Hyperinflammatory Immune Response in COVID-19: Host Genetic Factors in Pyrin Inflammasome and Immunity to Virus in a Spanish Population from Majorca Island.

COVID-19 Pyrin cytokine storm genetic markers hyperinflammatory immune response primary immunodeficiency

Journal

Biomedicines
ISSN: 2227-9059
Titre abrégé: Biomedicines
Pays: Switzerland
ID NLM: 101691304

Informations de publication

Date de publication:
16 Sep 2023
Historique:
received: 21 07 2023
revised: 31 08 2023
accepted: 05 09 2023
medline: 28 9 2023
pubmed: 28 9 2023
entrez: 28 9 2023
Statut: epublish

Résumé

The hyperinflammatory response caused by SARS-CoV-2 infection contributes to its severity, and many critically ill patients show features of cytokine storm (CS) syndrome. We investigated, by next-generation sequencing, 24 causative genes of primary immunodeficiencies whose defect predisposes to CS. We studied two cohorts with extreme phenotypes of SARS-CoV-2 infection: critical/severe hyperinflammatory patients (H-P) and asymptomatic patients (AM-risk-P) with a high risk (older age) to severe COVID-19. To explore inborn errors of the immunity, we investigated the presence of pathogenic or rare variants, and to identify COVID-19 severity-associated markers, we compared the allele frequencies of common genetic polymorphisms between our two cohorts. We found: 1 H-P carries the likely pathogenic variant c.887-2 A>C in the

Identifiants

pubmed: 37760989
pii: biomedicines11092548
doi: 10.3390/biomedicines11092548
pmc: PMC10525993
pii:
doi:

Types de publication

Journal Article

Langues

eng

Subventions

Organisme : Health Research Institute of the Balearic Islands (IdISBa)
ID : COVID-19/35

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Auteurs

Natalia Martínez-Pomar (N)

Immunology Department, Hospital Universitari Son Espases, 07120 Palma de Mallorca, Spain.
Health Research Institute of the Balearic Islands (IdISBa), 07120 Palma de Mallorca, Spain.

Vanesa Cunill (V)

Immunology Department, Hospital Universitari Son Espases, 07120 Palma de Mallorca, Spain.
Health Research Institute of the Balearic Islands (IdISBa), 07120 Palma de Mallorca, Spain.

Marina Segura-Guerrero (M)

Immunology Department, Hospital Universitari Son Espases, 07120 Palma de Mallorca, Spain.
Health Research Institute of the Balearic Islands (IdISBa), 07120 Palma de Mallorca, Spain.

Elisabet Pol-Pol (E)

Immunology Department, Hospital Universitari Son Espases, 07120 Palma de Mallorca, Spain.
Health Research Institute of the Balearic Islands (IdISBa), 07120 Palma de Mallorca, Spain.

Danilo Escobar Oblitas (D)

Immunology Department, Hospital Universitari Son Espases, 07120 Palma de Mallorca, Spain.
Health Research Institute of the Balearic Islands (IdISBa), 07120 Palma de Mallorca, Spain.

Jaime Pons (J)

Immunology Department, Hospital Universitari Son Espases, 07120 Palma de Mallorca, Spain.
Health Research Institute of the Balearic Islands (IdISBa), 07120 Palma de Mallorca, Spain.

Ignacio Ayestarán (I)

Health Research Institute of the Balearic Islands (IdISBa), 07120 Palma de Mallorca, Spain.
Intensive Care Unit (ICU), Hospital Universitari Son Espases, 07120 Palma de Mallorca, Spain.

Patricia C Pruneda (PC)

Dreamgenics, 33011 Oviedo, Spain.

Inés Losada (I)

Health Research Institute of the Balearic Islands (IdISBa), 07120 Palma de Mallorca, Spain.
Internal Medicine, Hospital Universitari Son Llàtzer, 07198 Palma de Mallorca, Spain.

Nuria Toledo-Pons (N)

Health Research Institute of the Balearic Islands (IdISBa), 07120 Palma de Mallorca, Spain.
Pneumology Department, Hospital Universitari Son Espases, 07120 Palma de Mallorca, Spain.

Mercedes García Gasalla (M)

Health Research Institute of the Balearic Islands (IdISBa), 07120 Palma de Mallorca, Spain.
Internal Medicine, Hospital Universitari Son Espases, 07120 Palma de Mallorca, Spain.

Joana Maria Ferrer Balaguer (JM)

Immunology Department, Hospital Universitari Son Espases, 07120 Palma de Mallorca, Spain.
Health Research Institute of the Balearic Islands (IdISBa), 07120 Palma de Mallorca, Spain.

Classifications MeSH