Blood Immunophenotypes of Idiopathic Pulmonary Fibrosis: Relationship with Disease Severity and Progression.


Journal

International journal of molecular sciences
ISSN: 1422-0067
Titre abrégé: Int J Mol Sci
Pays: Switzerland
ID NLM: 101092791

Informations de publication

Date de publication:
07 Sep 2023
Historique:
received: 25 07 2023
revised: 29 08 2023
accepted: 30 08 2023
medline: 4 10 2023
pubmed: 28 9 2023
entrez: 28 9 2023
Statut: epublish

Résumé

(1) The role of the immune response in the pathogenesis of idiopathic pulmonary fibrosis (IPF) remains controversial. We hypothesized that peripheral blood immune phenotypes will be different in IPF patients and may relate to the disease severity and progression. (2) Whole blood flow cytometry staining was performed at diagnosis in 32 IPF patients, and in 32 age- and smoking-matched healthy controls. Thirty-one IPF patients were followed up for one year and categorized as stable or progressors based on lung function, deterioration and/or death. At 18-60 months, immunophenotypes were characterized again. (3) The main results showed that: (1) compared to matched controls, at diagnosis, patients with IPF showed more neutrophils, CD8

Identifiants

pubmed: 37762135
pii: ijms241813832
doi: 10.3390/ijms241813832
pmc: PMC10531459
pii:
doi:

Substances chimiques

CD28 Antigens 0

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Subventions

Organisme : Instituto de Salud Carlos III
ID : FIS19/01152
Organisme : Instituto de Salud Carlos III
ID : PI21/00735

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Auteurs

Nuria Mendoza (N)

Institut d'Investigacions Biomediques August Pi i Sunyer (IDIBAPS), 08036 Barcelona, Spain.
Centro de Investigación Biomédica en Red de Enfermedades Respiratorias (CIBERES), 28029 Madrid, Spain.
Biomedicine Department, Universitat de Barcelona, 08036 Barcelona, Spain.

Sandra Casas-Recasens (S)

Institut d'Investigacions Biomediques August Pi i Sunyer (IDIBAPS), 08036 Barcelona, Spain.
Centro de Investigación Biomédica en Red de Enfermedades Respiratorias (CIBERES), 28029 Madrid, Spain.

Núria Olvera (N)

Institut d'Investigacions Biomediques August Pi i Sunyer (IDIBAPS), 08036 Barcelona, Spain.
Centro de Investigación Biomédica en Red de Enfermedades Respiratorias (CIBERES), 28029 Madrid, Spain.
Barcelona Supercomputing Center (BSC), 08034 Barcelona, Spain.

Fernanda Hernandez-Gonzalez (F)

Institut d'Investigacions Biomediques August Pi i Sunyer (IDIBAPS), 08036 Barcelona, Spain.
Biomedicine Department, Universitat de Barcelona, 08036 Barcelona, Spain.
Respiratory Institute, Clinic Barcelona, 08036 Barcelona, Spain.

Tamara Cruz (T)

Institut d'Investigacions Biomediques August Pi i Sunyer (IDIBAPS), 08036 Barcelona, Spain.
Centro de Investigación Biomédica en Red de Enfermedades Respiratorias (CIBERES), 28029 Madrid, Spain.

Núria Albacar (N)

Institut d'Investigacions Biomediques August Pi i Sunyer (IDIBAPS), 08036 Barcelona, Spain.
Centro de Investigación Biomédica en Red de Enfermedades Respiratorias (CIBERES), 28029 Madrid, Spain.
Respiratory Institute, Clinic Barcelona, 08036 Barcelona, Spain.

Xavier Alsina-Restoy (X)

Respiratory Institute, Clinic Barcelona, 08036 Barcelona, Spain.

Alejandro Frino-Garcia (A)

Respiratory Institute, Clinic Barcelona, 08036 Barcelona, Spain.

Gemma López-Saiz (G)

Respiratory Institute, Clinic Barcelona, 08036 Barcelona, Spain.

Lucas Robres (L)

Centro de Investigación Biomédica en Red de Enfermedades Respiratorias (CIBERES), 28029 Madrid, Spain.

Mauricio Rojas (M)

Department of Internal Medicine, The Ohio State University Wexner Medical Center, Columbus, OH 43210, USA.

Alvar Agustí (A)

Institut d'Investigacions Biomediques August Pi i Sunyer (IDIBAPS), 08036 Barcelona, Spain.
Centro de Investigación Biomédica en Red de Enfermedades Respiratorias (CIBERES), 28029 Madrid, Spain.
Biomedicine Department, Universitat de Barcelona, 08036 Barcelona, Spain.
Respiratory Institute, Clinic Barcelona, 08036 Barcelona, Spain.

Jacobo Sellarés (J)

Institut d'Investigacions Biomediques August Pi i Sunyer (IDIBAPS), 08036 Barcelona, Spain.
Centro de Investigación Biomédica en Red de Enfermedades Respiratorias (CIBERES), 28029 Madrid, Spain.
Respiratory Institute, Clinic Barcelona, 08036 Barcelona, Spain.

Rosa Faner (R)

Institut d'Investigacions Biomediques August Pi i Sunyer (IDIBAPS), 08036 Barcelona, Spain.
Centro de Investigación Biomédica en Red de Enfermedades Respiratorias (CIBERES), 28029 Madrid, Spain.
Biomedicine Department, Universitat de Barcelona, 08036 Barcelona, Spain.

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