Case Report: Response to ipilimumab and nivolumab in a patient with adrenocortical carcinoma.

adrenal cancer adrenocortical cancer immunotherapy ipilimumab nivolumab

Journal

Frontiers in oncology
ISSN: 2234-943X
Titre abrégé: Front Oncol
Pays: Switzerland
ID NLM: 101568867

Informations de publication

Date de publication:
2023
Historique:
received: 19 06 2023
accepted: 11 08 2023
medline: 25 9 2023
pubmed: 25 9 2023
entrez: 25 9 2023
Statut: epublish

Résumé

Adrenocortical carcinoma (ACC) is a rare malignancy with limited treatment options. The evidence for the use of immunotherapy in ACC has been conflicting, with overall response rates ranging from 6 - 33%. We describe the case of a 32 year old patient who was initially thought to have an inoperable clear cell renal cell carcinoma and was treated with immunotherapy with ipilimumab and nivolumab. The patient had an excellent partial response to treatment. Further work-up prior to consideration of surgery demonstrated that the tumour was an ACC, rather than a renal cancer. She had a right adrenalectomy and right hepatectomy, achieving an R0 resection and remains disease-free one year after surgery. This case illustrates the challenge of diagnosing ACC, and that doublet immunotherapy with ipilimumab and nivolumab can have significant clinical efficacy in ACC.

Sections du résumé

Background UNASSIGNED
Adrenocortical carcinoma (ACC) is a rare malignancy with limited treatment options. The evidence for the use of immunotherapy in ACC has been conflicting, with overall response rates ranging from 6 - 33%.
Case presentation UNASSIGNED
We describe the case of a 32 year old patient who was initially thought to have an inoperable clear cell renal cell carcinoma and was treated with immunotherapy with ipilimumab and nivolumab. The patient had an excellent partial response to treatment. Further work-up prior to consideration of surgery demonstrated that the tumour was an ACC, rather than a renal cancer. She had a right adrenalectomy and right hepatectomy, achieving an R0 resection and remains disease-free one year after surgery.
Conclusion UNASSIGNED
This case illustrates the challenge of diagnosing ACC, and that doublet immunotherapy with ipilimumab and nivolumab can have significant clinical efficacy in ACC.

Identifiants

pubmed: 37746287
doi: 10.3389/fonc.2023.1242560
pmc: PMC10516602
doi:

Types de publication

Case Reports

Langues

eng

Pagination

1242560

Informations de copyright

Copyright © 2023 Charles, Madhu, Powles, Boyde, Hughes, Kumar and Moorcraft.

Déclaration de conflit d'intérêts

The authors declare that the research was conducted in the absence of any commercial or financial relationships that could be construed as a potential conflict of interest.

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Auteurs

Rebecca Charles (R)

Pathology Department, University Hospital of Wales, Cardiff, United Kingdom.

Divine Madhu (D)

School of Medicine, Cardiff University, Cardiff, United Kingdom.

Alexander Powles (A)

Radiology Department, Swansea Bay University Health Board, Swansea, United Kingdom.

Adam Boyde (A)

Pathology Department, University Hospital of Wales, Cardiff, United Kingdom.

Owen Hughes (O)

Department of Urology, University Hospital of Wales, Cardiff, United Kingdom.

Nagappan Kumar (N)

Cardiff Liver Unit, University Hospital of Wales, Cardiff, United Kingdom.

Sing Yu Moorcraft (SY)

Oncology Department, South West Wales Cancer Centre and Swansea University Medical School, Swansea, United Kingdom.

Classifications MeSH