Removal of a thoracic intramedullary epidermoid tumor in a child.

child intradural tumor neurophysiological monitoring spinal cord epidermoid cyst

Journal

Neurosurgical focus: Video
ISSN: 2643-5217
Titre abrégé: Neurosurg Focus Video
Pays: United States
ID NLM: 101773517

Informations de publication

Date de publication:
Oct 2023
Historique:
received: 29 05 2023
accepted: 14 07 2023
medline: 20 10 2023
pubmed: 20 10 2023
entrez: 20 10 2023
Statut: epublish

Résumé

Epidermoid cysts are rare, benign neoplasms that account for less than 1% of all intraspinal tumors. The most common localization is in the lumbar area, and one-third of the tumors are intramedullary. In this video, the authors present removal of a thoracic intramedullary epidermoid tumor in a 6-year-old boy, carrier of a 22q11 gene duplication and affected by psychomotor retardation. He presented a 1-year history of progressive gait impairment. No history of lumbar puncture or trauma was reported. The procedure was performed under neurophysiological monitoring, and it was uneventful with complete recovery of neurological function. Technical nuances are illustrated.

Identifiants

pubmed: 37859944
doi: 10.3171/2023.7.FOCVID2366
pii: 2023.7.FOCVID2366
pmc: PMC10583810
doi:

Types de publication

Journal Article

Langues

eng

Pagination

V17

Informations de copyright

© 2023, The Authors.

Déclaration de conflit d'intérêts

Disclosures Dr. G. Cinalli reported personal fees from Integra NeuroSciences outside the submitted work.Dr. G. Cinalli reported personal fees from Integra NeuroSciences outside the submitted work.

Références

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Auteurs

Marianna Di Costanzo (MD)

Department of Pediatric Neurosurgery, Santobono-Pausilipon Children's Hospital AORN, Naples.
Division of Neurosurgery, Department of Neurosciences, Reproductive and Odonotostomatological Sciences, Università degli Studi di Napoli "Federico II," Naples.

Pietro Spennato (P)

Department of Pediatric Neurosurgery, Santobono-Pausilipon Children's Hospital AORN, Naples.

Francesca Vitulli (F)

Department of Pediatric Neurosurgery, Santobono-Pausilipon Children's Hospital AORN, Naples.
Division of Neurosurgery, Department of Neurosciences, Reproductive and Odonotostomatological Sciences, Università degli Studi di Napoli "Federico II," Naples.

Maria Allegra Cinalli (MA)

Department of Medicine and Surgery, University of Milan Bicocca, Milan.
Neurosurgery Department, Ospedale San Gerardo, Monza; and.

Maria De Liso (M)

Department of Pediatric Neuroradiology, Santobono-Pausilipon Children's Hospital AORN, Naples, Italy.

Claudio Ruggiero (C)

Department of Pediatric Neurosurgery, Santobono-Pausilipon Children's Hospital AORN, Naples.

Giuseppe Cinalli (G)

Department of Pediatric Neurosurgery, Santobono-Pausilipon Children's Hospital AORN, Naples.

Classifications MeSH