Apparently isolated CNS involvement in Erdheim-Chester disease: Case report.

Bone lesions Erdheim-Chester MRI

Journal

Radiology case reports
ISSN: 1930-0433
Titre abrégé: Radiol Case Rep
Pays: Netherlands
ID NLM: 101467888

Informations de publication

Date de publication:
Dec 2023
Historique:
received: 27 02 2023
revised: 28 08 2023
accepted: 12 09 2023
medline: 16 10 2023
pubmed: 16 10 2023
entrez: 16 10 2023
Statut: epublish

Résumé

We present the case of a 48-year-old-woman with apparently isolated central nervous system Erdheim-Chester disease characterized by brainstem involvement. Erdheim-Chester disease is extremely rare and multisystem impairment should always be sought in the suspicion of such pathology.

Identifiants

pubmed: 37840893
doi: 10.1016/j.radcr.2023.09.033
pii: S1930-0433(23)00672-6
pmc: PMC10570539
doi:

Types de publication

Case Reports

Langues

eng

Pagination

4431-4434

Informations de copyright

© 2023 The Authors. Published by Elsevier Inc. on behalf of University of Washington.

Références

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Auteurs

Giuseppe Romano (G)

Second Division of Neurology, University of Campania "Luigi Vanvitelli", Naples, Italy.

Mario Cirillo (M)

MRI Research Center SUN-FISM, University of Campania "Luigi Vanvitelli", Naples, Italy.

Simona Bonavita (S)

Second Division of Neurology, University of Campania "Luigi Vanvitelli", Naples, Italy.

Giuseppe Toro (G)

Department of Medical and Surgical Specialties and Dentistry, University of Campania "Luigi Vanvitelli", Naples, Italy.

Andrea Di Pietro (A)

Second Division of Neurology, University of Campania "Luigi Vanvitelli", Naples, Italy.

Luigi Lavorgna (L)

First Division of Neurology, University of Campania "Luigi Vanvitelli", Naples, Italy.

Elisabetta Maida (E)

Second Division of Neurology, University of Campania "Luigi Vanvitelli", Naples, Italy.

Francesca Pagliuca (F)

Pathology Unit, Department of Mental and Physical Health and Preventive Medicine, "Luigi Vanvitelli", Naples, Italy.

Fabrizio Urraro (F)

Department of Precision Medicine, University of Campania "Luigi Vanvitelli", Naples, Italy.

Cinzia Coppola (C)

Second Division of Neurology, University of Campania "Luigi Vanvitelli", Naples, Italy.

Giacomo Lus (G)

Second Division of Neurology, University of Campania "Luigi Vanvitelli", Naples, Italy.

Elisabetta Signoriello (E)

Second Division of Neurology, University of Campania "Luigi Vanvitelli", Naples, Italy.

Classifications MeSH