Bilateral Panuveitis in an Adolescent with Autoimmune Lymphoproliferative Syndrome Due to CTLA4 Haploinsufficiency.

ALPS CTLA4 haploinsufficiency autoimmune lymphoproliferative syndrome uveitis

Journal

Ocular immunology and inflammation
ISSN: 1744-5078
Titre abrégé: Ocul Immunol Inflamm
Pays: England
ID NLM: 9312169

Informations de publication

Date de publication:
13 Sep 2023
Historique:
medline: 13 9 2023
pubmed: 13 9 2023
entrez: 13 9 2023
Statut: aheadofprint

Résumé

To describe a case of bilateral panuveitis in an 11-year-old girl with autoimmune lymphoproliferative syndrome (ALPS) due to A 5-year-old girl developed cervical adenopathy, and autoimmune hemolytic anemia and thrombocytopenia consistent with Evan's Syndrome. She was subsequently diagnosed with autosomal dominant Panuveitis may be associated with ALPS due to

Identifiants

pubmed: 37703496
doi: 10.1080/09273948.2023.2250441
doi:

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Pagination

1-5

Auteurs

Richmond Woodward (R)

Department of Ophthalmology, Duke University School of Medicine, Durham, North Carolina, USA.

Andrew Gross (A)

Department of Ophthalmology, Duke University School of Medicine, Durham, North Carolina, USA.

Grant A Justin (GA)

Department of Ophthalmology, Duke University School of Medicine, Durham, North Carolina, USA.

Glenn J Jaffe (GJ)

Department of Ophthalmology, Duke University School of Medicine, Durham, North Carolina, USA.

Dilraj S Grewal (DS)

Department of Ophthalmology, Duke University School of Medicine, Durham, North Carolina, USA.

Classifications MeSH