Undifferentiated embryonal sarcoma of the liver: a case report of a rare case in an adult patient.

case report hepatic sarcoma neoplasm of the liver surgery of de liver undifferentiated embryonal sarcoma of the liver

Journal

Journal of surgical case reports
ISSN: 2042-8812
Titre abrégé: J Surg Case Rep
Pays: England
ID NLM: 101560169

Informations de publication

Date de publication:
Oct 2023
Historique:
received: 24 08 2023
accepted: 05 10 2023
medline: 24 10 2023
pubmed: 24 10 2023
entrez: 24 10 2023
Statut: epublish

Résumé

Undifferentiated embryonal sarcoma of the liver is a rare primary mesenchymal hepatic tumor that usually occurs in pediatric patients. In adulthood, this aggressive neoplasm represents only 7% of the liver sarcomas. This case reports a liver sarcoma occurring in a 49-year-old female patient. The patient was admitted in the emergency room with abdominal pain. Computerized tomography scan and magnetic resonance imaging showed a giant lobulated cystic mass in the right hepatic lobe, suggesting an atypical hemangioma. Right hepatectomy was performed. This rare case promotes a review of the differential diagnosis of liver primary neoplasms including sarcoma. The histological examination revealed an undifferentiated embryonal sarcoma. The patient underwent adjuvant chemotherapy. Currently, our patient is in complete sustained remission 4 years after chemotherapy.

Identifiants

pubmed: 37873046
doi: 10.1093/jscr/rjad578
pii: rjad578
pmc: PMC10590654
doi:

Types de publication

Case Reports

Langues

eng

Pagination

rjad578

Informations de copyright

Published by Oxford University Press and JSCR Publishing Ltd. © The Author(s) 2023.

Déclaration de conflit d'intérêts

None declared.

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Auteurs

Ana M Marques (AM)

General Surgery Department, Centro Hospitalar Tondela-Viseu, Rei Dom Duarte, 3504-509 Viseu, Portugal.

Guilherme Fontinha (G)

Pathological Anatomy Department, Centro Hospitalar e Universitário de Coimbra, Praceta Professor Mota Pinto, 3004-561 Coimbra, Portugal.

Maria João Ferreira (MJ)

Hepatobiliary and Pancreatic Department, Centro Hospitalar Tondela-Viseu, Rei Dom Duarte, 3504-509 Viseu, Portugal.

Milene Sá (M)

Colorectal Department, Centro Hospitalar Tondela-Viseu, Rei Dom Duarte, 3504-509 Viseu, Portugal.

Júlio Constantino (J)

Liver Transplant Department, Centro Hospitalar e Universitário de Coimbra, Praceta Professor Mota Pinto, 3004-561 Coimbra, Portugal.

Jorge Pereira (J)

Hepatobiliary and Pancreatic Department, Centro Hospitalar Tondela-Viseu, Rei Dom Duarte, 3504-509 Viseu, Portugal.

Classifications MeSH