: 37685353
pii: diagnostics13172812
doi: 10.3390/diagnostics13172812
pmc: PMC10487050
pii:
doi:

Types de publication

Journal Article

Langues

eng

Subventions

Organisme : Shire HG (now Takeda)
ID : Master Services Agreement 2011

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Auteurs

Filipa Curado (F)

CENTOGENE GmbH, 18055 Rostock, Germany.

Sabine Rösner (S)

CENTOGENE GmbH, 18055 Rostock, Germany.

Susanne Zielke (S)

CENTOGENE GmbH, 18055 Rostock, Germany.

Gina Westphal (G)

CENTOGENE GmbH, 18055 Rostock, Germany.

Ulrike Grittner (U)

Berlin Institute of Health, Charité-Universitätsmedizin Berlin, 10117 Berlin, Germany.
Institute of Biometry and Clinical Epidemiology, Charité-Universitätsmedizin Berlin, 10117 Berlin, Germany.

Volha Skrahina (V)

Rhythm Pharmaceuticals Inc., 20095 Hamburg, Germany.

Mohammed Alasel (M)

CENTOGENE GmbH, 18055 Rostock, Germany.

Ahmad Mehmood Malik (AM)

CENTOGENE GmbH, 18055 Rostock, Germany.

Christian Beetz (C)

CENTOGENE GmbH, 18055 Rostock, Germany.

Tobias Böttcher (T)

CENTOGENE GmbH, 18055 Rostock, Germany.

Gal Barel (G)

CENTOGENE GmbH, 18055 Rostock, Germany.

Ashish Prasad Sah (AP)

CENTOGENE GmbH, 18055 Rostock, Germany.

Tama Dinur (T)

Gaucher Unit, Shaare Zedek Medical Center, Jerusalem 9103102, Israel.

Nadeem Anjum (N)

The Children's Hospital and University of Child Health Sciences, Lahore 54600, Pakistan.

Quidad Ichraf (Q)

Children Hospital's Rabat, Neuropediatric-Metabolic, Rabat 6527, Morocco.

Yamna Kriouile (Y)

Children Hospital's Rabat, Neuropediatric-Metabolic, Rabat 6527, Morocco.

Zahra Hadipour (Z)

Soodbakhash Poly Clinic, Atiyeh Hospital, Tehran 1416753955, Iran.
Medical Genetics Department, Pars Research Center & Hospital, Tehran 1416753955, Iran.

Fatemeh Hadipour (F)

Soodbakhash Poly Clinic, Atiyeh Hospital, Tehran 1416753955, Iran.
Medical Genetics Department, Pars Research Center & Hospital, Tehran 1416753955, Iran.

Shoshana Revel-Vilk (S)

Gaucher Unit, Shaare Zedek Medical Center, Jerusalem 9103102, Israel.
Faculty of Medicine, Hebrew University of Jerusalem, Jerusalem 9112002, Israel.

Claudia Cozma (C)

CENTOGENE GmbH, 18055 Rostock, Germany.

Jörg Hartkamp (J)

CENTOGENE GmbH, 18055 Rostock, Germany.

Huma Cheema (H)

The Children's Hospital and University of Child Health Sciences, Lahore 54600, Pakistan.

Ari Zimran (A)

Gaucher Unit, Shaare Zedek Medical Center, Jerusalem 9103102, Israel.
Faculty of Medicine, Hebrew University of Jerusalem, Jerusalem 9112002, Israel.

Peter Bauer (P)

CENTOGENE GmbH, 18055 Rostock, Germany.
Medical Faculty, University of Rostock, 18057 Rostock, Germany.

Arndt Rolfs (A)

Medical Faculty, University of Rostock, 18057 Rostock, Germany.
Agyany Pharmaceutics Ltd., Jerusalem 9103102, Israel.
RCV Rare Disease GmbH, 10115 Berlin, Germany.

Classifications MeSH